日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Axonal TDP-43 condensates drive neuromuscular junction disruption through inhibition of local synthesis of nuclear encoded mitochondrial proteins

轴突 TDP-43 凝聚物通过抑制核编码线粒体蛋白的局部合成来驱动神经肌肉接头破坏

Topaz Altman #, Ariel Ionescu #, Amjad Ibraheem, Dominik Priesmann, Tal Gradus-Pery, Luba Farberov, Gayster Alexandra, Natalia Shelestovich, Ruxandra Dafinca, Noam Shomron, Florence Rage, Kevin Talbot, Michael E Ward, Amir Dori, Marcus Krüger, Eran Perlson

A CRMP4-dependent retrograde axon-to-soma death signal in amyotrophic lateral sclerosis

肌萎缩侧索硬化症中 CRMP4 依赖的逆行轴突至躯体死亡信号

Roy Maimon, Lior Ankol, Tal Gradus Pery, Topaz Altman, Ariel Ionescu, Romana Weissova, Michael Ostrovsky, Elizabeth Tank, Gayster Alexandra, Natalia Shelestovich, Yarden Opatowsky, Amir Dori, Sami Barmada, Martin Balastik, Eran Perlson

Targeting the Sigma-1 Receptor via Pridopidine Ameliorates Central Features of ALS Pathology in a SOD1G93A Model

通过普利多比定靶向 Sigma-1 受体可改善 SOD1G93A 模型中的 ALS 病理学核心特征

Ariel Ionescu, Tal Gradus, Topaz Altman, Roy Maimon, Noi Saraf Avraham, Michal Geva, Michael Hayden, Eran Perlson

miR126-5p Downregulation Facilitates Axon Degeneration and NMJ Disruption via a Non-Cell-Autonomous Mechanism in ALS

miR126-5p 下调通过 ALS 中的非细胞自主机制促进轴突变性和 NMJ 破坏

Roy Maimon, Ariel Ionescu, Avichai Bonnie, Sahar Sweetat, Shane Wald-Altman, Shani Inbar, Tal Gradus, Davide Trotti, Miguel Weil, Oded Behar, Eran Perlson

High content image analysis reveals function of miR-124 upstream of Vimentin in regulating motor neuron mitochondria

高内涵图像分析揭示了波形蛋白上游 miR-124 在调节运动神经元线粒体中的作用

Tal Yardeni, Raquel Fine, Yuvraj Joshi, Tal Gradus-Pery, Noga Kozer, Irit Reichenstein, Eran Yanowski, Shir Nevo, Hila Weiss-Tishler, Michal Eisenberg-Bord, Tal Shalit, Alexander Plotnikov, Haim M Barr, Eran Perlson, Eran Hornstein

Localization of RNAi Machinery to Axonal Branch Points and Growth Cones Is Facilitated by Mitochondria and Is Disrupted in ALS

RNAi 机制定位到轴突分支点和生长锥是由线粒体促成的,而在 ALS 中被破坏

Noga Gershoni-Emek, Topaz Altman, Ariel Ionescu, Christopher J Costa, Tal Gradus-Pery, Dianna E Willis, Eran Perlson

The receptor tyrosine kinase TrkB signals without dimerization at the plasma membrane

受体酪氨酸激酶 TrkB 在质膜上不发生二聚化而发出信号

Eitan Erez Zahavi, Noam Steinberg, Topaz Altman, Michael Chein, Yuvraj Joshi, Tal Gradus-Pery, Eran Perlson

ALS Along the Axons - Expression of Coding and Noncoding RNA Differs in Axons of ALS models

轴突上的 ALS - ALS 模型中轴突上编码和非编码 RNA 的表达不同

Nimrod Rotem, Iddo Magen, Ariel Ionescu, Noga Gershoni-Emek, Topaz Altman, Christopher J Costa, Tal Gradus, Metsada Pasmanik-Chor, Dianna E Willis, Iddo Z Ben-Dov, Eran Hornstein, Eran Perlson

Proteomic Analysis of Dynein-Interacting Proteins in Amyotrophic Lateral Sclerosis Synaptosomes Reveals Alterations in the RNA-Binding Protein Staufen1

肌萎缩侧索硬化症突触体中动力蛋白相互作用蛋白的蛋白质组学分析揭示了 RNA 结合蛋白 Staufen1 的改变

Noga Gershoni-Emek, Arnon Mazza, Michael Chein, Tal Gradus-Pery, Xin Xiang, Ka Wan Li, Roded Sharan, Eran Perlson

Phosphatidylserine Ameliorates Neurodegenerative Symptoms and Enhances Axonal Transport in a Mouse Model of Familial Dysautonomia

磷脂酰丝氨酸可改善家族性自主神经功能紊乱小鼠模型中的神经退行性症状并增强轴突运输

Shiran Naftelberg, Ziv Abramovitch, Shani Gluska, Sivan Yannai, Yuvraj Joshi, Maya Donyo, Keren Ben-Yaakov, Tal Gradus, Jonathan Zonszain, Chen Farhy, Ruth Ashery-Padan, Eran Perlson, Gil Ast