日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Novel cryptic ADAMTS13 epitopes uncover a distinct open ADAMTS13 conformation in immune-mediated TTP

新型隐蔽的ADAMTS13表位揭示了免疫介导的TTP中ADAMTS13独特的开放构象。

Bonnez, Quintijn; Boudry, Febe; De Waele, Laure; Vermeersch, Lisa; Kangro, Kadri; Pareyn, Inge; Tellier, Edwige; Kaplanski, Gilles; Tersteeg, Claudia; Joly, Bérangère S; Coppo, Paul; Veyradier, Agnès; De Meyer, Simon F; Vanhoorelbeke, Karen

Optimizing ADAMTS13 prophylaxis to reduce relapse and organ failure in congenital thrombotic thrombocytopenic purpura

优化ADAMTS13预防以减少先天性血栓性血小板减少性紫癜的复发和器官衰竭

Joly, Bérangère S; Joseph, Adrien; Bouzid, Raïda; Boisseau, Pierre; Kwon, Thérésa; Dossier, Claire; Gouge-Biebuyck, Nathalie; Boyer, Olivia; Tsatsaris, Vassilis; Harambat, Jérôme; Delmas, Yahsou; Moranne, Olivier; Sellier-Leclerc, Anne-Laure; Marie, Manon; Barbet, Christelle; Provôt, François; Benhamou, Ygal; Veyradier, Agnès; Coppo, Paul; Augusto, Jean-François; Azoulay, Elie; Barbay, Virginie; Benhamou, Ygal; Arnaud, Jaccard; Charvet-Rumpler, Anne; Chauveau, Dominique; Choukroun, Gabriel; Coindre, Jean-Philippe; Coppo, Paul; Delmas, Yahsou; Celia, Salanoubat; Dossier, Antoine; Simon, Ville; Frémeaux-Bacchi, Véronique; Galicier, Lionel; Grangé, Steven; Guidet, Bertrand; Halimi, Jean-Michel; Antoine, Neel; Jacobs, Frédéric; Joly, Bérangère; Kanouni, Tarik; Kaplanski, Gilles; Virginie, Rieu; Le Guern, Véronique; Moulin, Bruno; Rebibou, Jean-Michel; Ojeda Uribe, Mario; Parquet, Nathalie; Pène, Frédéric; Perez, Pierre; Poullin, Pascale; Pouteil-Noble, Claire; Presne, Claire; Provôt, Françoi; Laurent, Mesnard; Saheb, Samir; Seguin, Amélie; Servais, Aude; Stépanian, Alain; Veyradier, Agnè; Vigneau, Cécile; Wynckel, Alain; Zunic, Patricia; Krummel, Thierry; Ulrich, Marc; Hertig, Alexandre; Benoît, Suzon; Laurent, Gilardin; Le Quintrec, Moglie; Kwon, Theresa; Chatelet, Valérie; Ducheyron, Damien; Martis, Nihal; Marie, Manon; Ribes, David; Ronchetti, Anne-Marie

Health-related quality of life in adults with von Willebrand disease: results of the French real-life Willebrand study on health-related quality of life

成人血管性血友病患者的健康相关生活质量:法国真实世界血管性血友病健康相关生活质量研究的结果

Borel-Derlon, Annie; Veyradier, Agnès; Repessé, Yohann; Itzhar-Baïkan, Nathalie; Desprez, Dominique; Genre-Volot, Fabienne; Chambost, Hervé; Ardillon, Laurent; Pan-Petesch, Brigitte; Bayart, Sophie; Barthez-Toullec, Malika; Marin, Grégory; André-Bonnet, Marie Hélène; Susen, Sophie; von Mackensen, Sylvia; Goudemand, Jenny

Monitoring ADAMTS-13 conformation in immune-mediated thrombotic thrombocytopenic purpura: toward personalized management

监测免疫介导的血栓性血小板减少性紫癜中ADAMTS-13的构象:迈向个体化管理

Joly, Bérangère S; Roose, Elien; Dekimpe, Charlotte; Vanhoorelbeke, Karen; Veyradier, Agnès; Coppo, Paul

Caplacizumab use in immune-mediated thrombotic thrombocytopenic purpura: an international multicentre retrospective Cohort study (The Capla 1000+ project)

