日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A preclinical pig model of Angelman syndrome mirrors the early developmental trajectory of the human condition.

Angelman 综合征的临床前猪模型反映了人类疾病的早期发展轨迹

Myers Luke S, Christian Sarah G, Simpson Sean, Sper Renan, Taylor Clint, Montes Laura, Jepp Thomas B C, Ramos Daniela, Schuller Livia, Konganti Kranti, Friedeck Wade, Habib Ozair, Hodge McKaela, Taylor Alasdair J, Coffell Ashley, Schlafer Annalise, Matt Morgan, Revell Bradley, Knight Carol, Barreña Cristina C, Murphy William J, Weeber Edwin J, Segal David J, Anderson Anne, Nash Kevin R, Silverman Jill L, Piedrahita Jorge A, Dindot Scott V

Reelin and APP Cooperatively Modulate Dendritic Spine Formation In Vitro and In Vivo.

Reelin 和 APP 在体外和体内协同调节树突棘的形成

Lee Hyun-Ju, Park Jin-Hee, Trotter Justin H, Maher James N, Keenoy Kathleen E, Jang You Mi, Lee Youngeun, Kim Jae-Ick, Weeber Edwin J, Hoe Hyang-Sook

Generation of a Novel Rat Model of Angelman Syndrome with a Complete Ube3a Gene Deletion

构建一种具有完全Ube3a基因缺失的新型Angelman综合征大鼠模型

Dodge, Andie; Peters, Melinda M; Greene, Hayden E; Dietrick, Clifton; Botelho, Robert; Chung, Diana; Willman, Jonathan; Nenninger, Austin W; Ciarlone, Stephanie; Kamath, Siddharth G; Houdek, Pavel; Sumová, Alena; Anderson, Anne E; Dindot, Scott V; Berg, Elizabeth L; O'Geen, Henriette; Segal, David J; Silverman, Jill L; Weeber, Edwin J; Nash, Kevin R

Astaxanthin supplementation modulates cognitive function and synaptic plasticity in young and aged mice

补充虾青素可调节幼鼠和老年小鼠的认知功能和突触可塑性。

Grimmig, Bethany; Hudson, Charles; Moss, Lauren; Peters, Melinda; Subbarayan, Meena; Weeber, Edwin J; Bickford, Paula C

Strain-dependence of the Angelman Syndrome phenotypes in Ube3a maternal deficiency mice

Ube3a 母系缺陷小鼠中 Angelman 综合征表型的品系依赖性

Born, Heather A; Dao, An T; Levine, Amber T; Lee, Wai Ling; Mehta, Natasha M; Mehra, Shubhangi; Weeber, Edwin J; Anderson, Anne E

Reelin Proteolysis Affects Signaling Related to Normal Synapse Function and Neurodegeneration

Reelin蛋白水解影响与正常突触功能和神经退行性变相关的信号传导

Lussier, April L; Weeber, Edwin J; Rebeck, G William

Increased selenoprotein P in choroid plexus and cerebrospinal fluid in Alzheimer's disease brain

阿尔茨海默病患者脑脉络丛和脑脊液中硒蛋白P含量升高

Rueli, Rachel H L H; Parubrub, Arlene C; Dewing, Andrea S T; Hashimoto, Ann C; Bellinger, Miyoko T; Weeber, Edwin J; Uyehara-Lock, Jane H; White, Lon R; Berry, Marla J; Bellinger, Frederick P

Reelin supplementation recovers synaptic plasticity and cognitive deficits in a mouse model for Angelman syndrome

在安格曼综合征小鼠模型中,补充瑞林可恢复突触可塑性和认知缺陷。

Hethorn, Whitney R; Ciarlone, Stephanie L; Filonova, Irina; Rogers, Justin T; Aguirre, Daniela; Ramirez, Raquel A; Grieco, Joseph C; Peters, Melinda M; Gulick, Danielle; Anderson, Anne E; L Banko, Jessica; Lussier, April L; Weeber, Edwin J

Ligand-induced homotypic and heterotypic clustering of apolipoprotein E receptor 2

配体诱导的载脂蛋白E受体2的同型和异型聚集

Divekar, Shailaja D; Burrell, Teal C; Lee, Jennifer E; Weeber, Edwin J; Rebeck, G William

An open-label pilot trial of minocycline in children as a treatment for Angelman syndrome

一项关于米诺环素治疗儿童安格曼综合征的开放标签试点试验

Grieco, Joseph C; Ciarlone, Stephanie L; Gieron-Korthals, Maria; Schoenberg, Mike R; Smith, Amanda G; Philpot, Rex M; Heussler, Helen S; Banko, Jessica L; Weeber, Edwin J