日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Unbiased metabolome screen leads to personalized medicine strategy for amyotrophic lateral sclerosis

无偏代谢组学筛选为肌萎缩侧索硬化症的个性化医疗策略奠定基础

Boddy, Sarah; Islam, Mahjabin; Moll, Tobias; Kurz, Julian; Burrows, David; McGown, Alexander; Bhargava, Anushka; Julian, Thomas H; Harvey, Calum; Marshall, Jack Ng; Hall, Benjamin Pc; Allen, Scott P; Kenna, Kevin P; Sanderson, Eleanor; Zhang, Sai; Ramesh, Tennore; Snyder, Michael P; Shaw, Pamela J; McDermott, Christopher; Cooper-Knock, Johnathan

The effect of hyperglycemia on neurovascular coupling and cerebrovascular patterning in zebrafish

高血糖对斑马鱼神经血管耦合和脑血管模式形成的影响

Chhabria, Karishma; Plant, Karen; Bandmann, Oliver; Wilkinson, Robert N; Martin, Chris; Kugler, Elisabeth; Armitage, Paul A; Santoscoy, Paola Lm; Cunliffe, Vincent T; Huisken, Jan; McGown, Alexander; Ramesh, Tennore; Chico, Tim Ja; Howarth, Clare

Mutations in the Glycosyltransferase Domain of GLT8D1 Are Associated with Familial Amyotrophic Lateral Sclerosis

GLT8D1 糖基转移酶结构域突变与家族性肌萎缩侧索硬化症相关

Johnathan Cooper-Knock, Tobias Moll, Tennore Ramesh, Lydia Castelli, Alexander Beer, Henry Robins, Ian Fox, Isabell Niedermoser, Philip Van Damme, Matthieu Moisse, Wim Robberecht, Orla Hardiman, Monica P Panades, Abdelilah Assialioui, Jesus S Mora, A Nazli Basak, Karen E Morrison, Christopher E Shaw

Stable transgenic C9orf72 zebrafish model key aspects of the ALS/FTD phenotype and reveal novel pathological features

稳定的转基因 C9orf72 斑马鱼模拟了 ALS/FTD 表型的关键方面并揭示了新的病理特征

Matthew P Shaw, Adrian Higginbottom, Alexander McGown, Lydia M Castelli, Evlyn James, Guillaume M Hautbergue, Pamela J Shaw, Tennore M Ramesh

A zebrafish model exemplifies the long preclinical period of motor neuron disease

斑马鱼模型生动地展现了运动神经元疾病漫长的临床前期。

Ramesh, Tennore M; Shaw, Pamela J; McDearmid, Jonathan

Tardbpl splicing rescues motor neuron and axonal development in a mutant tardbp zebrafish

Tardbpl 剪接挽救突变 tardbp 斑马鱼的运动神经元和轴突发育

Channa A A Hewamadduma, Andrew J Grierson, Taylur P Ma, Luyuan Pan, Cecilia B Moens, Philip W Ingham, Tennore Ramesh, Pamela J Shaw

Axonal Transport Defects in a Mitofusin 2 Loss of Function Model of Charcot-Marie-Tooth Disease in Zebrafish.

斑马鱼线粒体融合蛋白 2 功能丧失模型中夏科-马里-图斯病的轴突运输缺陷

Chapman Anna L, Bennett Ellen J, Ramesh Tennore M, De Vos Kurt J, Grierson Andrew J