日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Mosquito environmental DNA metabarcoding dataset in water-holding containers in dengue fever-endemic areas of DKI Jakarta, Indonesia

印度尼西亚雅加达 DKI 登革热流行区盛水容器中的蚊子环境 DNA 元条形码数据集

Firmansyah, Nurhadi Eko; Irmayanti, Shinta; Faizah, Astri Nur; Sungkar, Saleha; Winita, Rawina

Condition-Specific Growth Charts for Children With Alagille Syndrome

阿拉吉尔综合征患儿的特定生长曲线图

Huysentruyt, Koen; Vandriel, Shannon M; Roelants, Mathieu; Piccoli, David A; Loomes, Kathleen M; Rand, Elizabeth B; Ebel, Noelle H; Feinstein, Jeffrey A; Jankowska, Irena; Czubkowski, Piotr; Gliwicz-Miedzinska, Dorota; Gonzales, Emmanuel M; Jacquemin, Emmanuel; Bouligand, Jérôme; Karpen, Saul J; Romero, Rene; Lin, Henry C; Fischler, Björn; Arnell, Henrik; Li, Li-Ting; Wang, Jian-She; Fawaz, Rima; Nastasio, Silvia; Kim, Kyung Mo; Oh, Seak Hee; D'Antiga, Lorenzo; Nicastro, Emanuele; Fischer, Ryan T; Siew, Susan M; Stormon, Michael; Lertudomphonwanit, Chatmanee; Hardikar, Winita; Shankar, Sahana; Squires, James E; Sundaram, Shikha S; Larson-Nath, Catherine; Kelly, Deirdre A; Hartley, Jane; Bulut, Pinar; Jensen, M Kyle; Jaramillo, Catalina; Roberts, Amin J; Evans, Helen M; Sokal, Étienne M; Demaret, Tanguy; Verkade, Henkjan J; Thompson, Richard J; Hansen, Bettina E; Cole, Tim J; Kamath, Binita M; Debray, Dominique; Lacaille, Florence; Brecelj, Jernej; El-Koofy, Nehal M; Elmonem, Mohamed A; Lee, Way Seah; Sanchez, Maria Camila; Cavalieri, Maria Lorena; Hajinicolaou, Christina; Schwarz, Kathleen B; Carvalho, Elisa; Rock, Nathalie; Karnsakul, Wikrom; Quiros-Tejeira, Ruben E; Alam, Seema; Nebbia, Gabriella; Mozer-Glassberg, Yael; Valentino, Pamela L; Santos-Silva, Ermelinda; Önal, Zerrin; Dezsofi-Gottl, Antal; Melere, Melina; Legarda Tamara, María; Eshun, John; Zellos, Aglaia; Indolfi, Giuseppe; Rogalidou, Maria; Blondet, Niviann; Luigi Calvo, Pier; Beretta, Marisa; Zizzo, Andréanne N; Arikan, Cigdem; Kasahara, Mureo; Kerkar, Nanda; Aqul, Amal A; Wolters, Victorien M; Borges Pinto, Raquel; Quintero Bernabeu, Jesus; Garcia, Jennifer; Wiecek, Sabina; Tzivinikos, Christos; Mujawar, Quais; Jimenez-Rivera, Carolina; Molera Busoms, Cristina; Gonçalves, Cristina; Bujanda, Luis

Phenotypic Divergence of JAG1- and NOTCH2-Associated Alagille Syndrome & Disease-Specific NOTCH2 Variant Classification Guidelines

