日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Spatial proteomics reveals recombinant human laminin-111 restores adhesion signaling to laminin-α2-deficient muscle

空间蛋白质组学揭示重组人层粘连蛋白-111可恢复层粘连蛋白-α2缺陷肌肉的粘附信号传导。

Hailey J Hermann,Ryan D Wuebbles,Marisela Dagda,Axel Muñoz,Lauren L Parker,Paula C Guzman,Lola T Byrne,Steven A Moore,Dean J Burkin

A gene therapy approach for the treatment of limb-girdle muscular dystrophy 2C/R5

基因疗法治疗肢带型肌营养不良症 2C/R5

Hermann, Hailey; Wuebbles, Ryan D; Burkin, Dean J

Transgenic overexpression of α7 integrin in smooth muscle attenuates allergen-induced airway inflammation in a murine model of asthma

平滑肌中 α7 整合素的转基因过度表达可减轻哮喘小鼠模型中过敏原诱发的气道炎症

Mariam A Ba, Annemarie Aiyuk, Karla Hernández, Jon M Evasovic, Ryan D Wuebbles, Dean J Burkin, Cherie A Singer

Transgenic mice expressing tunable levels of DUX4 develop characteristic facioscapulohumeral muscular dystrophy-like pathophysiology ranging in severity

表达可调节水平的 DUX4 的转基因小鼠会出现严重程度不等的特征性面肩肱型肌营养不良症样病理生理

Takako I Jones, Guo-Liang Chew, Pamela Barraza-Flores, Spencer Schreier, Monique Ramirez, Ryan D Wuebbles, Dean J Burkin, Robert K Bradley, Peter L Jones

Air Pollution and Noncommunicable Diseases: A Review by the Forum of International Respiratory Societies' Environmental Committee, Part 1: The Damaging Effects of Air Pollution

空气污染与非传染性疾病:国际呼吸学会论坛环境委员会综述,第一部分:空气污染的危害

Schraufnagel, Dean E; Balmes, John R; Cowl, Clayton T; De Matteis, Sara; Jung, Soon-Hee; Mortimer, Kevin; Perez-Padilla, Rogelio; Rice, Mary B; Riojas-Rodriguez, Horacio; Sood, Akshay; Thurston, George D; To, Teresa; Vanker, Anessa; Wuebbles, Donald J

Air Pollution and Noncommunicable Diseases: A Review by the Forum of International Respiratory Societies' Environmental Committee, Part 2: Air Pollution and Organ Systems

空气污染与非传染性疾病:国际呼吸学会论坛环境委员会综述,第二部分:空气污染与器官系统

Schraufnagel, Dean E; Balmes, John R; Cowl, Clayton T; De Matteis, Sara; Jung, Soon-Hee; Mortimer, Kevin; Perez-Padilla, Rogelio; Rice, Mary B; Riojas-Rodriguez, Horacio; Sood, Akshay; Thurston, George D; To, Teresa; Vanker, Anessa; Wuebbles, Donald J

Laminin-111 protein therapy enhances muscle regeneration and repair in the GRMD dog model of Duchenne muscular dystrophy

层粘连蛋白-111 蛋白疗法可增强杜氏肌营养不良症 GRMD 犬模型的肌肉再生和修复

Pamela Barraza-Flores, Tatiana M Fontelonga, Ryan D Wuebbles, Hailey J Hermann, Andreia M Nunes, Joe N Kornegay, Dean J Burkin

Human Galectin-1 Improves Sarcolemma Stability and Muscle Vascularization in the mdx Mouse Model of Duchenne Muscular Dystrophy

人类 Galectin-1 可改善杜氏肌营养不良症 mdx 小鼠模型中的肌膜稳定性和肌肉血管化

Ryan D Wuebbles, Vivian Cruz, Pam Van Ry, Pamela Barraza-Flores, Paul D Brewer, Peter Jones, Dean J Burkin

Impaired fetal muscle development and JAK-STAT activation mark disease onset and progression in a mouse model for merosin-deficient congenital muscular dystrophy

胎儿肌肉发育受损和 JAK-STAT 激活标记小鼠模型中美罗星缺乏型先天性肌营养不良症的发生和进展

Andreia M Nunes, Ryan D Wuebbles, Apurva Sarathy, Tatiana M Fontelonga, Marianne Deries, Dean J Burkin, Sólveig Thorsteinsdóttir

Galectin-1 Protein Therapy Prevents Pathology and Improves Muscle Function in the mdx Mouse Model of Duchenne Muscular Dystrophy

Galectin-1 蛋白疗法可预防杜氏肌营养不良症 mdx 小鼠模型的病理并改善肌肉功能

Pam M Van Ry, Ryan D Wuebbles, Megan Key, Dean J Burkin