Caplacizumab 在免疫介导的血栓性血小板减少性紫癜中的应用:一项国际多中心回顾性队列研究(Capla 1000+ 项目)

Coppo, Paul; Bubenheim, Michael; Benhamou, Ygal; Völker, Linus; Brinkkötter, Paul; Kühne, Lucas; Knöbl, Paul; Mingot-Castellano, Maria Eva; Pascual-Izquierdo, Cristina; de la Rubia, Javier; Del Rio Garma, Julio; Chaturvedi, Shruti; Masias, Camila; Mazepa, Marshall; Zheng, X Long; Sinkovits, György; Réti, Marienn; Patriquin, Christopher J; Pavenski, Katerina; Boechat, Tiago; Farias, João; Oliveira Ribeiro, Eduardo Flavio; Lobo de Andrade, Michaela Larissa; Veyradier, Agnès; Joly, Bérangère; Bouzid, Raïda; Sakai, Kazuya; Matsumoto, Masanori; Agosti, Pasquale; Mancini, Ilaria; Peyvandi, Flora; Gavriilaki, Eleni; Stubbs, Matthew; Hmaid, Amjad; Cataland, Spero; Lämmle, Bernhard; Scully, Marie

Efficacy and Safety of Obinutuzumab in Immune-Mediated Thrombotic Thrombocytopenic Purpura

奥妥珠单抗治疗免疫介导的血栓性血小板减少性紫癜的疗效和安全性

Weisinger, Julia; Bouzid, Raïda; Fadlallah, Jehane; Barbet, Christelle; Provot, Francois; Poullin, Pascale; Neel, Antoine; Marie, Manon; Rieu, Virginie; Kanouni, Tarik; Moranne, Olivier; Azoulay, Elie; Marjanovic, Zora; Corre, Elise; Joly, Anne-Christine; Baylatry, Minh-Tam; Joly, Bérangère S; Veyradier, Agnes; Coppo, Paul

Anti-ADAMTS13 Antibodies Trajectory is Associated With ADAMTS13 Recovery in Immune-Mediated TTP

抗ADAMTS13抗体轨迹与免疫介导的TTP中ADAMTS13的恢复相关。

Robert, Marie; Mageau, Arthur; Benhamou, Ygal; Provôt, François; Fadlallah, Jehane; Galicier, Lionel; Azoulay, Elie; Ait-Oufella, Hafid; Urbina, Tomas; Poullin, Pascale; Wynckel, Alain; Poulain, Coralie; Martis, Nihal; Perez, Pierre; Rieu, Virginie; Delmas, Yahsou; Halimi, Jean-Michel; Barbet, Christelle; Seguin, Amélie; Chatelet, Valérie; Augusto, Jean-François; Legendre, Mathieu; Moranne, Olivier; Philipponnet, Carole; Cador, Bérengère; Bouzid, Raïda; Joly, Bérangère S; Veyradier, Agnès; Coppo, Paul

Acquired thrombotic thrombocytopenic purpura without detectable anti-ADAMTS13 antibodies: a possible underlying autoimmune mechanism

无抗ADAMTS13抗体的获得性血栓性血小板减少性紫癜:一种可能的潜在自身免疫机制

Simon, Delphine; Leclercq, Mathilde; Joly, Bérangère; Veyradier, Agnès; Coppo, Paul; Benhamou, Ygal

Acquired thrombotic thrombocytopenic purpura of unidentified pathophysiology in patients with severe disease: completing the landscape of thrombotic thrombocytopenic purpura

重症患者不明原因获得性血栓性血小板减少性紫癜:完善血栓性血小板减少性紫癜的图谱

Joly, Bérangère S; Leclercq, Mathilde; Benhamou, Ygal; Veyradier, Agnès; Coppo, Paul

New Insights Into Renal Involvement During Immune-Mediated Thrombotic Thrombocytopenic Purpura

免疫介导的血栓性血小板减少性紫癜肾脏受累的新见解

Robert, Marie; Maisons, Valentin; Rabant, Marion; Servais, Aude; Antunes, Charles; Fage, Nicolas; von Tokarski, Florent; Chauvet, Sophie; Dekeyser, Manon; Wynckel, Alain; Duval, Anna; Baroukh, Nadine; Veyradier, Agnès; Joly, Bérangère S; Coppo, Paul; Halimi, Jean-Michel