日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Posttransplant B cell Development and Function in Patients with B cell Positive SCID Caused by Pathogenic Variants in IL2RG and JAK3

由IL2RG和JAK3致病变异引起的B细胞阳性重症联合免疫缺陷症(SCID)患者的移植后B细胞发育和功能

Jacobsen, Eva-Maria; Khazaleh, Abdallah; Felgentreff, Kerstin; Furlan, Ingrid; Wustrau, Katharina; Sirin, Mehtap; Cario, Holger; Mayer, Benjamin; Pannicke, Ulrich; Schwarz, Klaus; Debatin, Klaus-Michael; Friedrich, Wilhelm; Schulz, Ansgar S; Hoenig, Manfred

American ginseng (Panax quinquefolius L.) extracts (G1899) reverse stress-induced behavioral abnormalities in mice

西洋参(Panax quinquefolius L.)提取物(G1899)可逆转小鼠应激诱导的行为异常

Lee, Rahmi; Wiles, McKennon J; Black, Ellison R; Roh, Seung Hyun; Bouckova, Evelina; Wustrau, Madison H; Flowers, Joshua C; Vetter, Paige E; Lee, Jaehoon; Han, Byung-Cheol; Kim, Seonil

Beyond genotype: challenges in predicting disease risk for carriers of biallelic perforin variants

超越基因型:预测双等位基因穿孔素变异携带者疾病风险的挑战

Wegehaupt, Oliver; Borisov, Oleg; Sieni, Elena; Oyen, Florian; Mann, Jasmin; Coniglio, Maria Luisa; Chinnici, Aurora; Pegoraro, Francesco; Beneforti, Linda; Gilmour, Kimberly; Moshous, Despina; de Saint Basile, Geneviève; Zhang, Wenying; Marsh, Rebecca; De Fusco, Carmela; Wustrau, Katharina; Timeus, Fabio; Micalizzi, Concetta; Gunsilius, Eberhard; Hosking, Laine; Choo, Sharon; Ghosh, Sujal; Köttgen, Anna; Lehmberg, Kai; Ehl, Stephan

Ketamine Reverses Chronic Stress-Induced Behavioral Changes via the Expression of Ca(2+)-Permeable AMPA Receptors in Mice

氯胺酮通过诱导小鼠体内Ca(2+)通透性AMPA受体的表达来逆转慢性应激诱导的行为改变

Flowers, Joshua C; Vetter, Paige E; Wiles, McKennon J; Roh, Seung Hyun; Black, Ellison R; Bouckova, Evelina; Wustrau, Madison H; Lee, Rahmi; Lee, Sang-Hun; Kim, Seonil

Case report: Granulocyte-macrophage colony-stimulating factor sargramostim did not rescue the neutrophil phenotype in two patients with JAGN1-mutant severe congenital neutropenia

病例报告:粒细胞-巨噬细胞集落刺激因子沙格司亭未能挽救两例JAGN1突变型重度先天性中性粒细胞减少症患者的中性粒细胞表型

Farmand, Susan; Aydin, Susanne Eva; Wustrau, Katharina; Böhm, Svea; Ayuk, Francis; Escherich, Gabriele; Skokowa, Julia; Müller, Ingo; Lehmberg, Kai

MAP kinase activating death domain deficiency is a novel cause of impaired lymphocyte cytotoxicity

MAP激酶激活死亡结构域缺陷是淋巴细胞细胞毒性受损的一种新原因

Schütze, Kerstin; Groß, Miriam; Cornils, Kerstin; Wustrau, Katharina; Schneppenheim, Sonja; Lenhartz, Henning; Korenke, G Christoph; Janka, Gritta; Ledig, Svea; Müller, Ingo; Ehl, Stephan; Lehmberg, Kai

Ketamine's rapid antidepressant effects are mediated by Ca2+-permeable AMPA receptors

氯胺酮的快速抗抑郁作用是由 Ca2+ 通透性 AMPA 受体介导的

Anastasiya Zaytseva #, Evelina Bouckova #, McKennon J Wiles #, Madison H Wustrau #, Isabella G Schmidt #, Hadassah Mendez-Vazquez, Latika Khatri, Seonil Kim

Reduced-Intensity/Reduced-Toxicity Conditioning Approaches Are Tolerated in XIAP Deficiency but Patients Fare Poorly with Acute GVHD

XIAP 缺陷患者可以耐受降低强度/降低毒性的预处理方案,但急性移植物抗宿主病 (GVHD) 的发生率较低。

Arnold, Danielle E; Nofal, Rofida; Wakefield, Connor; Lehmberg, Kai; Wustrau, Katharina; Albert, Michael H; Morris, Emma C; Heimall, Jennifer R; Bunin, Nancy J; Kumar, Ashish; Jordan, Michael B; Cole, Theresa; Choo, Sharon; Brettig, Tim; Speckmann, Carsten; Ehl, Stephan; Salamonowicz, Malgorzata; Wahlstrom, Justin; Rao, Kanchan; Booth, Claire; Worth, Austen; Marsh, Rebecca A

Irradiation-free re-conditioning in children following graft failure of a T cell-depleted graft from a haploidentical parent

儿童接受来自单倍体相合亲本的T细胞耗竭移植失败后,可采用无辐射再治疗。

Aydin, Susanne; Kruchen, Anne; Wustrau, Katharina; Doering, Michaela; Schrum, Johanna; Müller, Ingo

Cell Versus Cytokine - Directed Therapies for Hemophagocytic Lymphohistiocytosis (HLH) in Inborn Errors of Immunity

针对先天性免疫缺陷引起的噬血细胞性淋巴组织细胞增生症 (HLH) 的细胞与细胞因子靶向疗法

Wegehaupt, Oliver; Wustrau, Katharina; Lehmberg, Kai; Ehl, Stephan