Undocking of an extensive ciliary network induces proteostasis and cell fate switching resulting in severe primary ciliary dyskinesia
广泛的纤毛网络解离会诱导蛋白质稳态和细胞命运转变,从而导致严重的原发性纤毛运动障碍。
期刊:Science Translational Medicine
影响因子:14.6
doi:10.1126/scitranslmed.adp5173
Brody, Steven L; Pan, Jiehong; Huang, Tao; Xu, Jian; Xu, Huihui; Koenitizer, Jeffrey R; Brennan, Steven K; Nanjundappa, Rashmi; Saba, Thomas G; Rumman, Nisreen; Berical, Andrew; Hawkins, Finn J; Wang, Xiangli; Zhang, Rui; Mahjoub, Moe R; Horani, Amjad; Dutcher, Susan K