日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Nemo-like kinase disrupts nuclear import and drives TDP43 mislocalization in ALS

Nemo样激酶干扰核输入并导致ALS中TDP43错误定位。

Bekier, Michael E 2nd; Pinarbasi, Emile; Krishnan, Gopinath; Mesojedec, Jack J; Hurley, Madelaine; Harikumar Sheela, Harisankar; Collins, Catherine A; Ghaffari, Layla; de Majo, Martina; Ullian, Erik M; Koontz, Mark; Coleman, Sarah; Li, Xingli; Tank, Elizabeth Mh; Waksmacki, Jacob; Gao, Fen-Biao; Barmada, Sami J

Preliminary and Ongoing Investigation of Human Induced Pluripotent Stem Cell‐Derived Frontotemporal Dementia Cortical Organoids Assessed by Mass Spectrometry

利用质谱法对人诱导多能干细胞衍生的额颞叶痴呆皮质类器官进行初步和持续研究

Lewis, Allison; Keshara, Rashmiparvathi; Kim, Yung Hae; Grapin-Botton, Anne; Best, Merci N; Lamp, Jared; Umstead, Andrew; Sierra, Mariana; Spencer, Amber; Erturk, Ilkim; Tank, Elizabeth M; Sexton, Jonathan; Barmada, Sami; Vega, Irving E; Paulson, Henry L

Nemo-like kinase disrupts nuclear import and drives TDP43 mislocalization in ALS

Nemo样激酶干扰核输入并导致ALS中TDP43错误定位。

Bekier, Michael E 2nd; Pinarbasi, Emile; Mesojedec, Jack J; Ghaffari, Layla; de Majo, Martina; Ullian, Erik; Koontz, Mark; Coleman, Sarah; Li, Xingli; Tank, Elizabeth M H; Waksmacki, Jacob; Barmada, Sami

Preliminary and Ongoing Investigation of Human Induced Pluripotent Stem Cell‐Derived Frontotemporal Dementia Cortical Organoids Assessed by Mass Spectrometry

利用质谱法对人诱导多能干细胞衍生的额颞叶痴呆皮质类器官进行初步和持续研究

Pagano, Nathan; Perez, Gerard Aguilar; Garcia-Milian, Rolando; Manuelidis, Laura; Anwer, Mehwish; Swaro, Aditya; Bristow, Brianna; Fan, Jianjia; Cheng, Wai Hang; Cembrowski, Mark; Wellington, Cheryl L; Lorincz‐Comi, Noah J; Cheng, Feixiong; Song, Wenqiang; Chen, Xin; Paz, Isabela Rivera; Hou, Yuan; Zhou, Yadi; Xu, Jielin; Martin, William; Pieper, Andrew A; Haines, Jonathan L; Mina, Chung; Wendt, Stefan; Lin, Ada J; Ebert, Sarah N; Brennan, Declan J; Cai, Wenji; Bai, Yanyang; Kong, Da Young; Sorrentino, Stefano; Groten, Christopher J; Lee, Christopher; Frew, Jonathan; Choi, Hyun B; Karamboulas, Konstantina; Delhaye, Mathias; Kaplan, David R; Miller, Freda; MacVicar, Brian A; Nygaard, Haakon B; Lorincz‐Comi, Noah J; Cheng, Feixiong; Wijesinghe, Printha; Xi, Jeanne; Campbell, Matthew; Chen, Si Xuan; Pham, Wellington; Matsubara, Joanne A; Xu, Jielin; Zhou, Yadi; Lorincz‐Comi, Noah J; Dou, Lijun; Hou, Yuan; Qiu, Yunguang; Pieper, Andrew A; Cheng, Feixiong; Best, Merci N; Lamp, Jared; Umstead, Andrew; Sierra, Mariana; Spencer, Amber; Erturk, Ilkim; Tank, Elizabeth M; Sexton, Jonathan; Barmada, Sami; Vega, Irving E; Paulson, Henry L

Molecular Visualization of Neuronal TDP43 Pathology In Situ

神经元TDP43病理的分子可视化

Erwin, Amanda L; Fernandez, Martin G; Chang, Matthew L; Attili, Durga; Bekier, Michael; Pinarbasi, Emile S; Russ, Jennifer E; Sutanto, Renaldo; Thomas, Dafydd; Shen, Xinfei; Baldridge, Ryan D; Tank, Elizabeth M H; Barmada, Sami J; Mosalaganti, Shyamal

TDP43 autoregulation gives rise to shortened isoforms that are tightly controlled by both transcriptional and post-translational mechanisms.

TDP43 自身调节产生较短的异构体,这些异构体受到转录和翻译后机制的严格控制

Dykstra Megan M, Weskamp Kaitlin, Gómez Nicolás B, Waksmacki Jacob, Tank Elizabeth, Glineburg M Rebecca, Snyder Allison, Pinarbasi Emile, Bekier Michael, Li Xingli, Bai Jen, Shahzad Shameena, Nedumaran Juno, Wieland Clare, Stewart Corey, Willey Sydney, Grotewold Nikolas, McBride Jonathon, Moran John J, Suryakumar Aditya V, Lucas Michael, Tessier Peter, Ward Michael, Todd Peter, Barmada Sami J

Shortened TDP43 isoforms upregulated by neuronal hyperactivity drive TDP43 pathology in ALS

神经元过度活跃导致TDP43亚型缩短,进而引发ALS中的TDP43病理。

Weskamp, Kaitlin; Tank, Elizabeth M; Miguez, Roberto; McBride, Jonathon P; Gómez, Nicolás B; White, Matthew; Lin, Ziqiang; Gonzalez, Carmen Moreno; Serio, Andrea; Sreedharan, Jemeen; Barmada, Sami J

Insights into intragenic and extragenic effectors of prion propagation using chimeric prion proteins

利用嵌合朊病毒蛋白深入了解朊病毒传播的基因内和基因外效应因子

True, Heather L; Kalastavadi, Tejas; Tank, Elizabeth M H

Prion protein repeat expansion results in increased aggregation and reveals phenotypic variability

朊病毒蛋白重复序列扩增导致聚集增加并揭示表型变异性

Tank, Elizabeth M H; Harris, David A; Desai, Amar A; True, Heather L