日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Somatic deficiency of the human E3 ubiquitin ligase CBL in leukocytes impairs B cell but not T cell development and function.

白细胞中人类 E3 泛素连接酶 CBL 的体细胞缺陷会损害 B 细胞的发育和功能,但不会影响 T 细胞的发育和功能。

Vatovec Taja, Neehus Anna-Lena, Jackson Katherine J L, Avery Danielle T, Bagarić Ivan, Erazo Lucia, Arango-Franco Carlos A, Ogishi Masato, Ahmed Syed F, Cederholm Axel, Russell Amanda J, Della Mina Erika, Al-Rifai Dena, Bull Rowena, Buetow Lori, Sobrino Steicy, Zhang Allison, Wahlster Lara, Michelet Marine, Parvaneh Nima, Peel Jessica, Barzaghi Federica, Leardini Davide, Philippot Quentin, Saettini Francesco, Dutrieux Jacques, de Muylder Benedicte, Vendemini Francesca, Baccelli Francesco, Catala Albert, Gambineri Eleonora, Veltroni Marinella, Pandiarajan Vignesh, Aguilar Yurena, Haerynck Filomeen, Elliott Michael, Turville Stuart, Brillot Fabienne, Khan Taushif, Consonni Filippo, Berteloot Laureline, Sewell William A, Rao Geetha, Largeaud Laetitia, Conti Francesca, Roullion Cecile, Masson Cécile, Pegoraro Francesco, Ye Tianyi, Joubran Samantha, Villalpando Emily, Bessot Boris, Seeleuthner Yoann, Le Voyer Tom, Rosain Jérémie, Li Hailun, Janda Zarah, Muratore Edoardo, Soudée Camille, Delabesse Eric, Goulvestre Claire, Shahrooei Mohammad, Puel Anne, André Isabelle, Bole-Feysot Christine, Abel Laurent, Erlacher Miriam, Béziat Vivien, Lagresle-Peyrou Chantal, Cheynier Remi, Six Emmanuelle, Marr Nico, Pasquet Marlène, Alsina Laia, Goodnow Christopher C, Landegren Nils, Aiuti Alessandro, Zhang Peng, Masetti Riccardo, Huang Danny T, Ma Cindy S, Casanova Jean-Laurent, Sankaran Vijay G, Bustamante Jacinta, Tangye Stuart G, Bohlen Jonathan

Bone Marrow CD8 + Abundance Inversely Correlates with Progressive Marrow Fibrosis and Myelodysplastic Evolution in GATA2 Deficiency: Case Report

GATA2缺陷患者骨髓CD8+细胞丰度与进行性骨髓纤维化和骨髓增生异常综合征进展呈负相关:病例报告

Vendemini, Francesca; Roncareggi, Samuele; L'Imperio, Vincenzo; Guerra, Fabiola; Mottadelli, Federica; Chiarini, Marco; Maglia, Oscar; Sala, Simona; Fazio, Grazia; Piazza, Rocco; Bonanomi, Sonia; Biondi, Andrea; Saettini, Francesco

Outcomes of children with haematological malignancies given second haploidentical haematopoietic stem cell transplantation with either TCRαβ/CD19 depletion or post-transplant cyclophosphamide

接受第二次单倍体造血干细胞移植治疗血液系统恶性肿瘤患儿,并分别采用TCRαβ/CD19耗竭或移植后环磷酰胺治疗的疗效

Masetti, Riccardo; Leardini, Davide; Gottardi, Francesca; Baccelli, Francesco; Ottaviano, Giorgio Antonio Maria; Vendemini, Francesca; Saglio, Francesco; Pierri, Filomena; Algeri, Mattia; Del Bufalo, Francesca; Merli, Pietro; Prete, Arcangelo; Cesaro, Simone; Ussowicz, Marek; Faraci, Maura; Zecca, Marco; Fagioli, Franca; Balduzzi, Adriana; Dalle, Jean-Hugues; Locatelli, Franco; Pagliara, Daria

Autoinflammation in patients with leukocytic CBL loss of heterozygosity is caused by constitutive ERK-mediated monocyte activation

