日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Z variant heterozygosity in alpha-1 antitrypsin deficiency: disease risk and treatment implications

α1-抗胰蛋白酶缺乏症中Z变异杂合性:疾病风险和治疗意义

Hersh, Craig P; Teckman, Jeffrey H; Strnad, Pavel; Hakim, Aaron; Carroll, Tomás P; Hall, Ian P; Ghosh, Auyon J; Barjaktarevic, Igor; McElvaney, Noel G; Kaserman, Joseph E; Lomas, David A; Strange, Charlie; Drummond, M Bradley; Rennard, Stephen; Hanna, Kathi E; Clark, Virginia C; Goldklang, Monica P; Iverson, Peg; Wilson, Andrew A

Increased serum GM-CSF at diagnosis of biliary atresia is associated with improved biliary drainage.

胆道闭锁诊断时血清 GM-CSF 水平升高与胆道引流改善相关

Taylor Sarah A, Harpavat Sanjiv, Gromer Kyle D, Andreev Victor, Loomes Kathleen M, Bezerra Jorge A, Jarasvaraparn Chaowapong, Wang Kasper, Horslen Simon, Rosenthal Philip, Teckman Jeffrey, Valentino Pamela L, Ng Vicky L, Karpen Saul J, Sokol Ronald J, Alonso Estella M, Mack Cara L

Prospective Multicenter Longitudinal Measurement of Liver Stiffness in School-Age Children With Cholestatic Liver Disease

前瞻性多中心纵向研究测量学龄期胆汁淤积性肝病患儿的肝脏硬度

Shneider, Benjamin L; Goodrich, Nathan P; Ye, Wen; Molleston, Jean P; Leung, Daniel H; Sokol, Ronald J; Cavallo, Laurel; Wang, Kasper; Valentino, Pamela L; Teckman, Jeffery H; Squires, James E; Sundaram, Shikha S; Rosenthal, Philip; Romero, Rene; Miethke, Alexander G; Loomes, Kathleen M; Kohli, Rohit; Karpen, Saul J; Kamath, Binita M; Jensen, M Kyle; Bezerra, Jorge A; Bass, Lee M; Magee, John C

Diagnostic accuracy of serum matrix metalloproteinase-7 as a biomarker of biliary atresia in a large North American cohort

血清基质金属蛋白酶-7作为胆道闭锁生物标志物的诊断准确性:一项北美大型队列研究

Pandurangi, Sindhu; Mourya, Reena; Nalluri, Shreya; Fei, Lin; Dong, Shun; Harpavat, Sanjiv; Guthery, Stephen L; Molleston, Jean P; Rosenthal, Philip; Sokol, Ronald J; Wang, Kasper S; Ng, Vicky; Alonso, Estella M; Hsu, Evelyn K; Karpen, Saul J; Loomes, Kathleen M; Magee, John C; Shneider, Benjamin L; Horslen, Simon P; Teckman, Jeffrey H; Bezerra, Jorge A

Fibrosis, biomarkers and liver biopsy in AAT deficiency and relation to liver Z protein polymer accumulation

α1-抗胰蛋白酶缺乏症中的纤维化、生物标志物和肝活检及其与肝脏Z蛋白聚合物积累的关系

Suri, Anandini; Zhang, Zidong; Neuschwander-Tetri, Brent; Lomas, David A; Heyer-Chauhan, Nina; Burling, Keith; Loomba, Rohit; Brenner, David A; Nagy, Rosemary; Wilson, Andrew; Carpenter, Danielle; Blomenkamp, Keith; Teckman, Jeffrey

Biomarkers Associated With Future Severe Liver Disease in Children With Alpha-1-Antitrypsin Deficiency

与α1-抗胰蛋白酶缺乏症患儿未来发生严重肝病相关的生物标志物

Teckman, Jeffrey H; Buchanan, Paula; Blomenkamp, Keith Steven; Heyer-Chauhan, Nina; Burling, Keith; Lomas, David A

A Gastroenterologist's Guide to Care Transitions in Cystic Fibrosis from Pediatrics to Adult Care

胃肠病学家指导囊性纤维化患者从儿科到成人护理的过渡

Patel, Dhiren; Baliss, Michelle; Saikumar, Pavithra; Numan, Laith; Teckman, Jeffrey; Hachem, Christine

Sarcopenia is associated with osteopenia and impaired quality of life in children with genetic intrahepatic cholestatic liver disease

肌少症与遗传性肝内胆汁淤积性肝病患儿的骨质减少和生活质量下降有关。

Boster, Julia M; Goodrich, Nathan P; Spino, Cathie; Loomes, Kathleen M; Alonso, Estella M; Kamath, Binita M; Sokol, Ronald J; Karpen, Saul; Miethke, Alexander; Shneider, Benjamin L; Molleston, Jean P; Kohli, Rohit; Horslen, Simon P; Rosenthal, Philip; Valentino, Pamela L; Teckman, Jeffrey H; Hangartner, Thomas N; Sundaram, Shikha S

Neonatal cholestasis in children with Alpha-1-AT deficiency is a risk for earlier severe liver disease with male predominance

患有α1-抗胰蛋白酶缺乏症的儿童发生新生儿胆汁淤积症会增加其早期罹患严重肝病的风险,且男性患者居多。

Teckman, Jeffrey; Rosenthal, Philip; Ignacio, Rosalinda V; Spino, Cathie; Bass, Lee M; Horslen, Simon; Wang, Kasper; Magee, John C; Karpen, Saul; Asai, Akihiro; Molleston, Jean P; Squires, Robert H; Kamath, Binita M; Guthery, Stephen L; Loomes, Kathleen M; Shneider, Benjamin L; Sokol, Ronald J

Change in Health-Related Quality of Life in Youth with Chronic Hepatitis B Living in North America: A 5-Year Cohort Study

北美慢性乙型肝炎青少年健康相关生活质量的变化:一项为期5年的队列研究

Schwarzenberg, Sarah Jane; King, Wendy C; Ling, Simon C; Murray, Karen F; Mogul, Douglas; Rosenthal, Philip; Rodriguez-Baez, Norberto; Teckman, Jeffrey; Schwarz, Kathleen B