日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Isolation of a novel human prion strain from a PRNP codon 129 heterozygous vCJD patient

从一名PRNP基因129密码子杂合的vCJD患者中分离出一种新型人类朊病毒株

Zhang, Fuquan; Joiner, Susan; Linehan, Jacqueline M; Pintilii, Florin; Nazari, Tamsin; Argentina, Fabio; Preston, Connor; Taema, Maged; Cunningham, Thomas J; Asante, Emmanuel A; Mok, Tzehow; Mead, Simon; Brandner, Sebastian; Collinge, John; Wadsworth, Jonathan D F

PRNP E146G mutation inherited prion disease: distinctive clinical, pathological and fluid biomarker features.

PRNP E146G 突变遗传性朊病毒病:独特的临床、病理和体液生物标志物特征

Coysh Thomas, Jaunmuktane Zane, Hosszu Laszlo L P, Majbour Nour, Zhang Fuquan, Campbell Tracy, Darwent Lee, Matus Marcelo Barria, Chan Edgar, Holm-Mercer Leah, Mok Tze How, Wadsworth Jonathan D F, Bieschke Jan, Nithi Kannan, Brandner Sebastian, Smith Colin, Esiri Margaret, Collinge John, Mead Simon

Prion strains viewed through the lens of cryo-EM

通过冷冻电镜观察朊病毒株

Manka, Szymon W; Wenborn, Adam; Collinge, John; Wadsworth, Jonathan D F

Humanized Transgenic Mice Are Resistant to Chronic Wasting Disease Prions From Norwegian Reindeer and Moose

人源化转基因小鼠对来自挪威驯鹿和驼鹿的慢性消耗性疾病朊病毒具有抵抗力

Wadsworth, Jonathan D F; Joiner, Susan; Linehan, Jacqueline M; Jack, Kezia; Al-Doujaily, Huda; Costa, Helena; Ingold, Thea; Taema, Maged; Zhang, Fuquan; Sandberg, Malin K; Brandner, Sebastian; Tran, Linh; Vikøren, Turid; Våge, Jørn; Madslien, Knut; Ytrehus, Bjørnar; Benestad, Sylvie L; Asante, Emmanuel A; Collinge, John

Overexpression of mouse prion protein in transgenic mice causes a non-transmissible spongiform encephalopathy

转基因小鼠体内小鼠朊病毒蛋白的过度表达会导致一种非传染性海绵状脑病。

Jackson, Graham S; Linehan, Jacqueline; Brandner, Sebastian; Asante, Emmanuel A; Wadsworth, Jonathan D F; Collinge, John

Evaluation of plasma tau and neurofilament light chain biomarkers in a 12-year clinical cohort of human prion diseases

对人类朊病毒疾病12年临床队列中血浆tau蛋白和神经丝轻链生物标志物的评估

Thompson, Andrew G B; Anastasiadis, Prodromos; Druyeh, Ronald; Whitworth, Ines; Nayak, Annapurna; Nihat, Akin; Mok, Tze How; Rudge, Peter; Wadsworth, Jonathan D F; Rohrer, Jonathan; Schott, Jonathan M; Heslegrave, Amanda; Zetterberg, Henrik; Collinge, John; Jackson, Graham S; Mead, Simon

Spontaneous generation of prions and transmissible PrP amyloid in a humanised transgenic mouse model of A117V GSS

在A117V GSS人源化转基因小鼠模型中,朊病毒和可传播的PrP淀粉样蛋白的自发产生

Asante, Emmanuel A; Linehan, Jacqueline M; Tomlinson, Andrew; Jakubcova, Tatiana; Hamdan, Shyma; Grimshaw, Andrew; Smidak, Michelle; Jeelani, Asif; Nihat, Akin; Mead, Simon; Brandner, Sebastian; Wadsworth, Jonathan D F; Collinge, John

Structural features distinguishing infectious ex vivo mammalian prions from non-infectious fibrillar assemblies generated in vitro

区分体外感染性哺乳动物朊病毒和体外生成的非感染性纤维状聚集体的结构特征

Terry, Cassandra; Harniman, Robert L; Sells, Jessica; Wenborn, Adam; Joiner, Susan; Saibil, Helen R; Miles, Mervyn J; Collinge, John; Wadsworth, Jonathan D F

Recent Advances in Understanding Mammalian Prion Structure: A Mini Review

哺乳动物朊病毒结构研究的最新进展:简述

Terry, Cassandra; Wadsworth, Jonathan D F

Evaluating the causality of novel sequence variants in the prion protein gene by example

以实例评估朊病毒蛋白基因中新型序列变异的因果关系

Mok, Tze How; Koriath, Carolin; Jaunmuktane, Zane; Campbell, Tracy; Joiner, Susan; Wadsworth, Jonathan D F; Hosszu, Laszlo L P; Brandner, Sebastian; Parvez, Ambereen; Truelsen, Thomas Clement; Lund, Eva Løbner; Saha, Romi; Collinge, John; Mead, Simon