日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Pretreatment serum bile acid composition and predictability of subsequent response to odevixibat in patients with bile salt export pump (BSEP) deficiency

胆汁酸输出泵(BSEP)缺乏症患者治疗前血清胆汁酸组成与后续对奥德维西巴治疗反应的预测性

Nomden, Mark; Kuipers, Folkert; Lexmond, Willem S; Gu, Tao; Valcheva, Velichka; Lindström, Erik; Verkade, Henkjan J

FGF1 ameliorates hepatic steatosis through acute activation of the unfolded protein response and VLDL production

FGF1通过急性激活未折叠蛋白反应和VLDL生成来改善肝脂肪变性。

van Zutphen, Tim; Struik, Dicky; Liu, Weilin; Liu, Sihao; Sermikli, Benan Pelin; Wolters, Justina C; Verkade, Henkjan J; Atkins, Annette R; Downes, Michael; Evans, Ronald M; Jonker, Johan W

The conjugation-resistant bile acid norUDCA cures liver fibrosis but impairs systemic energy metabolism

抗结合胆汁酸norUDCA可治愈肝纤维化,但会损害全身能量代谢。

Evangelakos, Ioannis; Verkade, Esther; Rohde, Julia K; Zaufel, Alex; Vargek, Martin; Heine, Markus; Worthmann, Anna; Graute, Sebastian; Manka Fuh, Marceline; Gunasekaran, Karthikeyan; Kumari, Manju; Schwinge, Dorothee; von Bergen, Martin; Rolle-Kampczyk, Ulrike; Engelmann, Beatrice; Breinbauer, Rolf; Fuerst, Rita; Saleem, Umber; de Boer, Jan Freark; Schlein, Christian; Hansen, Arne; Scheja, Ludger; Kuipers, Folkert; Moustafa, Tarek; Heeren, Joerg

Farnesoid x Receptor Deficiency Promotes Hepatocytic Injury in Cyp2c70-Deficient Mice With a Human-Like Bile Acid Composition

法尼醇X受体缺陷会促进Cyp2c70缺陷小鼠(其胆汁酸组成与人类相似)的肝细胞损伤。

de Vries, Hilde D; Li, Jinxiao; Ustyantsev, Kirill; Hovingh, Milaine V; Mulder, Niels L; Havinga, Rick; Palmiotti, Anna; de Bruyn, Krisztina; Attema, Brecht; Weersing, Ellen; Thomas, Rachel E; Bloks, Vincent W; Berezikov, Eugene; van Faassen, Martijn; Verkade, Henkjan J; de Boer, Jan Freark; Kuipers, Folkert

Subconjunctival Triamcinolone Acetonide Injection Compared with Dexamethasone Ophthalmic Insert for Inflammation Prophylaxis After Cataract Surgery: A Comparative Clinical Study

结膜下注射曲安奈德与地塞米松滴眼液用于白内障术后炎症预防的比较:一项临床研究

Gannamaneni, Kartik; Reddy, Karthik; Shapiro, Jeremy N; Levine, Harry; Verkade, Angela J; Armenti, Stephen T; Hood, Christopher T; Mian, Shahzad I

P-1787. Tailor Swiftly: Lessons Learned from a Nationwide Implementation of an Antimicrobial Stewardship Program for Asymptomatic Bacteriuria

P-1787. 迅速调整:从全国范围内实施无症状菌尿抗菌药物管理计划中汲取的经验教训

Peddie, Christopher J; Genoud, Christel; Kreshuk, Anna; Meechan, Kimberly; Micheva, Kristina D; Narayan, Kedar; Pape, Constantin; Parton, Robert G; Schieber, Nicole L; Schwab, Yannick; Titze, Benjamin; Verkade, Paul; Aubrey, Aubrey; Collinson, Lucy M; Wang, Shiyang; Liechty, Benjamin; Patel, Seema; Weber, Jeffrey; Hollman, Travis; Snuderl, Matija; Karajannis, Matthias; Amenta, Eva; Haltom, Trenton M; Donnelly, John P; Braund, Sophia; Hernandez, Rogelio; Chou, Andrew; Brehm, Tyler; Stevens, Vanessa W; Trautner, Barbara

