日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A Refined Method for Micro-Scale Blood Cystine Measurement in Preclinical Cystinosis Models

一种用于临床前胱氨酸病模型中微量血液胱氨酸测量的改进方法

De Leo, Ester; Cairoli, Sara; Rega, Laura Rita; Colucci, Manuela; Taranta, Anna; Goffredo, Bianca Maria; Emma, Francesco; Bellomo, Francesco

Ketogenic Diet and Progression of Kidney Disease in Animal Models of Nephropathic Cystinosis.

生酮饮食与肾病性胱氨酸病动物模型肾脏疾病进展的关系

Bellomo Francesco, Pugliese Sara, Cairoli Sara, Krohn Patrick, De Stefanis Cristiano, Raso Roberto, Rega Laura Rita, Taranta Anna, De Leo Ester, Ciolfi Andrea, Cicolani Nicolò, Petrini Stefania, Luciani Alessandro, Goffredo Bianca Maria, Porzio Ottavia, Devuyst Olivier, Dionisi-Vici Carlo, Emma Francesco

Nlrp2 deletion ameliorates kidney damage in a mouse model of cystinosis

Nlrp2 缺失可减轻胱氨酸病小鼠模型中的肾脏损伤

Rossi, Marianna Nicoletta; Matteo, Valentina; Diomedi-Camassei, Francesca; De Leo, Ester; Devuyst, Olivier; Lamkanfi, Mohamed; Caiello, Ivan; Loricchio, Elena; Bellomo, Francesco; Taranta, Anna; Emma, Francesco; De Benedetti, Fabrizio; Prencipe, Giusi

Carboxyl-Terminal SSLKG Motif of the Human Cystinosin-LKG Plays an Important Role in Plasma Membrane Sorting

人胱氨酸蛋白酶-LKG的羧基末端SSLKG基序在质膜分选过程中发挥重要作用

Bellomo, Francesco; Taranta, Anna; Petrini, Stefania; Venditti, Rossella; Rocchetti, Maria Teresa; Rega, Laura Rita; Corallini, Serena; Gesualdo, Loreto; De Matteis, Maria Antonietta; Emma, Francesco