日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Congenital T-cell activation impairs transitional-to-follicular B-cell maturation in humans

先天性T细胞活化会损害人类过渡型B细胞向滤泡型B细胞的成熟过程。

Allard-Chamard, Hugues; Hillier, Kirsty; Ramseier, Michelle L; Bertocchi, Alice; Kaneko, Naoki; Premo, Katherine; Yuen, Grace; Karpel, Marshall; Mahajan, Vinay S; Tsekeri, Christina; Hong, Joseph S; Vencic, Jean; Crotty, Rory; Sharda, Anish V; Barmettler, Sara; Westermann-Clark, Emma; Walter, Jolan E; Ghebremichael, Musie; Shalek, Alex K; Farmer, Jocelyn R; Pillai, Shiv

Factors associated with and kinetics of anti-IFN-α autoantibodies in RAG1/2 deficiency

RAG1/2缺陷中抗IFN-α自身抗体的相关因素及动力学

Wang, Chen; Potts, David Evan; Sun, Bijun; Toth, Marta; Ujhazi, Boglarka; Sharapova, Svetlana; Miller, Rahim; Rosen, Lindsey; Yilmaz, Melis; Larsen, Kellie; Delmonte, Ottavia M; Poskitt, Laura E; Allenspach, Eric J; de la Morena, Maria Teresa; Ward, Brant R; Hernandez, Joseph D; Geier, Christoph B; Bolanos, Hannie Zomer; Al-Herz, Waleed; Kuijpers, Taco W; Petrov, Andrej A; Savic, Sinisa; Chen, Karin; Westermann-Clark, Emma; Dutmer, Cullen M; Kanariou, Maria G; Adeli, Mehdi; Palma, Paolo; Bonfim, Carmem; Lycopoulou, Evangelia; Wolska-Kusnierz, Beata; de Barros Dorna, Mayra; Dbaibo, Ghassan; Bleesing, Jack; Moshous, Despina; Licciardi, Francesco; Neven, Benedicte; Schuetz, Catharina; Geha, Raif S; Miano, Maurizio; Goldman, Stanton C; Raasch, Jason; Gonzalez-Granado, Luis Ignacio; Celmeli, Fatih; Baris, Safa; Abraham, Roshini S; Buchbinder, David K; Butte, Manish J; Wang, Ji-Yang; Wang, Xiaochuan; Strauss, Kevin A; Holland, Steven M; Notarangelo, Luigi D; Walter, Jolan E

Clinical, immunological features, treatments, and outcomes of autoimmune hemolytic anemia in patients with RAG deficiency

RAG缺陷患者自身免疫性溶血性贫血的临床、免疫学特征、治疗和预后

Wang, Chen; Sun, Bijun; Wu, Kevin; Farmer, Jocelyn R; Ujhazi, Boglarka; Geier, Christoph B; Gordon, Sumai; Westermann-Clark, Emma; Savic, Sinisa; Secord, Elizabeth; Sargur, Ravishankar; Chen, Karin; Jin, Jay J; Dutmer, Cullen M; Kanariou, Maria G; Adeli, Mehdi; Palma, Paolo; Bonfim, Carmem; Lycopoulou, Evangelia; Wolska-Kusnierz, Beata; Dbaibo, Ghassan; Bleesing, Jack; Moshous, Despina; Neven, Benedicte; Schuetz, Catharina; Geha, Raif S; Notarangelo, Luigi D; Miano, Maurizio; Buchbinder, David K; Csomos, Krisztian; Wang, Wenjie; Wang, Ji-Yang; Wang, Xiaochuan; Walter, Jolan E

Matrix Metalloproteinase 7 Expression and Apical Epithelial Defects in Atp8b1 Mutant Mouse Model of Pulmonary Fibrosis

基质金属蛋白酶7表达和肺纤维化Atp8b1突变小鼠模型中的顶端上皮缺陷

Westermann-Clark, Emma; Soundararajan, Ramani; Fukumoto, Jutaro; Patil, Sahebgowda Sidramagowda; Stearns, Timothy M; Saji, Smita; Czachor, Alexander; Hernandez-Cuervo, Helena; Breitzig, Mason; Krishnamurthy, Sudarshan; Lockey, Richard F; Kolliputi, Narasaiah

Primary Immunodeficiency in Children With Autoimmune Cytopenias: Retrospective 154-Patient Cohort

