日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

How Congenital Skin Lesions Are Perceived by Health Professionals in the Delivery Room-The Reconnaissance Study

产房医护人员如何看待先天性皮肤损伤——初步研究

Berthelot, Brieuc; Prémel, Juliette; Pichereau, Maud; Moulinier, Emma; Vabres, Pauline; Martin, Ludovic

A postzygotic GNA13 variant upregulates the RHOA/ROCK pathway and alters melanocyte function in a mosaic skin hypopigmentation syndrome

合子后 GNA13 变异上调 RHOA/ROCK 通路并改变马赛克皮肤色素减退综合征中的黑素细胞功能

Rana El Masri, Alberto Iannuzzo, Paul Kuentz, Rachida Tacine, Marie Vincent, Sébastien Barbarot, Fanny Morice-Picard, Franck Boralevi, Naia Oillarburu, Juliette Mazereeuw-Hautier, Yannis Duffourd, Laurence Faivre, Arthur Sorlin, Pierre Vabres #, Jérôme Delon #6

Characteristics and Therapeutic Strategies for Diffuse Cutaneous Mastocytosis

弥漫性皮肤肥大细胞增生症的特征和治疗策略

Pernea, Paula; Méni, Cecile; Rossignol, Julien; Aubert, Hélène; Barbarot, Sébastien; Bellon, Nathalia; Bing-Lecointe, Anne-Claire; Bonigen, Julie; Bursztejn, Anne-Claire; Carré, Delphine; Phan, Alice; Puzenat, Eve; Skowron, François; Vabres, Pierre; Welfringer-Morin, Anne; Drabent, Philippe; Fraitag, Sylvie; Garcelon, Nicolas; Agopian, Julie; Dubreuil, Patrice; Mallet, Stéphanie; Barete, Stéphane; Arock, Michel; Hermine, Olivier; Bodemer, Christine; Polivka, Laura

Long-Term Efficacy and Safety of Rituximab in Patients With Pemphigus Foliaceus Compared With Pemphigus Vulgaris

利妥昔单抗治疗落叶型天疱疮与寻常型天疱疮的长期疗效和安全性比较

Tedbirt, Billal; Houivet, Estelle; Maho-Vaillant, Maud; Golinski, Marie-Laure; Calbo, Sébastien; Prost-Squarcioni, Catherine; Labeille, Bruno; Picard-Dahan, Catherine; Chaby, Guillaume; Richard, Marie-Aleth; Tancrède-Bohin, Emmanuelle; Duvert-Lehembre, Sophie; Delaporte, Emmanuel; Bernard, Philippe; Caux, Frédéric; Alexandre, Marina; Musette, Philippe; Ingen-Housz-Oro, Saskia; Vabres, Pierre; Quereux, Gaëlle; Dupuy, Alain; Debarbieux, Sébastien; Avenel-Audran, Martine; D'Incan, Michel; Bédane, Christophe; Bénéton, Nathalie; Jullien, Denis; Dupin, Nicolas; Misery, Laurent; Machet, Laurent; Beylot-Barry, Marie; Dereure, Olivier; Sassolas, Bruno; Cordel, Nadège; Jeudy, Géraldine; Benichou, Jacques; Hébert, Vivien; Joly, Pascal

Laser Processing of Ti Contacts for Ohmic Behavior on P‑Type 4H-SiC

采用激光加工技术在 P 型 4H-SiC 上制备具有欧姆特性的钛触点

Vabres, Roberto; Bellocchi, Gabriele; Bongiorno, Corrado; Vivona, Marilena; Roccaforte, Fabrizio; Badalà, Paolo; Mancuso, Paola; Puglisi, Valeria; Rascunà, Simone; Crupi, Isodiana

Incontinentia pigmenti underlies thymic dysplasia, autoantibodies to type I IFNs, and viral diseases