Condition-Specific Growth Charts for Children With Alagille Syndrome

阿拉吉尔综合征患儿的特定生长曲线图

Huysentruyt, Koen; Vandriel, Shannon M; Roelants, Mathieu; Piccoli, David A; Loomes, Kathleen M; Rand, Elizabeth B; Ebel, Noelle H; Feinstein, Jeffrey A; Jankowska, Irena; Czubkowski, Piotr; Gliwicz-Miedzinska, Dorota; Gonzales, Emmanuel M; Jacquemin, Emmanuel; Bouligand, Jérôme; Karpen, Saul J; Romero, Rene; Lin, Henry C; Fischler, Björn; Arnell, Henrik; Li, Li-Ting; Wang, Jian-She; Fawaz, Rima; Nastasio, Silvia; Kim, Kyung Mo; Oh, Seak Hee; D'Antiga, Lorenzo; Nicastro, Emanuele; Fischer, Ryan T; Siew, Susan M; Stormon, Michael; Lertudomphonwanit, Chatmanee; Hardikar, Winita; Shankar, Sahana; Squires, James E; Sundaram, Shikha S; Larson-Nath, Catherine; Kelly, Deirdre A; Hartley, Jane; Bulut, Pinar; Jensen, M Kyle; Jaramillo, Catalina; Roberts, Amin J; Evans, Helen M; Sokal, Étienne M; Demaret, Tanguy; Verkade, Henkjan J; Thompson, Richard J; Hansen, Bettina E; Cole, Tim J; Kamath, Binita M; Debray, Dominique; Lacaille, Florence; Brecelj, Jernej; El-Koofy, Nehal M; Elmonem, Mohamed A; Lee, Way Seah; Sanchez, Maria Camila; Cavalieri, Maria Lorena; Hajinicolaou, Christina; Schwarz, Kathleen B; Carvalho, Elisa; Rock, Nathalie; Karnsakul, Wikrom; Quiros-Tejeira, Ruben E; Alam, Seema; Nebbia, Gabriella; Mozer-Glassberg, Yael; Valentino, Pamela L; Santos-Silva, Ermelinda; Önal, Zerrin; Dezsofi-Gottl, Antal; Melere, Melina; Legarda Tamara, María; Eshun, John; Zellos, Aglaia; Indolfi, Giuseppe; Rogalidou, Maria; Blondet, Niviann; Luigi Calvo, Pier; Beretta, Marisa; Zizzo, Andréanne N; Arikan, Cigdem; Kasahara, Mureo; Kerkar, Nanda; Aqul, Amal A; Wolters, Victorien M; Borges Pinto, Raquel; Quintero Bernabeu, Jesus; Garcia, Jennifer; Wiecek, Sabina; Tzivinikos, Christos; Mujawar, Quais; Jimenez-Rivera, Carolina; Molera Busoms, Cristina; Gonçalves, Cristina; Bujanda, Luis

Factors Associated with Vision Outcomes in Microbial Keratitis: A Multisite Prospective Cohort Study

微生物性角膜炎视力预后相关因素:一项多中心前瞻性队列研究

Woodward, Maria A; Vogt, Emily L; Niziol, Leslie M; Mian, Shahzad I; Sugar, Alan; Verkade, Angela; Nallasamy, Nambi; Pawar, Mercy; Kang, Linda; Miller, Keith D; Winter, Suzanne; Farsiu, Sina; Prajna, N Venkatesh

Phenotypic Divergence of JAG1- and NOTCH2-Associated Alagille Syndrome & Disease-Specific NOTCH2 Variant Classification Guidelines

