Targeted deletion of the AAA-ATPase Ruvbl1 in mice disrupts ciliary integrity and causes renal disease and hydrocephalus
在小鼠中靶向删除 AAA-ATPase Ruvbl1 会破坏纤毛完整性并导致肾脏疾病和脑积水
期刊:Experimental and Molecular Medicine
影响因子:9.5
doi:10.1038/s12276-018-0108-z
Claudia Dafinger, Markus M Rinschen, Lori Borgal, Carolin Ehrenberg, Sander G Basten, Mareike Franke, Martin Höhne, Manfred Rauh, Heike Göbel, Wilhelm Bloch, F Thomas Wunderlich, Dorien J M Peters, Dirk Tasche, Tripti Mishra, Sandra Habbig, Jörg Dötsch, Roman-Ulrich Müller, Jens C Brüning, Thorsten