日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

An optimized Western blot assay provides a comprehensive assessment of the physiological endoproteolytic processing of the prion protein.

优化的蛋白质印迹分析可对朊病毒蛋白的生理性内蛋白水解加工进行全面评估

Vanni Ilaria, Iacobone Floriana, D'Agostino Claudia, Giovannelli Matteo, Pirisinu Laura, Altmeppen Hermann Clemens, Castilla Joaquin, Torres Juan Maria, Agrimi Umberto, Nonno Romolo

Wide distribution of prion infectivity in the peripheral tissues of vCJD and sCJD patients

vCJD 和 sCJD 患者外周组织中朊病毒感染性的广泛分布

Douet, Jean-Yves; Huor, Alvina; Cassard, Hervé; Lugan, Séverine; Aron, Naima; Arnold, Mark; Vilette, Didier; Torres, Juan-Maria; Ironside, James W; Andreoletti, Olivier

Two distinct conformers of PrP(D) type 1 of sporadic Creutzfeldt-Jakob disease with codon 129VV genotype faithfully propagate in vivo

散发性克雅氏病中1型PrP(D)蛋白的两种不同构象异构体,其129VV密码子基因型,均能在体内忠实地遗传。

Cali, Ignazio; Espinosa, Juan Carlos; Nemani, Satish K; Marin-Moreno, Alba; Camacho, Manuel V; Aslam, Rabail; Kitamoto, Tetsuyuki; Appleby, Brian S; Torres, Juan Maria; Gambetti, Pierluigi

MicroRNA Alterations in a Tg501 Mouse Model of Prion Disease

Tg501小鼠朊病毒病模型中microRNA的改变

Toivonen, Janne M; Sanz-Rubio, David; López-Pérez, Óscar; Marín-Moreno, Alba; Bolea, Rosa; Osta, Rosario; Badiola, Juan J; Zaragoza, Pilar; Espinosa, Juan-Carlos; Torres, Juan-Maria; Martín-Burriel, Inmaculada

Prions from Sporadic Creutzfeldt-Jakob Disease Patients Propagate as Strain Mixtures

散发性克雅氏病患者的朊病毒以毒株混合物的形式传播

Cassard, Hervé; Huor, Alvina; Espinosa, Juan-Carlos; Douet, Jean-Yves; Lugan, Severine; Aron, Naima; Vilette, Didier; Delisle, Marie-Bernadette; Marín-Moreno, Alba; Peran, Patrice; Beringue, Vincent; Torres, Juan Maria; Ironside, James W; Andreoletti, Olivier

Correlation between Bioassay and Protein Misfolding Cyclic Amplification for Variant Creutzfeldt-Jakob Disease Decontamination Studies

变异型克雅氏病去污研究中生物测定与蛋白质错误折叠循环扩增的相关性

Bélondrade, Maxime; Jas-Duval, Christelle; Nicot, Simon; Bruyère-Ostells, Lilian; Mayran, Charly; Herzog, Laetitia; Reine, Fabienne; Torres, Juan Maria; Fournier-Wirth, Chantal; Béringue, Vincent; Lehmann, Sylvain; Bougard, Daisy

The emergence of classical BSE from atypical/Nor98 scrapie

经典疯牛病从非典型/Nor98羊瘙痒症中出现

Huor, Alvina; Espinosa, Juan Carlos; Vidal, Enric; Cassard, Hervé; Douet, Jean-Yves; Lugan, Séverine; Aron, Naima; Marín-Moreno, Alba; Lorenzo, Patricia; Aguilar-Calvo, Patricia; Badiola, Juan; Bolea, Rosa; Pumarola, Martí; Benestad, Sylvie L; Orge, Leonore; Thackray, Alana M; Bujdoso, Raymond; Torres, Juan-Maria; Andreoletti, Olivier

Regional and subtype-dependent miRNA signatures in sporadic Creutzfeldt-Jakob disease are accompanied by alterations in miRNA silencing machinery and biogenesis

散发性克雅氏病中区域性和亚型依赖性的miRNA特征伴随着miRNA沉默机制和生物合成的改变。

Llorens, Franc; Thüne, Katrin; Martí, Eulàlia; Kanata, Eirini; Dafou, Dimitra; Díaz-Lucena, Daniela; Vivancos, Ana; Shomroni, Orr; Zafar, Saima; Schmitz, Matthias; Michel, Uwe; Fernández-Borges, Natalia; Andréoletti, Olivier; Del Río, José Antonio; Díez, Juana; Fischer, Andre; Bonn, Stefan; Sklaviadis, Theodoros; Torres, Juan Maria; Ferrer, Isidre; Zerr, Inga

Prion Diseases in Animals and Zoonotic Potential

动物朊病毒疾病及其人畜共患病潜力

Torres, Juan Maria; Marin-Moreno, Alba; Andreoletti, Olivier; Espinosa, Juan-Carlos; Beringue, Vincent; Aguilar, Patricia; Fernandez-Borges, Natalia

Detection of infectivity in blood of persons with variant and sporadic Creutzfeldt-Jakob disease

检测变异型和散发型克雅氏病患者血液中的传染性

Douet, Jean Yves; Zafar, Saima; Perret-Liaudet, Armand; Lacroux, Caroline; Lugan, Séverine; Aron, Naima; Cassard, Herve; Ponto, Claudia; Corbière, Fabien; Torres, Juan Maria; Zerr, Inga; Andreoletti, Olivier