Ineffective erythropoiesis in beta-thalassemia is characterized by increased iron absorption mediated by down-regulation of hepcidin and up-regulation of ferroportin
β-地中海贫血中的无效红细胞生成的特点是,铁吸收增加,这是由铁调素的下调和铁转运蛋白的上调介导的
期刊:Blood
影响因子:21
doi:10.1182/blood-2006-09-048868
Sara Gardenghi, Maria F Marongiu, Pedro Ramos, Ella Guy, Laura Breda, Amy Chadburn, YiFang Liu, Ninette Amariglio, Gideon Rechavi, Eliezer A Rachmilewitz, William Breuer, Z Ioav Cabantchik, Diedra M Wrighting, Nancy C Andrews, Maria de Sousa, Patricia J Giardina, Robert W Grady, Stefano Rivella