白细胞性CBL杂合性缺失患者的自身炎症是由组成型ERK介导的单核细胞活化引起的。

Bohlen, Jonathan; Bagarić, Ivan; Vatovec, Taja; Ogishi, Masato; Ahmed, Syed F; Cederholm, Axel; Buetow, Lori; Sobrino, Steicy; Le Floc'h, Corentin; Arango-Franco, Carlos A; Seabra, Luis; Michelet, Marine; Barzaghi, Federica; Leardini, Davide; Saettini, Francesco; Vendemini, Francesca; Baccelli, Francesco; Catala, Albert; Gambineri, Eleonora; Veltroni, Marinella; Aguilar de la Red, Yurena; Rice, Gillian I; Consonni, Filippo; Berteloot, Laureline; Largeaud, Laetitia; Conti, Francesca; Roullion, Cécile; Masson, Cécile; Bessot, Boris; Seeleuthner, Yoann; Le Voyer, Tom; Rinchai, Darawan; Rosain, Jérémie; Neehus, Anna-Lena; Erazo-Borrás, Lucia; Li, Hailun; Janda, Zarah; Cho, En-Jui; Muratore, Edoardo; Soudée, Camille; Lainé, Candice; Delabesse, Eric; Goulvestre, Claire; Ma, Cindy S; Puel, Anne; Tangye, Stuart G; André, Isabelle; Bole-Feysot, Christine; Abel, Laurent; Erlacher, Miriam; Zhang, Shen-Ying; Béziat, Vivien; Lagresle-Peyrou, Chantal; Six, Emmanuelle; Pasquet, Marlène; Alsina, Laia; Aiuti, Alessandro; Zhang, Peng; Crow, Yanick J; Landegren, Nils; Masetti, Riccardo; Huang, Danny T; Casanova, Jean-Laurent; Bustamante, Jacinta

Safety and efficacy of narsoplimab in pediatric and adult patients with transplant-associated thrombotic microangiopathy: a real-world experience

narsoplimab治疗移植相关血栓性微血管病患儿及成人患者的安全性和有效性:一项真实世界研究

Castelli, Marta; Micò, Maria Caterina; Grassi, Anna; Algarotti, Alessandra; Lussana, Federico; Finazzi, Maria Chiara; Rambaldi, Benedetta; Pavoni, Chiara; Rizzuto, Giuliana; Tebaldi, Paola; Vendemini, Francesca; Verna, Marta; Bonanomi, Sonia; Biondi, Andrea; Balduzzi, Adriana; Rambaldi, Alessandro; Gotti, Giacomo

Mutations of SETBP1 and JAK3 in juvenile myelomonocytic leukemia: a report from the Italian AIEOP study group

SETBP1 和 JAK3 基因突变与幼年型骨髓单核细胞白血病:意大利 AIEOP 研究组的报告

Bresolin, Silvia; De Filippi, Paola; Vendemini, Francesca; D'Alia, Mirko; Zecca, Marco; Meyer, Lueder H; Danesino, Cesare; Locatelli, Franco; Masetti, Riccardo; Basso, Giuseppe; Te Kronnie, Geertruy

Impact of inflammatory cytokine gene polymorphisms on developing acute graft-versus-host disease in children undergoing allogeneic hematopoietic stem cell transplantation

炎症细胞因子基因多态性对接受异基因造血干细胞移植的儿童发生急性移植物抗宿主病的影响

Masetti, Riccardo; Zama, Daniele; Urbini, Milena; Astolfi, Annalisa; Libri, Virginia; Vendemini, Francesca; Morello, William; Rondelli, Roberto; Prete, Arcangelo; Pession, Andrea

MYCN is a novel oncogenic target in pediatric T-cell acute lymphoblastic leukemia

MYCN是儿童T细胞急性淋巴细胞白血病中一种新的致癌靶点

Astolfi, Annalisa; Vendemini, Francesca; Urbini, Milena; Melchionda, Fraia; Masetti, Riccardo; Franzoni, Monica; Libri, Virginia; Serravalle, Salvatore; Togni, Marco; Paone, Giuseppina; Montemurro, Luca; Bressanin, Daniela; Chiarini, Francesca; Martelli, Alberto M; Tonelli, Roberto; Pession, Andrea

PS2-08: “I Didn’t Know They Did That!” Discovering and Maximizing the Capacity of the HMO Research Network

PS2-08:“我不知道他们还做这个!” 发现并最大限度地发挥 HMO 研究网络的能力

Cattoni, Alessandro; Nicolosi, Maria Laura; Capitoli, Giulia; Gadda, Alberto; Molinari, Silvia; Louka, Sotiris; Buonsante, Andrea; Orlandi, Simona; Salierno, Gianluca; Bellani, Iacopo; Vendemini, Francesca; Ottaviano, Giorgio; Gaiero, Alberto; Fichera, Graziella; Biondi, Andrea; Balduzzi, Adriana; Iqbal, Zahra; Agrawal, Rajeev; Odom, Joanne; Rethy, Janine; Walter, Grace; Jabbarpour, Yalda; Siddiqi, Anam; Huffstetler, Alison; Carvajal, Diana; Ronis, Sarah; Stange, Kurt; Kleinman, Lawrence; Thompson, Ella; Greene, Sarah; Johnson, Karin; Larson, Eric; Steiner, John