A hypomorphic model of CPS1 deficiency for investigating the effects of hyperammonemia on the developing nervous system.
CPS1 缺陷的低效模型,用于研究高氨血症对发育中神经系统的影响
期刊:Disease Models & Mechanisms
影响因子:3.3
doi:10.1242/dmm.052303
Bakshi Stuti, Diep Taryn, Willis Brandon J, Reyes Rachel, Wu Grace F, Makris Georgios, Poms Martin, Day Isabel, Sun Qin, Zhuravka Irina, Lueptow Lindsay, Tang Michelle, Cromie Gareth A, Dudley Aimée M, Häberle Johannes, Lipshutz Gerald S