日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Correction to: An international survey of allogeneic hematopoietic cell transplantation for X-linked agammaglobulinemia

更正:一项关于X连锁无丙种球蛋白血症异基因造血干细胞移植的国际调查

Nishimura, Akira; Uppuluri, Ramya; Raj, Revathi; Swaminathan, Venkateswaran Vellaichamy; Cheng, Yifei; Abu-Arja, Rolla F; Fu, Bin; Laberko, Alexandra; Albert, Michael H; Hauck, Fabian; Bucciol, Giorgia; Bigley, Venetia; Elcombe, Suzanne; Kharya, Gaurav; Pronk, Cornelis Jan H; Wehr, Claudia; Neven, Bénédicte; Warnatz, Klaus; Meyts, Isabelle; Morio, Tomohiro; Gennery, Andrew R; Kanegane, Hirokazu

Recombination junctions from antibody isotype switching classify immune and DNA repair dysfunction

抗体同型转换产生的重组连接可对免疫和DNA修复功能障碍进行分类。

Clara Vázquez García #,Benedikt Obermayer #,Baerbel Keller,Mikhail Lebedin,Christoph Ratswohl,Hassan Abolhassani,Antonia Busse,Michela Di Virgilio,Stephan Mathas,Dorothee Speiser,Dieter Beule,Qiang Pan-Hammarström,Klaus Warnatz,Kathrin de la Rosa

Expansion of CD57(+) CD8 T cells in common variable immunodeficiency with hepatopathy and CMV infection

常见变异型免疫缺陷伴肝病和巨细胞病毒感染中CD57(+)CD8 T细胞扩增

Bez, Patrick; Santangeli, Enrico; Goldacker, Sigune; Salzer, Ulrich; Warnatz, Klaus

Case Report: Late-onset primary hemophagocytic lymphohistiocytosis leading to the diagnosis of Griscelli syndrome type 2 in a young woman with phenotypically inapparent partial albinism

病例报告:一名表型不明显的年轻女性,因迟发性原发性噬血细胞性淋巴组织细胞增生症确诊为格里塞利综合征2型。

Rausch, Johanna; Herold, Stephanie; Liebhäuser, Simone; Bülbül, Yagmur; Antunes Ferreira, Edite; Wenz, Till; Legscha, Kevin Jan; Bros, Matthias; Butsch, Florian; Kriege, Oliver; Warnatz, Klaus; Groß, Miriam; Lehmberg, Kai; Lichtenfeld, Helena Clara; La Rosée, Paul; Radsak, Markus Philipp; Theobald, Matthias; Echchannaoui, Hakim; Munder, Markus

Do CVID patients on SCIG have more autoimmune (thrombo)cytopenic events than CVID patients on IVIG?

接受皮下注射免疫球蛋白(SCIG)治疗的CVID患者是否比接受静脉注射免疫球蛋白(IVIG)治疗的CVID患者更容易发生自身免疫性(血小板)减少症?

Camacho-Ordonez, Nadezhda; Hirsch, Aleksandra; Campos, Luiza; Goldacker, Sigune; Burns, Siobhan O; Moreira, Fernando; Warnatz, Klaus; Grimbacher, Bodo

CD21low B cells reveal a unique glycosylation pattern with hypersialylation and hyperfucosylation

CD21low B 细胞表现出独特的糖基化模式,具有高唾液酸化和高岩藻糖基化

Peter Tobias Felixberger, Geoffroy Andrieux, Andrea Maul-Pavicic, Sigune Goldacker, Ina Harder, Sylvia Gutenberger, Jonathan J M Landry, Vladimir Benes, Till Fabian Jakob, Melanie Boerries, Lars Nitschke, Reinhard Edmund Voll, Klaus Warnatz #, Baerbel Keller #

Bronchiectasis, Low IgG Levels and Lack of Vaccination are Risk Factors for Covid-19 Hospitalization in X-linked Agammaglobulinemia - A Retrospective Multicenter Study

支气管扩张、低IgG水平和未接种疫苗是X连锁无丙种球蛋白血症患者新冠肺炎住院的危险因素——一项回顾性多中心研究

Stenlander, Caroline; Lindahl, Hannes; Wahren-Borgström, Emelie; Geier, Christoph B; Sediva, Anna; Fevang, Børre; Milito, Cinzia; Varandas, Cláudia; Roca-Oporto, Cristina; Pulvirenti, Federica; Hodl, Isabel; Malkusova, Ivana; Rivière, Jacques G; Litzman, Jiri; Walter, Jolan E; Hanitsch, Leif G; Neth, Olaf; Kralickova, Pavlina; Miller, Rahim; Shaffren, Serena; Silva, Susana L; Katzenstein, Terese; Martelius, Timi; Steiner, Urs C; Smith, C I Edvard; Warnatz, Klaus; Bergman, Peter