色素失禁症是胸腺发育不良、I型干扰素自身抗体和病毒性疾病的病因。

Jérémie Rosain ,Tom Le Voyer # ,Xian Liu # ,Adrian Gervais # ,Laura Polivka # ,Axel Cederholm # ,Laureline Berteloot # ,Audrey V Parent # ,Alessandra Pescatore # ,Ezia Spinosa # ,Snezana Minic # ,Ana Elisa Kiszewski # ,Miyuki Tsumura # ,Chloé Thibault # ,Maria Esnaola Azcoiti # ,Jelena Martinovic # ,Quentin Philippot # ,Taushif Khan # ,Astrid Marchal # ,Bénédicte Charmeteau-De Muylder # ,Lucy Bizien # ,Caroline Deswarte # ,Lillia Hadjem ,Marie-Odile Fauvarque ,Karim Dorgham ,Daniel Eriksson ,Emilia Liana Falcone ,Mathilde Puel ,Sinem Ünal ,Amyrath Geraldo ,Corentin Le Floc'h ,Hailun Li ,Sylvie Rheault ,Christine Muti ,Claire Bobrie-Moyrand ,Anne Welfringer-Morin ,Ramsay L Fuleihan ,Romain Lévy ,Marie Roelens ,Liwei Gao ,Marie Materna ,Silvia Pellegrini ,Lorenzo Piemonti ,Emilie Catherinot ,Jean-Christophe Goffard ,Arnaud Fekkar ,Aissata Sacko-Sow ,Camille Soudée ,Soraya Boucherit ,Anna-Lena Neehus ,Cristina Has ,Stefanie Hübner ,Géraldine Blanchard-Rohner ,Blanca Amador-Borrero ,Takanori Utsumi ,Maki Taniguchi ,Hiroo Tani ,Kazushi Izawa ,Takahiro Yasumi ,Sotaro Kanai ,Mélanie Migaud ,Mélodie Aubart ,Nathalie Lambert ,Guy Gorochov ,Capucine Picard ,Claire Soudais ,Anne-Sophie L'Honneur ,Flore Rozenberg ,Joshua D Milner ,Shen-Ying Zhang ,Pierre Vabres ,Dusan Trpinac ,Nico Marr ,Nathalie Boddaert ,Isabelle Desguerre ,Manolis Pasparakis ,Corey N Miller ,Cláudia S Poziomczyk ,Laurent Abel ,Satoshi Okada ,Emmanuelle Jouanguy ,Rémi Cheynier ,Qian Zhang ,Aurélie Cobat ,Vivien Béziat ,Bertrand Boisson ,Julie Steffann ,Francesca Fusco ,Matilde Valeria Ursini ,Smail Hadj-Rabia ,Christine Bodemer ,Jacinta Bustamante ,Hervé Luche ,Anne Puel # ,Gilles Courtois # ,Paul Bastard # ,Nils Landegren # ,Mark S Anderson # ,Jean-Laurent Casanova #

Sustained Remission Without Corticosteroids Among Patients With Pemphigus Who Had Rituximab as First-Line Therapy: Follow-Up of the Ritux 3 Trial

利妥昔单抗一线治疗天疱疮患者无需使用皮质类固醇即可持续缓解:Ritux 3 试验的随访

Tedbirt, Billal; Maho-Vaillant, Maud; Houivet, Estelle; Mignard, Claire; Golinski, Marie-Laure; Calbo, Sébastien; Prost-Squarcioni, Catherine; Labeille, Bruno; Picard-Dahan, Catherine; Chaby, Guillaume; Richard, Marie-Aleth; Tancrede-Bohin, Emmanuelle; Duvert-Lehembre, Sophie; Delaporte, Emmanuel; Bernard, Philippe; Caux, Frédéric; Alexandre, Marina; Musette, Philippe; Ingen-Housz-Oro, Saskia; Vabres, Pierre; Quereux, Gaëlle; Dupuy, Alain; Debarbieux, Sébastien; Avenel-Audran, Martine; D'Incan, Michel; Bédane, Christophe; Bénéton, Nathalie; Jullien, Denis; Dupin, Nicolas; Misery, Laurent; Machet, Laurent; Beylot-Barry, Marie; Dereure, Olivier; Sassolas, Bruno; Benichou, Jacques; Joly, Pascal; Hébert, Vivien

A phase II double-blind multicentre, placebo-controlled trial to assess the efficacy and safety of alpelisib (BYL719) in paediatric and adult patients with Megalencephaly-CApillary malformation Polymicrogyria syndrome (MCAP): the SESAM study protocol

一项评估alpelisib (BYL719)治疗巨脑畸形-毛细血管畸形-多小脑回综合征 (MCAP) 儿童和成人患者的疗效和安全性的II期双盲多中心安慰剂对照试验:SESAM研究方案

Luu, Maxime; Vabres, Pierre; Espitalier, Aurélie; Maurer, Agnès; Garde, Aurore; Racine, Caroline; Carpentier, Maud; Rega, Adélaide; Loffroy, Romaric; Hadouiri, Nawale; Boddaert, Nathalie; Curie, Aurore; Guibaud, Laurent; Chebbi, Mouna; Charligny, Julie; Kuentz, Paul; Canaud, Guillaume; Bahi-Buisson, Nadia; Fleck, Camille; Cransac, Amelie; Bardou, Marc; Faivre, Laurence

Outcomes after reversed corneal graft rejection: a report from the European VISICORT project

逆转角膜移植排斥反应后的结局:来自欧洲VISICORT项目的一份报告

Iselin, Katja C; Hjortdal, Jesper; Armitage, W John; Tole, Derek; Pleyer, Uwe; Vabres, Bertrand; Griffin, Matthew D; Murphy, Conor C

PTPN11 Mosaicism Causes a Spectrum of Pigmentary and Vascular Neurocutaneous Disorders and Predisposes to Melanoma

PTPN11 嵌合体可导致一系列色素性和血管性神经皮肤疾病,并易患黑色素瘤

Satyamaanasa Polubothu,Nicole Bender,Siobhan Muthiah,Davide Zecchin,Charalambos Demetriou,Sara Barberan Martin,Sony Malhotra,Jana Travnickova,Zhiqiang Zeng,Markus Böhm,Sebastien Barbarot,Catherine Cottrell,Olivia Davies,Eulalia Baselga,Nigel P Burrows,Virginie Carmignac,Joey Santiago Diaz,Christine Fink,Holger A Haenssle,Rudolf Happle,Mark Harland,Jacquelyn Majerowski,Pierre Vabres,Marie Vincent,Julia A Newton-Bishop,D Tim Bishop,Dawn Siegel,E Elizabeth Patton,Maya Topf,Neil Rajan,Beth Drolet,Veronica A Kinsler