JAG1 和 NOTCH2 相关阿拉吉尔综合征的表型差异及疾病特异性 NOTCH2 变异分类指南

Vandriel, Shannon M; Li, Li-Ting; She, Huiyu; Wang, Jian-She; Loomes, Kathleen M; Piccoli, David A; Jankowska, Irena; Czubkowski, Piotr; Gliwicz-Miedzińska, Dorota; D'Antiga, Lorenzo; Nicastro, Emanuele; Lacaille, Florence; Debray, Dominique; Sokal, Étienne M; Demaret, Tanguy; Fawaz, Rima L; Nastasio, Silvia; Kim, Kyung Mo; Oh, Seak Hee; Fischler, Björn; Arnell, Henrik; Larson-Nath, Catherine; Hardikar, Winita; Shankar, Sahana; Sundaram, Shikha S; Chaidez, Alexander; Bulut, Pinar; Calvo, Pier Luigi; Kasahara, Mureo; Blondet, Niviann; Lurz, Eberhard; Kavallar, Anna-Maria; Gonzales, Emmanuel M; Jacquemin, Emmanuel; Bouligand, Jérôme; Ebel, Noelle H; Feinstein, Jeffrey A; Siew, Susan M; Stormon, Michael O; Karpen, Saul J; Romero, Rene; Jensen, M Kyle; Jaramillo, Catalina; Squires, James E; Bedoyan, Sarah M; Kelly, Deirdre A; Hartley, Jane; Verkade, Henkjan J; Lee, Way Seah; Lertudomphonwanit, Chatmanee; Fischer, Ryan T; Lin, Henry C; Rock, Nathalie; Mozer-Glassberg, Yael; Roberts, Amin J; Evans, Helen M; Karnsakul, Wikrom; Nebbia, Gabriella; Wolters, Victorien M; Valentino, Pamela L; Bernabeu, Jesus Quintero; Aqul, Amal A; Arikan, Cigdem; Tamara, María Legarda; Busoms, Cristina Molera; Sandahl, Thomas Damgaard; Indolfi, Giuseppe; Zizzo, Andréanne N; Zellos, Aglaia; Quiros-Tejeira, Ruben E; Santos-Silva, Ermelinda; Schwarz, Kathleen B; Brecelj, Jernej; Sanchez, Maria Camila; Cavalieri, Maria Lorena; Tzivinikos, Christos; Wiecek, Sabina; Eshun, John; Kerkar, Nanda; Mujawar, Quais; Önal, Zerrin; Gonçalves, Cristina; Garcia, Jennifer; Alam, Seema; Jimenez-Rivera, Carolina; Bujanda, Luis; Thompson, Richard J; Hansen, Bettina E; Spinner, Nancy B; Gilbert, Melissa A; Kamath, Binita M

Elevated Serum Bile Acids Predict Poor Liver Outcomes in Children With Alagille Syndrome: Results From the GALA Study Group

血清胆汁酸水平升高预示阿拉吉勒综合征患儿肝脏预后不良:GALA研究组的结果

Perez, Carla Fiorella Murillo; Vandriel, Shannon M; Gonzales, Emmanuel M; Wang, Jian-She; Li, Li-Ting; She, Huiyu; Jankowska, Irena; Czubkowski, Piotr; Gliwicz-Miedzińska, Dorota; Jacquemin, Emmanuel; Bouligand, Jérôme; D'Antiga, Lorenzo; Nicastro, Emanuele; Fischler, Björn; Arnell, Henrik; Siew, Susan M; Stormon, Michael; Loomes, Kathleen M; Piccoli, David A; Rand, Elizabeth B; Squires, James E; Karpen, Saul J; Romero, Rene; Kasahara, Mureo; Önal, Zerrin; Sokal, Étienne; Demaret, Tanguy; Wiecek, Sabina; Lacaille, Florence; Debray, Dominique; Hardikar, Winita; Shankar, Sahana; Valentino, Pamela L; Sundaram, Shikha S; Ebel, Noelle H; Feinstein, Jeffrey A; Waisbourd-Zinman, Orith; Lin, Henry C; Rock, Nathalie; Verkade, Henkjan J; Jensen, M Kyle; Jaramillo, Catalina; Kim, Kyung Mo; Oh, Seak Hee; Brecemiclj, Jernej; Alam, Seema; Indolfi, Giuseppe; Blondet, Niviann; Fawaz, Rima; Nastasio, Silvia; Calvo, Pier Luigi; Nebbia, Gabriella; Arikan, Cigdem; Larson-Nath, Catherine; Zizzo, Andréanne N; Sandahl, Thomas Damgaard; Tzivinikos, Christos; El-Koofy, Nehal M; Elmonem, Mohamed A; Aqul, Amal A; Karnsakul, Wikrom; Bulut, Pinar; Kerkar, Nanda; Wolters, Victorien M; Roberts, Amin J; Evans, Helen M; Sanchez, Maria Camila; Cavalieri, Maria Lorena; Kelly, Deirdre A; Hartley, Jane; Lee, Way Seah; Hajinicolaou, Christina; Lertudomphonwanit, Chatmanee; Fischer, Ryan T; Bernabeu, Jesus Quintero; Quiros-Tejeira, Ruben E; Ferreira, Cristina Targa; Carvalho, Elisa; Eshun, John; Zellos, Aglaia; Dezsőfi, Antal; Pinto, Raquel Borges; Schwarz, Kathleen; Rogalidou, Maria; Garcia, Jennifer; Tamara, María Legarda; Beretta, Marisa; Mujawar, Quais; Santos-Silva, Ermelinda; Busoms, Cristina Molera; Lurz, Eberhard; Gonçalves, Cristina; Jimenez-Rivera, Carolina; Banales, Jesus M; Thompson, Richard J; Hansen, Bettina E; Kamath, Binita M

