日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A novel computational model of human iPSC-derived ventricular myocytes with improved L-type calcium current for application to Timothy syndrome

一种新型的人类iPSC衍生心室肌细胞计算模型,具有改进的L型钙电流,可用于Timothy综合征的研究。

Simone, Francesca; Trancuccio, Alessandro; Sochacki, Jaroslaw Karol; Prieto, Celia Martínez; Priori, Silvia G; Pavarino, Luca F; Santiago, Demetrio J

Molecular insights into the rescue mechanism of an HERG activator against severe LQT2 mutations.

从分子层面揭示了 HERG 激活剂对抗严重 LQT2 突变的拯救机制

Kumawat Amit, Tavazzani Elisa, Lentini Giovanni, Trancuccio Alessandro, Kukavica Deni, Oldani Amanda, Denegri Marco, Priori Silvia G, Camilloni Carlo

Nutritional Factors and Arrhythmic Risk in Long QT Syndrome: A Narrative Review of Mechanistic and Clinical Evidence

营养因素与长QT间期综合征心律失常风险:机制和临床证据的叙述性综述

Mazzanti, Andrea; Floriano, Matteo; Kukavica, Deni; Trancuccio, Alessandro; Priori, Silvia G

Prognostic relevance of baseline exercise stress test in RYR2-related CPVT

RYR2相关儿茶酚胺敏感性室性心动过速(CPVT)中基线运动负荷试验的预后意义

Kukavica, Deni; Pili, Gianluca; Trancuccio, Alessandro; Giannini, Gala; Pergola, Valerio; Memmi, Mirella; Gambelli, Patrick; Marino, Maira; Morini, Massimo; Bloise, Raffaella; Napolitano, Carlo; Mazzanti, Andrea; Priori, Silvia G

Genetics in arrhythmogenic cardiomyopathies: where are we now and where are we heading to?

致心律失常性心肌病遗传学:我们现在处于什么阶段,我们将走向何方?

Mazzanti, Andrea; Kukavica, Deni; Trancuccio, Alessandro; Scilabra, Gabriele G; Coppini, Lucia; Pergola, Valerio; Tempo, Erika; Pili, Gianluca; Napolitano, Carlo; Priori, Silvia G

Implantable cardioverter defibrillator use in arrhythmogenic right ventricular cardiomyopathy in North America and Europe

北美和欧洲植入式心脏复律除颤器在致心律失常性右室心肌病中的应用

Carrick, Richard T; De Marco, Corrado; Gasperetti, Alessio; Bosman, Laurens P; Gourraud, Jean-Baptiste; Trancuccio, Alessandro; Mazzanti, Andrea; Murray, Brittney; Pendleton, Catherine; Tichnell, Crystal; Tandri, Harikrishna; Zeppenfeld, Katja; Wilde, Arthur A M; Davies, Brianna; Seifer, Colette; Roberts, Jason D; Healey, Jeff S; MacIntyre, Ciorsti; Alqarawi, Wael; Tadros, Rafik; Cutler, Michael J; Targetti, Mattia; Calò, Leonardo; Vitali, Francesco; Bertini, Matteo; Compagnucci, Paolo; Casella, Michela; Dello Russo, Antonio; Cappelletto, Chiara; De Luca, Antonio; Stolfo, Davide; Duru, Firat; Jensen, Henrik K; Svensson, Anneli; Dahlberg, Pia; Hasselberg, Nina E; Di Marco, Andrea; Jordà, Paloma; Arbelo, Elena; Moreno Weidmann, Zoraida; Borowiec, Karolina; Delinière, Antoine; Biernacka, Elżbieta K; van Tintelen, J Peter; Platonov, Pyotr G; Olivotto, Iacopo; Saguner, Ardan M; Haugaa, Kristina H; Cox, Moniek; Tondo, Claudio; Merlo, Marco; Krahn, Andrew D; Te Riele, Anneline S J M; Wu, Katherine C; Calkins, Hugh; James, Cynthia A; Cadrin-Tourigny, Julia

A novel computational model of swine ventricular myocyte reveals new insights into disease mechanisms and therapeutic approaches in Timothy Syndrome.

一种新型的猪心室肌细胞计算模型揭示了蒂莫西综合征的疾病机制和治疗方法的新见解

Trancuccio Alessandro, Tarifa Carmen, Bongianino Rossana, Priori Silvia G, Santiago Demetrio J

Transmural APD heterogeneity determines ventricular arrhythmogenesis in LQT8 syndrome: Insights from Bidomain computational modeling

跨壁动作电位时程异质性决定了LQT8综合征的室性心律失常发生:来自双域计算模型的启示

Scacchi, Simone; Pavarino, Luca F; Mazzanti, Andrea; Trancuccio, Alessandro; Priori, Silvia G; Colli Franzone, Piero

Unexpected impairment of INa underpins reentrant arrhythmias in a knock-in swine model of Timothy syndrome

意外的 INa 损伤是 Timothy 综合征敲入猪模型中折返性心律失常的基础

Andreu Porta-Sánchez #, Andrea Mazzanti #, Carmen Tarifa #, Deni Kukavica #, Alessandro Trancuccio #, Muhammad Mohsin, Elisa Zanfrini, Andrea Perota, Roberto Duchi, Kevin Hernandez-Lopez, Miguel Eduardo Jáuregui-Abularach, Valerio Pergola, Eugenio Fernandez, Rossana Bongianino, Elisa Tavazzani, Patr

Arrhythmic risk prediction in arrhythmogenic right ventricular cardiomyopathy: external validation of the arrhythmogenic right ventricular cardiomyopathy risk calculator

心律失常性右室心肌病心律失常风险预测:心律失常性右室心肌病风险计算器的外部验证

Jordà, Paloma; Bosman, Laurens P; Gasperetti, Alessio; Mazzanti, Andrea; Gourraud, Jean Baptiste; Davies, Brianna; Frederiksen, Tanja Charlotte; Weidmann, Zoraida Moreno; Di Marco, Andrea; Roberts, Jason D; MacIntyre, Ciorsti; Seifer, Colette; Delinière, Antoine; Alqarawi, Wael; Kukavica, Deni; Minois, Damien; Trancuccio, Alessandro; Arnaud, Marine; Targetti, Mattia; Martino, Annamaria; Oliviero, Giada; Pipilas, Daniel C; Carbucicchio, Corrado; Compagnucci, Paolo; Dello Russo, Antonio; Olivotto, Iacopo; Calò, Leonardo; Lubitz, Steven A; Cutler, Michael J; Chevalier, Philippe; Arbelo, Elena; Priori, Silvia Giuliana; Healey, Jeffrey S; Calkins, Hugh; Casella, Michela; Jensen, Henrik Kjærulf; Tondo, Claudio; Tadros, Rafik; James, Cynthia A; Krahn, Andrew D; Cadrin-Tourigny, Julia