COVID-19 progression and convalescence in common variable immunodeficiency patients show dysregulated adaptive immune responses and persistent type I interferon and inflammasome activation

常见变异型免疫缺陷患者的 COVID-19 病情进展和康复期表现出适应性免疫反应失调以及 I 型干扰素和炎症小体持续激活。

Rodríguez-Ubreva, Javier; Calafell-Segura, Josep; Calvillo, Celia L; Keller, Baerbel; Ciudad, Laura; Handfield, Louis-François; de la Calle-Fabregat, Carlos; Godoy-Tena, Gerard; Andrés-León, Eduardo; Hoo, Regina; Porter, Tarryn; Prigmore, Elena; Hofmann, Maike; Decker, Annegrit; Martín, Javier; Vento-Tormo, Roser; Warnatz, Klaus; Ballestar, Esteban

IL-7-dependent and -independent lineages of IL-7R-dependent human T cells

IL-7依赖性和非IL-7依赖性IL-7R依赖性人类T细胞谱系

Arango-Franco, Carlos A; Ogishi, Masato; Unger, Susanne; Delmonte, Ottavia M; Orrego, Julio César; Yatim, Ahmad; Velasquez-Lopera, Margarita M; Zea-Vera, Andrés F; Bohlen, Jonathan; Chbihi, Marwa; Fayand, Antoine; Sánchez, Juan Pablo; Rojas, Julian; Seeleuthner, Yoann; Le Voyer, Tom; Philippot, Quentin; Payne, Kathryn J; Gervais, Adrian; Erazo-Borrás, Lucia V; Correa-Londoño, Luis A; Cederholm, Axel; Gallón-Duque, Alejandro; Goncalves, Pedro; Doisne, Jean-Marc; Horev, Liran; Charmeteau-de Muylder, Bénédicte; Álvarez, Jesús Á; Arboleda, Diana M; Pérez-Zapata, Lizet; Vásquez-Echeverri, Estefanía; Moncada-Vélez, Marcela; López, Juan A; Caicedo, Yolanda; Palterer, Boaz; Patiño, Pablo J; Montoya, Carlos J; Chaldebas, Matthieu; Zhang, Peng; Nguyen, Tina; Ma, Cindy S; Jeljeli, Mohamed; Alzate, Juan F; Cabarcas, Felipe; Khan, Taushif; Rinchai, Darawan; Prétet, Jean-Luc; Boisson, Bertrand; Marr, Nico; Ibrahim, Ruba; Molho-Pessach, Vered; Boisson-Dupuis, Stéphanie; Kiritsi, Dimitra; Barata, João T; Landegren, Nils; Neven, Bénédicte; Abel, Laurent; Lisco, Andrea; Béziat, Vivien; Jouanguy, Emmanuelle; Bustamante, Jacinta; Di Santo, James P; Tangye, Stuart G; Notarangelo, Luigi D; Cheynier, Rémi; Natsuga, Ken; Arias, Andrés A; Franco, José Luis; Warnatz, Klaus; Casanova, Jean-Laurent; Puel, Anne

A novel transmembrane CXCR4 variant that expands the WHIM genotype-phenotype paradigm

一种新型跨膜CXCR4变体,扩展了WHIM基因型-表型范式

Zmajkovicova, Katarina; Pawar, Sumit; Sharapova, Svetlana O; Geier, Christoph B; Wiest, Ivana; Nguyen, Chi; Monticelli, Halenya; Maier-Munsa, Sabine; Chen, Kelly; Sleasman, John W; Aleshkevich, Svetlana; Polyakova, Ekaterina; Sakovich, Inga; Warnatz, Klaus; Grimbacher, Bodo; Proietti, Michele; Sondheimer, Neal; Ujhazi, Boglarka; Gordon, Sumai; Ellison, Maryssa; Yilmaz, Melis; Walter, Jolan E; Badarau, Adriana; Taveras, Arthur G; Neff, Jadee L; Bledsoe, Jacob R; Tarrant, Teresa K