A new multisystem ERCC1-hepatorenal syndrome: insights from a clinical cohort, molecular pathogenesis, and management guidelines

一种新的多系统ERCC1肝肾综合征:来自临床队列、分子发病机制和治疗指南的见解

White, Susan M; Wondergem, Annelotte P; Breet, Isa; Dittmaier, Maren; Bell, Katrina; Richmond, Christopher M; Hardikar, Winita; Bhatia, Kanika; Quinlan, Catherine; Orchard, David; D'Souza, Areetha; Chazin, Walter J; Smith, Christopher; Sparkes, Rebecca; Lam, Simon; Carter, Alexandra; Hopkin, Robert J; Khendek, Leticia; Sullivan, Bonnie R; Becher, Naja; Simonsen, Anne Katrine W; Kvistgaard, Helene; Dempsey, Katherine; Miethke, Alexander G; Gregersen, Pernille Axél; Phillips, Eliza; Luijsterburg, Martijn S

Event-free survival of maralixibat-treated patients with Alagille syndrome compared to a real-world cohort from GALA

与来自 GALA 的真实世界队列相比,接受 maralixibat 治疗的 Alagille 综合征患者的无事件生存期

Hansen, Bettina E; Vandriel, Shannon M; Vig, Pamela; Garner, Will; Mogul, Douglas B; Loomes, Kathleen M; Piccoli, David A; Rand, Elizabeth B; Jankowska, Irena; Czubkowski, Piotr; Gliwicz-Miedzińska, Dorota; Gonzales, Emmanuel M; Jacquemin, Emmanuel; Bouligand, Jérôme; D'Antiga, Lorenzo; Nicastro, Emanuele; Arnell, Henrik; Fischler, Björn; Sokal, Étienne; Demaret, Tanguy; Siew, Susan; Stormon, Michael; Karpen, Saul J; Romero, Rene; Ebel, Noelle H; Feinstein, Jeffrey A; Roberts, Amin J; Evans, Helen M; Sundaram, Shikha S; Chaidez, Alexander; Hardikar, Winita; Shankar, Sahana; Fischer, Ryan T; Lacaille, Florence; Debray, Dominique; Lin, Henry C; Jensen, M Kyle; Jaramillo, Catalina; Karthikeyan, Palaniswamy; Indolfi, Giuseppe; Verkade, Henkjan J; Larson-Nath, Catherine; Quiros-Tejeira, Ruben E; Valentino, Pamela L; Rogalidou, Maria; Dezsőfi, Antal; Squires, James E; Schwarz, Kathleen; Calvo, Pier Luigi; Bernabeu, Jesus Quintero; Zizzo, Andréanne N; Nebbia, Gabriella; Bulut, Pinar; Santos-Silva, Ermelinda; Fawaz, Rima; Nastasio, Silvia; Karnsakul, Wikrom; Tamara, María Legarda; Busoms, Cristina Molera; Kelly, Deirdre A; Sandahl, Thomas Damgaard; Jimenez-Rivera, Carolina; Banales, Jesus M; Mujawar, Quais; Li, Li-Ting; She, Huiyu; Wang, Jian-She; Kim, Kyung Mo; Oh, Seak Hee; Sanchez, Maria Camila; Cavalieri, Maria Lorena; Lee, Way Seah; Hajinicolaou, Christina; Lertudomphonwanit, Chatmanee; Waisbourd-Zinman, Orith; Arikan, Cigdem; Alam, Seema; Carvalho, Elisa; Melere, Melina; Eshun, John; Önal, Zerrin; Desai, Dev M; Wiecek, Sabina; Pinto, Raquel Borges; Wolters, Victorien M; Garcia, Jennifer; Beretta, Marisa; Kerkar, Nanda; Brecelj, Jernej; Rock, Nathalie; Lurz, Eberhard; Blondet, Niviann; Shah, Uzma; Thompson, Richard J; Kamath, Binita M

Safety, pharmacokinetics, and potential neurological interactions of ivermectin, tafenoquine, and chloroquine in Rhesus macaques.