儿童自身免疫性血细胞减少症的原发性免疫缺陷:154例患者回顾性队列研究

Westermann-Clark, Emma; Meehan, Cristina Adelia; Meyer, Anna K; Dasso, Joseph F; Amre, Devendra; Ellison, Maryssa; Patel, Bhumika; Betensky, Marisol; Hauk, Charles Isaac; Mayer, Jennifer; Metts, Jonathan; Leiding, Jennifer W; Sriaroon, Panida; Kumar, Ambuj; Ayala, Irmel; Walter, Jolan E

Clinical Characteristics of SARS-CoV2 Infected and Exposed Patients at a Tertiary Care Allergy/Immunology Program in Florida

佛罗里达州一家三级过敏/免疫学中心SARS-CoV-2感染和暴露患者的临床特征

Szukiewicz, Dariusz; Playfair, J H L; Miranda, Mary Ann; Dasso, Joseph; Ellison, Maryssa; Trotter, Jessica; Timothy, Priyanka; Chitty-Lopez, Maria; Duff, Carla; Nieves, Daime; Westermann-Clark, Emma; Tang, Nathan; Sher, Mandel; Ballow, Mark; Leiding, Jennifer; Sriaroon, Panida; Walter, Jolan

Case Report: A Novel Pathogenic Missense Mutation in FAS: A Multi-Generational Case Series of Autoimmune Lymphoproliferative Syndrome

病例报告:FAS 中一种新的致病性错义突变:多代自身免疫性淋巴增生综合征病例系列

Gaefke, Claudia L; Metts, Jonathan; Imanirad, Donya; Nieves, Daime; Terranova, Paola; Dell'Orso, Gianluca; Gambineri, Eleonora; Miano, Maurizio; Lockey, Richard F; Walter, Jolan Eszter; Westermann-Clark, Emma

Outcomes and Treatment Strategies for Autoimmunity and Hyperinflammation in Patients with RAG Deficiency

RAG缺陷患者自身免疫和过度炎症的结局和治疗策略

Farmer, Jocelyn R; Foldvari, Zsofia; Ujhazi, Boglarka; De Ravin, Suk See; Chen, Karin; Bleesing, Jack J H; Schuetz, Catharina; Al-Herz, Waleed; Abraham, Roshini S; Joshi, Avni Y; Costa-Carvalho, Beatriz T; Buchbinder, David; Booth, Claire; Reiff, Andreas; Ferguson, Polly J; Aghamohammadi, Asghar; Abolhassani, Hassan; Puck, Jennifer M; Adeli, Mehdi; Cancrini, Caterina; Palma, Paolo; Bertaina, Alice; Locatelli, Franco; Di Matteo, Gigliola; Geha, Raif S; Kanariou, Maria G; Lycopoulou, Lilia; Tzanoudaki, Marianna; Sleasman, John W; Parikh, Suhag; Pinero, Gloria; Fischer, Bernard M; Dbaibo, Ghassan; Unal, Ekrem; Patiroglu, Turkan; Karakukcu, Musa; Al-Saad, Khulood Khalifa; Dilley, Meredith A; Pai, Sung-Yun; Dutmer, Cullen M; Gelfand, Erwin W; Geier, Christoph B; Eibl, Martha M; Wolf, Hermann M; Henderson, Lauren A; Hazen, Melissa M; Bonfim, Carmem; Wolska-Kuśnierz, Beata; Butte, Manish J; Hernandez, Joseph D; Nicholas, Sarah K; Stepensky, Polina; Chandrakasan, Shanmuganathan; Miano, Maurizio; Westermann-Clark, Emma; Goda, Vera; Kriván, Gergely; Holland, Steven M; Fadugba, Olajumoke; Henrickson, Sarah E; Ozen, Ahmet; Karakoc-Aydiner, Elif; Baris, Safa; Kiykim, Ayca; Bredius, Robbert; Hoeger, Birgit; Boztug, Kaan; Pashchenko, Olga; Neven, Benedicte; Moshous, Despina; Villartay, Jean-Pierre de; Bousfiha, Ahmed Aziz; Hill, Harry R; Notarangelo, Luigi D; Walter, Jolan E

Economic considerations in the treatment of systemic allergic reactions

治疗全身性过敏反应的经济因素

Westermann-Clark, Emma; Pepper, Amber N; Lockey, Richard F

Global gene profiling of aging lungs in Atp8b1 mutant mice

Atp8b1 突变小鼠衰老肺的整体基因分析

Ramani Soundararajan, Timothy M Stearns, Alexander Czachor, Jutaro Fukumoto, Christina Turn, Emma Westermann-Clark, Mason Breitzig, Lee Tan, Richard F Lockey, Benjamin L King, Narasaiah Kolliputi