日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Loss of ADAMTS9 disrupts ciliogenesis and collagen homeostasis resulting in Nephronophthisis-like polycystic kidneys

ADAMTS9 的缺失会破坏纤毛发生和胶原蛋白稳态,导致类似肾痨的多囊肾。

Fischer, Sydney; Robert, Karyn L; Ahmed, Manu; Kane, Griffin I; Kavanaugh, Matthew A; Wang, Wei; Tran, Pamela V; Atukorale, Prabhani U; Nandadasa, Sumeda

Novel insights into palatal shelf elevation dynamics in normal mouse embryos.

对正常小鼠胚胎腭突抬升动态的新见解

Goering Jeremy P, Moedritzer Michael, Stetsiv Marta, Isai Dona Greta, Hufft-Martinez Brittany M, Tran An J, Umar Zaid, Rickabaugh Madison K, Keselman Paul, Chauhan Munish, Tran Pamela V, Brooks William M, Fischer Kenneth J, Czirok Andras, Saadi Irfan

Notch3 deletion regulates HIV-1 gene expression and systemic inflammation to ameliorate chronic kidney disease

Notch3 缺失通过调节 HIV-1 基因表达和全身炎症来改善慢性肾脏疾病

Thornton, Mackenzie; Sommer, Nicole; McGonigle, Mercedes; Kumar Ram, Anil; Yerrathota, Sireesha; Ehirim, Henrietta; Chaturvedi, Aakriti; Dinh Phan, Johnny; Chakraborty, Anubhav; Chakravarthi, V Praveen; Gunewardena, Sumedha; Tyagi, Mudit; Talreja, Jaya; Wang, Tao; Singhal, Pravin; Tran, Pamela V; Fields, Timothy A; Ray, Patricio E; Dhillon, Navneet K; Sharma, Madhulika

Targeting Ogt in ADPKD mitigates metabolic reprogramming and renal cystogenesis, extending survival

在常染色体显性多囊肾病(ADPKD)中靶向 Ogt 可减轻代谢重编程和肾囊肿形成,从而延长生存期。

Kavanaugh, Matthew A; Ahmad, Saleem; Isai, Dona Greta; Riddell, Heather A L; Assis, Amanda P; Ranganathan, Chadhve; Chaturvedi, Aakriti; Lam, Vincent; Muthineni, Nikhitha; Abid, Rayyan; Jurgensmeyer, Jenna E; Blades, Casey; Pritchard, Michele T; Sharma, Madhulika; Wallace, Darren P; Parnell, Stephen C; Slawson, Chad; Tran, Pamela V

Genetic interaction of Specc1l and Thm1 reveals cytoskeletal-ciliary crosstalk

Specc1l 和 Thm1 的基因相互作用揭示了细胞骨架-纤毛的串扰

Hufft-Martinez, Brittany M; Thalman, Dana N; Tran, An J; Goering, Jeremy P; Stetsiv, Marta; Moedritzer, Michael; Wilson, Sarah C; Wang, Henry H; Tran, Pamela V; Saadi, Irfan

Rag GTPases Suppress Renal Cystic Disease by Inhibiting TFEB Independently of mTORC1.

Rag GTP酶通过抑制TFEB抑制肾囊性疾病,且该过程独立于mTORC1

de Fatima Silva Flaviane, Boucher Alexander R Jr, Li Huawei, Chen Qingbo, Gaughan Maria, Korobkina Ekaterina D, Isidor Marie Sophie, Smith Abigail O, Shen Kuang, Allison Derek B, Tran Pamela V, Pazour Gregory J, Guertin David A

Pkd2 Deficiency in Embryonic Aqp2 + Progenitor Cells Is Sufficient to Cause Severe Polycystic Kidney Disease.

胚胎 Aqp2 + 祖细胞中 Pkd2 缺乏足以引起严重的多囊肾病

Tsilosani Akaki, Gao Chao, Chen Enuo, Lightle Andrea R, Shehzad Sana, Sharma Madhulika, Tran Pamela V, Bates Carlton M, Wallace Darren P, Zhang Wenzheng

Actin cytoskeletal regulation of ciliogenesis in development and disease

肌动蛋白细胞骨架对发育和疾病中纤毛发生的调控

Hufft-Martinez, Brittany M; Wang, Henry H; Saadi, Irfan; Tran, Pamela V

Corrigendum to "Ttc21b deficiency attenuates autosomal dominant polycystic kidney disease in a kidney tubular- and maturation-dependent manner." Kidney Int. 2022;102:577-591

对“Ttc21b 缺陷以肾小管和成熟依赖的方式减弱常染色体显性多囊肾病”一文的更正。肾脏国际杂志,2022;102:577-591

Wang, Wei; Silva, Luciane M; Wang, Henry H; Kavanaugh, Matthew A; Pottorf, Tana S; Allard, Bailey A; Jacobs, Damon T; Dong, Ruochen; Cornelius, Joseph T; Chaturvedi, Aakriti; Swenson-Fields, Katherine I; Fields, Timothy A; Pritchard, Michele T; Sharma, Madhulika; Slawson, Chad; Wallace, Darren P; Calvet, James P; Tran, Pamela V

SPECC1L: a cytoskeletal protein that regulates embryonic tissue dynamics

SPECC1L:一种调节胚胎组织动态的细胞骨架蛋白

Saadi, Irfan; Goering, Jeremy P; Hufft-Martinez, Brittany M; Tran, Pamela V