JAG1 和 NOTCH2 相关阿拉吉尔综合征的表型差异及疾病特异性 NOTCH2 变异分类指南

Vandriel, Shannon M; Li, Li-Ting; She, Huiyu; Wang, Jian-She; Loomes, Kathleen M; Piccoli, David A; Jankowska, Irena; Czubkowski, Piotr; Gliwicz-Miedzińska, Dorota; D'Antiga, Lorenzo; Nicastro, Emanuele; Lacaille, Florence; Debray, Dominique; Sokal, Étienne M; Demaret, Tanguy; Fawaz, Rima L; Nastasio, Silvia; Kim, Kyung Mo; Oh, Seak Hee; Fischler, Björn; Arnell, Henrik; Larson-Nath, Catherine; Hardikar, Winita; Shankar, Sahana; Sundaram, Shikha S; Chaidez, Alexander; Bulut, Pinar; Calvo, Pier Luigi; Kasahara, Mureo; Blondet, Niviann; Lurz, Eberhard; Kavallar, Anna-Maria; Gonzales, Emmanuel M; Jacquemin, Emmanuel; Bouligand, Jérôme; Ebel, Noelle H; Feinstein, Jeffrey A; Siew, Susan M; Stormon, Michael O; Karpen, Saul J; Romero, Rene; Jensen, M Kyle; Jaramillo, Catalina; Squires, James E; Bedoyan, Sarah M; Kelly, Deirdre A; Hartley, Jane; Verkade, Henkjan J; Lee, Way Seah; Lertudomphonwanit, Chatmanee; Fischer, Ryan T; Lin, Henry C; Rock, Nathalie; Mozer-Glassberg, Yael; Roberts, Amin J; Evans, Helen M; Karnsakul, Wikrom; Nebbia, Gabriella; Wolters, Victorien M; Valentino, Pamela L; Bernabeu, Jesus Quintero; Aqul, Amal A; Arikan, Cigdem; Tamara, María Legarda; Busoms, Cristina Molera; Sandahl, Thomas Damgaard; Indolfi, Giuseppe; Zizzo, Andréanne N; Zellos, Aglaia; Quiros-Tejeira, Ruben E; Santos-Silva, Ermelinda; Schwarz, Kathleen B; Brecelj, Jernej; Sanchez, Maria Camila; Cavalieri, Maria Lorena; Tzivinikos, Christos; Wiecek, Sabina; Eshun, John; Kerkar, Nanda; Mujawar, Quais; Önal, Zerrin; Gonçalves, Cristina; Garcia, Jennifer; Alam, Seema; Jimenez-Rivera, Carolina; Bujanda, Luis; Thompson, Richard J; Hansen, Bettina E; Spinner, Nancy B; Gilbert, Melissa A; Kamath, Binita M

Elevated Serum Bile Acids Predict Poor Liver Outcomes in Children With Alagille Syndrome: Results From the GALA Study Group

血清胆汁酸水平升高预示阿拉吉勒综合征患儿肝脏预后不良:GALA研究组的结果

Perez, Carla Fiorella Murillo; Vandriel, Shannon M; Gonzales, Emmanuel M; Wang, Jian-She; Li, Li-Ting; She, Huiyu; Jankowska, Irena; Czubkowski, Piotr; Gliwicz-Miedzińska, Dorota; Jacquemin, Emmanuel; Bouligand, Jérôme; D'Antiga, Lorenzo; Nicastro, Emanuele; Fischler, Björn; Arnell, Henrik; Siew, Susan M; Stormon, Michael; Loomes, Kathleen M; Piccoli, David A; Rand, Elizabeth B; Squires, James E; Karpen, Saul J; Romero, Rene; Kasahara, Mureo; Önal, Zerrin; Sokal, Étienne; Demaret, Tanguy; Wiecek, Sabina; Lacaille, Florence; Debray, Dominique; Hardikar, Winita; Shankar, Sahana; Valentino, Pamela L; Sundaram, Shikha S; Ebel, Noelle H; Feinstein, Jeffrey A; Waisbourd-Zinman, Orith; Lin, Henry C; Rock, Nathalie; Verkade, Henkjan J; Jensen, M Kyle; Jaramillo, Catalina; Kim, Kyung Mo; Oh, Seak Hee; Brecemiclj, Jernej; Alam, Seema; Indolfi, Giuseppe; Blondet, Niviann; Fawaz, Rima; Nastasio, Silvia; Calvo, Pier Luigi; Nebbia, Gabriella; Arikan, Cigdem; Larson-Nath, Catherine; Zizzo, Andréanne N; Sandahl, Thomas Damgaard; Tzivinikos, Christos; El-Koofy, Nehal M; Elmonem, Mohamed A; Aqul, Amal A; Karnsakul, Wikrom; Bulut, Pinar; Kerkar, Nanda; Wolters, Victorien M; Roberts, Amin J; Evans, Helen M; Sanchez, Maria Camila; Cavalieri, Maria Lorena; Kelly, Deirdre A; Hartley, Jane; Lee, Way Seah; Hajinicolaou, Christina; Lertudomphonwanit, Chatmanee; Fischer, Ryan T; Bernabeu, Jesus Quintero; Quiros-Tejeira, Ruben E; Ferreira, Cristina Targa; Carvalho, Elisa; Eshun, John; Zellos, Aglaia; Dezsőfi, Antal; Pinto, Raquel Borges; Schwarz, Kathleen; Rogalidou, Maria; Garcia, Jennifer; Tamara, María Legarda; Beretta, Marisa; Mujawar, Quais; Santos-Silva, Ermelinda; Busoms, Cristina Molera; Lurz, Eberhard; Gonçalves, Cristina; Jimenez-Rivera, Carolina; Banales, Jesus M; Thompson, Richard J; Hansen, Bettina E; Kamath, Binita M