伊维菌素、他非诺喹和氯喹在恒河猴中的安全性、药代动力学和潜在的神经系统相互作用

Vanachayangkul Pattaraporn, Kodchakorn Chanikarn, Ta-Aksorn Winita, Im-Erbsin Rawiwan, Tungtaeng Anchalee, Tipthara Phornpimon, Tarning Joel, Lugo-Roman Luis A, Wojnarski Mariusz, Vesely Brian A, Kobylinski Kevin C

Incidence, management and outcomes in hepatic artery complications after paediatric liver transplantation: protocol of the retrospective, international, multicentre HEPATIC Registry

儿童肝移植术后肝动脉并发症的发生率、处理和预后:回顾性、国际、多中心 HEPATIC 注册研究方案

Li, Weihao; van der Doef, Hubert P J; Wildhaber, Barbara E; Marra, Paolo; Bravi, Michela; Pinelli, Domenico; Minetto, Julia; Dip, Marcelo; Sierre, Sergio; de Santibañes, Martin; Ardiles, Victoria; Uno, Jimmy Walker; Hardikar, Winita; Bates, Sue; Goh, Lynette; Aldrian, Denise; Seisenbacher, Jonathan; Vogel, Georg F; Neto, Joao Seda; Antunes da Fonseca, Eduardo; Magalhães Costa, Carolina; Ferreira, Cristina T; Nader, Luiza S; Farina, Marco A; Dajani, Khaled Z; Parente, Alessandro; Bigam, David L; Liang, Ting-Bo; Bai, Xueli; Zhang, Wei; Gonsorčíková, Lucie; Froněk, Jiří; Bohuš, Šimon; Franchi-Abella, Stéphanie; Gonzales, Emmanuel; Guérin, Florent; Junge, Norman; Baumann, Ulrich; Richter, Nicolas; Hartleif, Steffen; Sturm, Ekkehard; Rajakannu, Muthukumarassamy; Palaniappan, Kumar; Rela, Mohamed; Pawaria, Arti; Rajakrishnan, Haritha; Surendran, Sudhindran; Kumar, Mukesh; Agarwal, Shaleen; Gupta, Subhash; Asthana, Sonal; Bandewar, Vaishnavi; Raichurkar, Karthik; Spada, Marco; Monti, Lidia; Alterio, Tommaso; Yanagi, Yusuke; Uchida, Hajime; Komine, Ryuji; Evans, Helen; Carr-Boyd, Peter; Duncan, David; Stefanowicz, Marek; Latka-Grot, Julita; Kolesnik, Adam; Broering, Dieter C; Raptis, Dimitri A; Ann H Marquez, Kris; Mali, Vidyadhar; Aw, Marion; Beretta, Marisa; Van der Schyff, Francisca; Quintero-Bernabeu, Jesús; Mercadal-Hally, Maria; Larrarte K, Mauricio; Andres, Ane M; Hernandez-Oliveros, Francisco; Frauca, Esteban; Casswall, Thomas; Jorns, Carl; Delle, Martin; Gupte, Girish; Sharif, Khalid; McGuirk, Simon; Superina, Riccardo; Caicedo, Juan Carlos; Jaramillo, Catalina; Bitterfeld, Leandra; Kastenberg, Zachary; Shah, Amit A; Domenick, Bryanna; Acord, Michael R; Mazariegos, George V; Soltys, Kyle; DiNorcia, Joseph; Antala, Swanti; Florman, Sander S; Buchholz, Bettina M; Herden, Uta; Fischer, Lutz; Dierckx, Rudi A J O; Hartog, Hermien; Bokkers, Reinoud P H

Arterial structure and function in children with inflammatory bowel disease

炎症性肠病患儿的动脉结构和功能

Jois, Asha; Zannino, Diana; Catto-Smith, Anthony G; Kaegi, Meg; Mynard, Jonathan P; Rosenbaum, Jeremy; Oliver, Mark; Hardikar, Winita; Alex, George; Burgner, David

Production of Nanocellulose from Sugarcane Bagasse and Development of Nanocellulose Conjugated with Polylysine for Fumonisin B1 Toxicity Absorption

利用甘蔗渣生产纳米纤维素以及开发用于吸收伏马毒素 B1 毒性的聚赖氨酸结合纳米纤维素

Parichat Thipchai, Korawan Sringarm, Winita Punyodom, Kittisak Jantanasakulwong, Sarinthip Thanakkasaranee, Rangsan Panyathip, Chaiwat Arjin, Pornchai Rachtanapun