日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Correction to: A Multicentric Clinical Study to Evaluate Pharmacokinetics, Efficacy, and Safety of Immune Globulin Subcutaneous 20% Weekly/Biweekly Dosing in Treatment-Experienced Patients and Loading/Weekly Maintenance Dosing in Treatment-Naïve Patients with Primary Immunodeficiency

更正:一项多中心临床研究,旨在评估免疫球蛋白皮下注射20%(每周/每两周一次)在经治疗患者中的药代动力学、疗效和安全性,以及在初治原发性免疫缺陷患者中的负荷剂量/每周维持剂量。

Lumry, William R; Palumbo, Michael; Hsu, Connie; Hussain, Iftikhar; McNeil, Donald; Bridges, Tracy; Wedner, H James; Scarupa, Mark; Mondou, Elsa; Nanaware-Kharade, Nisha; Hanna, Kim; Coll, Montse Querolt; Oliveras, Juan

N-glycosylation in the SERPIN domain of the C1-esterase inhibitor in hereditary angioedema.

遗传性血管性水肿中 C1 酯酶抑制剂 SERPIN 结构域的 N-糖基化

Ren Zhen, Bao John, Zhao Shuangxia, Pozzi Nicola, Wedner H James, Atkinson John P

A Multicentric Clinical Study to Evaluate Pharmacokinetics, Efficacy, and Safety of Immune Globulin Subcutaneous 20% Weekly/Biweekly Dosing in Treatment-Experienced Patients and Loading/Weekly Maintenance Dosing in Treatment-Naïve Patients with Primary Immunodeficiency

一项多中心临床研究,旨在评估免疫球蛋白皮下注射20%(每周/每两周一次)在经治疗患者中的药代动力学、疗效和安全性,以及在初治原发性免疫缺陷患者中负荷剂量/每周维持剂量的疗效。

Lumry, William R; Palumbo, Michael; Hsu, Connie; Hussain, Iftikhar; McNeil, Donald; Bridges, Tracy; Wedner, H James; Scarupa, Mark; Mondou, Elsa; Nanaware-Kharade, Nisha; Hanna, Kim; Coll, Montse Querolt; Oliveras, Juan

Impact of hereditary angioedema attacks on health-related quality of life and work productivity

遗传性血管性水肿发作对健康相关生活质量和工作效率的影响

O'Connor, Maeve; Busse, Paula J; Craig, Timothy J; Radojicic, Cristine; Wedner, H James; Danese, Sherry; Ulloa, Julie; Desai, Vibha; Andriotti, Tomas; Audhya, Paul K; Christiansen, Sandra

Sustained Effectiveness, Tolerability, and Safety of Long-Term Prophylaxis with Lanadelumab in Hereditary Angioedema: The Prospective, Phase 4, Noninterventional EMPOWER Real-World Study

Lanadelumab 长期预防治疗遗传性血管性水肿的持续有效性、耐受性和安全性:前瞻性、4 期、非干预性 EMPOWER 真实世界研究

Bernstein, Jonathan A; Betschel, Stephen D; Busse, Paula J; Banerji, Aleena; Wedner, H James; Manning, Michael; Zaragoza-Urdaz, Rafael H; Anderson, John; Gagnon, Remi; Baptist, Alan P; Soteres, Daniel; Lumry, William R; Craig, Timothy; Petroni, Daniel; Hsu, F Ida; Nova Estepan, Daniel; Juethner, Salomé; Watt, Maureen; Khutoryansky, Natalie; Zuraw, Bruce L

Gastrointestinal pathology in Good's syndrome, thinking beyond common variable immunodeficiency: a clinicopathological observation

Good综合征的胃肠道病理学:超越常见变异型免疫缺陷的思考:一项临床病理学观察

Navale, Pooja; Zimmerman, Ofer; Wedner, James; Pande, Anupam; Ballentine, Samuel

Immunoglobulin replacement products protect against SARS-CoV-2 infection in vivo despite poor neutralizing activity

免疫球蛋白替代产品尽管中和活性较差,但仍可在体内预防 SARS-CoV-2 感染

Ofer Zimmerman, Alexa Michelle Altman Doss, Baoling Ying, Chieh-Yu Liang, Samantha R Mackin, Hannah G Davis-Adams, Lucas J Adams, Laura A VanBlargan, Rita E Chen, Suzanne M Scheaffer, Pritesh Desai, Saravanan Raju, Tarisa L Mantia, Caitlin C O'Shaughnessy, Jennifer Marie Monroy, H James Wedner, Chri

Insights into the pathogenesis of hereditary angioedema using genetic sequencing and recombinant protein expression analyses

利用基因测序和重组蛋白表达分析深入了解遗传性血管性水肿的发病机制

Ren, Zhen; Zhao, Shuangxia; Li, Tiandao; Wedner, H James; Atkinson, John P

mRNA vaccine boosting enhances antibody responses against SARS-CoV-2 Omicron variant in individuals with antibody deficiency syndromes

mRNA 疫苗增强剂可增强患有抗体缺陷综合征的个体对 SARS-CoV-2 Omicron 变体的抗体反应

Ofer Zimmerman, Alexa Michelle Altman Doss, Paulina Kaplonek, Chieh-Yu Liang, Laura A VanBlargan, Rita E Chen, Jennifer Marie Monroy, H James Wedner, Anthony Kulczycki Jr, Tarisa L Mantia, Caitlin C O'Shaughnessy, Hannah G Davis-Adams, Harry L Bertera, Lucas J Adams, Saravanan Raju, Fang R Zhao, Chr

SARS-CoV-2 booster vaccination rescues attenuated IgG1 memory B cell response in primary antibody deficiency patients

SARS-CoV-2 加强疫苗接种可挽救原发性抗体缺陷患者减弱的 IgG1 记忆 B 细胞反应

Frank J Lin, Alexa Michelle Altman Doss, Hannah G Davis-Adams, Lucas J Adams, Christopher H Hanson, Laura A VanBlargan, Chieh-Yu Liang, Rita E Chen, Jennifer Marie Monroy, H James Wedner, Anthony Kulczycki, Tarisa L Mantia, Caitlin C O'Shaughnessy, Saravanan Raju, Fang R Zhao, Elise Rizzi, Christoph