日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Meningitis without Rash after Reactivation of Varicella Vaccine Strain in a 12-Year-Old Immunocompetent Boy

一名12岁免疫功能正常的男孩在水痘疫苗株再激活后出现无皮疹脑膜炎

Bierbaum, Sibylle; Fischer, Veronika; Briedigkeit, Lutz; Werner, Claudius; Hengel, Hartmut; Huzly, Daniela

Prevalence and course of disease after lung resection in primary ciliary dyskinesia: a cohort & nested case-control study

原发性纤毛运动障碍肺切除术后疾病的患病率和病程:一项队列研究和嵌套病例对照研究

Kouis, Panayiotis; Goutaki, Myrofora; Halbeisen, Florian S; Gioti, Ifigeneia; Middleton, Nicos; Amirav, Israel; Barbato, Angelo; Behan, Laura; Boon, Mieke; Emiralioglu, Nagehan; Haarman, Eric G; Karadag, Bulent; Koerner-Rettberg, Cordula; Lazor, Romain; Loebinger, Michael R; Maitre, Bernard; Mazurek, Henryk; Morgan, Lucy; Nielsen, Kim Gjerum; Omran, Heymut; Özçelik, Ugur; Price, Mareike; Pogorzelski, Andrzej; Snijders, Deborah; Thouvenin, Guillaume; Werner, Claudius; Zivkovic, Zorica; Kuehni, Claudia E; Yiallouros, Panayiotis K

The international primary ciliary dyskinesia cohort (iPCD Cohort): methods and first results

国际原发性纤毛运动障碍队列研究(iPCD队列):方法和初步结果

Goutaki, Myrofora; Maurer, Elisabeth; Halbeisen, Florian S; Amirav, Israel; Barbato, Angelo; Behan, Laura; Boon, Mieke; Casaulta, Carmen; Clement, Annick; Crowley, Suzanne; Haarman, Eric; Hogg, Claire; Karadag, Bulent; Koerner-Rettberg, Cordula; Leigh, Margaret W; Loebinger, Michael R; Mazurek, Henryk; Morgan, Lucy; Nielsen, Kim G; Omran, Heymut; Schwerk, Nicolaus; Scigliano, Sergio; Werner, Claudius; Yiallouros, Panayiotis; Zivkovic, Zorica; Lucas, Jane S; Kuehni, Claudia E

European Respiratory Society guidelines for the diagnosis of primary ciliary dyskinesia

欧洲呼吸学会关于原发性纤毛运动障碍诊断的指南

Lucas, Jane S; Barbato, Angelo; Collins, Samuel A; Goutaki, Myrofora; Behan, Laura; Caudri, Daan; Dell, Sharon; Eber, Ernst; Escudier, Estelle; Hirst, Robert A; Hogg, Claire; Jorissen, Mark; Latzin, Philipp; Legendre, Marie; Leigh, Margaret W; Midulla, Fabio; Nielsen, Kim G; Omran, Heymut; Papon, Jean-Francois; Pohunek, Petr; Redfern, Beatrice; Rigau, David; Rindlisbacher, Bernhard; Santamaria, Francesca; Shoemark, Amelia; Snijders, Deborah; Tonia, Thomy; Titieni, Andrea; Walker, Woolf T; Werner, Claudius; Bush, Andrew; Kuehni, Claudia E

Evolutionary Proteomics Uncovers Ancient Associations of Cilia with Signaling Pathways.

进化蛋白质组学揭示纤毛与信号通路之间的古老关联

Sigg Monika Abedin, Menchen Tabea, Lee Chanjae, Johnson Jeffery, Jungnickel Melissa K, Choksi Semil P, Garcia Galo 3rd, Busengdal Henriette, Dougherty Gerard W, Pennekamp Petra, Werner Claudius, Rentzsch Fabian, Florman Harvey M, Krogan Nevan, Wallingford John B, Omran Heymut, Reiter Jeremy F

Primary Ciliary Dyskinesia: An Update on Clinical Aspects, Genetics, Diagnosis, and Future Treatment Strategies

原发性纤毛运动障碍:临床表现、遗传学、诊断和未来治疗策略的最新进展

Mirra, Virginia; Werner, Claudius; Santamaria, Francesca

Study protocol, rationale and recruitment in a European multi-centre randomized controlled trial to determine the efficacy and safety of azithromycin maintenance therapy for 6 months in primary ciliary dyskinesia

一项欧洲多中心随机对照试验的研究方案、原理和招募情况,旨在确定阿奇霉素维持治疗6个月对原发性纤毛运动障碍的疗效和安全性。

Kobbernagel, Helene E; Buchvald, Frederik F; Haarman, Eric G; Casaulta, Carmen; Collins, Samuel A; Hogg, Claire; Kuehni, Claudia E; Lucas, Jane S; Omran, Heymut; Quittner, Alexandra L; Werner, Claudius; Nielsen, Kim G

Collecting clinical data in primary ciliary dyskinesia- challenges and opportunities

原发性纤毛运动障碍临床数据收集——挑战与机遇

Amirav, Israel; Roduta Roberts, Mary; Mussaffi, Huda; Mandelberg, Avigdor; Roth, Yehudah; Abitbul, Revital; Luder, Anthony; Blau, Hannah; Alkrinawi, Soliman; Aviram, Micha; Ben-Ami, Marta; Rotschild, Moshe; Bentur, Lea; Shoseyov, David; Cohen-Cymberknoh, Malena; Kerem, Eitan; Avital, Avraham; Springer, Chaim; Hevroni, Avigdor; Dabbah, Husein; Elizur, Arnon; Picard, Elie; Goldberg, Shmuel; Rivlin, Joseph; Livnat, Galit; Lavie, Moran; Alias, Nael; Soferman, Ruth; Olbrich, Heike; Raidt, Johanna; Wallmeier, Julia; Werner, Claudius; Loges, Niki T; Omran, Heymut

A reach-out system for video microscopy analysis of ciliary motions aiding PCD diagnosis

一种用于纤毛运动视频显微镜分析的远程系统,可辅助原发性纤毛运动障碍(PCD)的诊断。

Amirav, Israel; Mussaffi, Huda; Roth, Yehudah; Schmidts, Miriam; Omran, Heymut; Werner, Claudius

The nexin-dynein regulatory complex subunit DRC1 is essential for motile cilia function in algae and humans

连接蛋白-动力蛋白调节复合物亚基DRC1对于藻类和人类的运动纤毛功能至关重要。

Wirschell, Maureen; Olbrich, Heike; Werner, Claudius; Tritschler, Douglas; Bower, Raqual; Sale, Winfield S; Loges, Niki T; Pennekamp, Petra; Lindberg, Sven; Stenram, Unne; Carlén, Birgitta; Horak, Elisabeth; Köhler, Gabriele; Nürnberg, Peter; Nürnberg, Gudrun; Porter, Mary E; Omran, Heymut