日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Capturing disease severity in LIS1-lissencephaly reveals proteostasis dysregulation in patient-derived forebrain organoids.

通过捕捉 LIS1-无脑回畸形的疾病严重程度,揭示了患者来源的前脑类器官中的蛋白质稳态失调。

Zillich Lea, Gasparotto Matteo, Rossetti Andrea Carlo, Fechtner Olivia, Maillard Camille, Hoffrichter Anne, Zillich Eric, Jabali Ammar, Marsoner Fabio, Artioli Annasara, Wilkens Ruven, Schroeter Christina B, Hentschel Andreas, Witt Stephanie H, Melzer Nico, Meuth Sven G, Ruck Tobias, Koch Philipp, Roos Andreas, Bahi-Buisson Nadia, Francis Fiona, Ladewig Julia

hiPSC-neurons recapitulate the subtype-specific cell intrinsic nature of susceptibility to neurodegenerative disease-relevant aggregation.

hiPSC-神经元重现了亚型特异性细胞内在的易感性,这种易感性与神经退行性疾病相关的聚集有关

Weidling Ian, Preiss Christina N, Chancellor Sarah E, Srivastava Gyan, Gibilisco Lauren, Lin Gen, Brennan Melanie Shackett, Lee Janice, Roth Lindsay M, Morozova Olga, Nam Kyong Nyon, Patel Nehal R, Liu Qing, Thomas J K, Reinhardt Peter, Wilkens Ruven, Ehrnhoefer Dagmar E, Striebinger Andreas, Barghorn Stefan, Xanthopoulos Christina, Weil Marie-Theres, Biesinger Sandra, Cik Miroslav, Romanul Nandini, Yanamandra Kiran, Welker Alessandra M, Wu Jessica, Gasparini Laura, Stöhr Jan, Langlois Xavier, Manos Justine D

BMP, MEK, and WNT inhibition with NGN2 expression for rapid generation of hiPSC-derived neurons amenable to regional patterning.

通过抑制 BMP、MEK 和 WNT 以及 NGN2 表达,可以快速生成适合区域模式化的 hiPSC 衍生神经元

Habich Carina, Kowalski Alexandra, Wachter Astrid, Heimann Michaela J, Wolf Michael, Kummer Markus P, Nicolaisen Nathalie, Sliwinski Christopher, Reinhardt Lydia, Heil Veronika, Lange Timo, Untucht Christopher, Miller Loan N, Korffmann Jürgen, Geist Daniela, Schöndorf David, Lee Heyne, Bahnassawy Lamiaa, Mielich-Süss Benjamin, Brennan Melanie S, Wilkens Ruven, Röwe Julian, Weidling Ian, Rudolf Rüdiger, Hafner Mathias, Manos Justine D, Cik Miroslav, Reinhardt Peter