日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Refined Transgenic Mouse Models Which Recapitulate the Natural Features of Chronic Wasting Disease With Rapid Prion Disease Onsets

能够重现慢性消耗性疾病自然特征并快速发生朊病毒疾病的改良转基因小鼠模型

DeFranco, Joseph P; Kim, Sehun; Atkinson, Zoe N; Crowell, Jenna; Lei, Samantha; Bian, Jifeng; Telling, Glenn C

Enhanced lysosomal activity prevents infection with PrP(Sc) and the seeding activity of α-synuclein & tau prions

溶酶体活性增强可阻止 PrP(Sc) 感染以及 α-突触核蛋白和 tau 朊病毒的播散活性。

Mercer, Robert C C; Le, Nhat T T; Mirza-Romero, Nadia A; Orbe, Isabel C; Flaherty, Erin; DeFranco, Joseph P; Lavigna, Giada; Gatdula, Jean R P; Fraser, Douglas G; Sundaravadivelu, Aravind; Vultaggio, Janelle S; Beeler, Aaron B; Chiesa, Roberto; Telling, Glenn C; Harris, David A

Leveraging the dominant-negative effect of the kuru-protective G127V prion protein variant as a novel therapeutic strategy

利用库鲁病保护性朊病毒蛋白变体G127V的显性负效应作为一种新型治疗策略

Gatdula, Jean R P; Orbe, Isabel C; Tolton, Samantha G; Saunders, Linnea M; Vultaggio, Janelle S; Mercer, Robert C C; Bartz, Jason C; Telling, Glenn C; Eraña, Hasier; Castilla, Joaquín; Harris, David A

Regulated coexpression of PrP from different species in mice impacts the replication and host range properties of prion strains

小鼠体内不同物种PrP的调控性共表达会影响朊病毒株的复制和宿主范围特性。

DeFranco, Joseph P; Bian, Jifeng; Kim, Sehun; Atkinson, Zoe N; Crowell, Jenna; Kang, Hae-Eun; Bodrogi, Hannah O; Christiansen, Jeffrey R; Díaz-Domínguez, Carlos M; Telling, Glenn C

Conservation of strain properties of bank vole-adapted chronic wasting disease in the absence of glycosylation and membrane anchoring

在缺乏糖基化和膜锚定的情况下,田鼠适应性慢性消耗性疾病的菌株特性得以保留

Vidal, Enric; Eraña, Hasier; Charco, Jorge M; Lorenzo, Nuria L; Giler, Samanta; Ordóñez, Montserrat; Fernández-Muñoz, Eva; San-Juan-Ansoleaga, Maitena; Telling, Glenn C; Sánchez-Martín, Manuel A; Geijo, Mariví; Requena, Jesús R; Castilla, Joaquín

Effect of primary structural variation on cervid prion protein in flexibility, stability, and spontaneous misfolding propensity

一级结构变异对鹿朊病毒蛋白的柔性、稳定性和自发错误折叠倾向的影响

Díaz-Domínguez, Carlos M; Eraña, Hasier; Peccati, Francesca; Vidal, Enric; Charco, Jorge M; Sampedro-Torres-Quevedo, Cristina; Pérez-Castro, Miguel A; Lorenzo, Nuria L; Giler, Samanta; Telling, Glenn C; Geijo, Mariví; Requena, Jesús R; Jiménez-Osés, Gonzalo; Castilla, Joaquín

The Strain Properties of Korean and North American Chronic Wasting Disease Prions Are Indistinguishable

韩国和北美慢性消耗性疾病朊病毒的毒株特性无法区分

Sohn, Hyun Joo; DeFranco, Joseph P; Park, Hoo Chang; Park, Kyung Je; Bian, Jifeng; Crowell, Jenna; Kim, Sehun; Webster, Bailey K; Kang, Hae-Eun; Telling, Glenn C

The Evolution of Experimental Rodent Models for Prion Diseases

朊病毒疾病实验啮齿动物模型的演变

DeFranco, Joseph P; Telling, Glenn C

Lysosomal Enhancement Prevents Infection with PrP(Sc), α-Synuclein & Tau Prions.

溶酶体增强可预防 PrP(Sc)、α-突触核蛋白和 Tau 朊病毒的感染

Mercer Robert C C, Le Nhat T T, Mirza-Romero Nadia A, Flaherty Erin, DeFranco Joseph P, Lavigna Giada, Orbe Isabel C, Gatdula Jean R P, Fraser Douglas G, Sundaravadivelu Aravind, Vultaggio Janelle S, Beeler Aaron B, Chiesa Roberto, Telling Glenn C, Harris David A

Novel Prion Strain as Cause of Chronic Wasting Disease in a Moose, Finland

芬兰一头驼鹿患上慢性消耗性疾病,一种新型朊病毒株被发现

Sun, Julianna L; Kim, Sehun; Crowell, Jenna; Webster, Bailey K; Raisley, Emma K; Lowe, Diana C; Bian, Jifeng; Korpenfelt, Sirkka-Liisa; Benestad, Sylvie L; Telling, Glenn C