日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

PCDSOS: a novel clinical predictive tool for screening primary ciliary dyskinesia in adult bronchiectasis patients-a multicenter derivation and external validation study

PCDSOS:一种用于筛查成人支气管扩张患者原发性纤毛运动障碍的新型临床预测工具——一项多中心推导和外部验证研究

Zhou, Wangji; Wang, Lin; Chen, Qiaoling; Wang, Yaqi; Pang, Haiyu; Guo, Anhui; Wu, Aohua; Liu, Xueqi; Dai, Jinrong; Meng, Shuzhen; Wang, Rongchun; Yang, Danhui; Liu, Yaping; Zhu, Weiguo; Xu, Kai-Feng; Zhang, Xue; Luo, Hong; Tian, Xinlun

Pulmonary hemorrhage as an early clue: an integrated clinical-imaging-genetic diagnostic insight for vascular Ehlers-Danlos syndrome

肺出血作为早期线索:血管型埃勒斯-当洛斯综合征的临床-影像-遗传学综合诊断见解

Wang, Yaqi; Xie, Huaiya; Song, Lan; Xu, Kexin; Fan, Junping; Wang, Ping; Wu, Nan; Zhang, Ting; Shi, Juhong; Xu, Kai-Feng; Tian, Xinlun; Zhang, Xue

Six-minute walk distance predicting the risk of mortality in lymphangioleiomyomatosis patients

六分钟步行距离可预测淋巴管肌瘤病患者的死亡风险

Yang, Luning; Zhang, Xiaoxin; Wang, Luyi; Cheng, Chongsheng; Wang, Hanghang; Zhang, Miaoyan; Liu, Song; Xu, Wenshuai; Liu, Junya; Dai, Jinrong; Meng, Shuzhen; Yang, Yanli; Wang, Shao-Ting; Tian, Xinlun; Xu, Kai-Feng

Genetic strategies for negative or variant of uncertain significance findings in exome sequencing in hereditary bronchiectasis: a case series

遗传性支气管扩张症外显子组测序中阴性或意义未明变异结果的遗传策略:病例系列

Zhou, Wangji; Li, Yixuan; Chen, Qiaoling; Wang, Yaqi; Li, Aoyue; Lu, Wanqing; Li, Xiaogang; Xu, Kai-Feng; Zhang, Xue; Liu, Yaping; Tian, Xinlun

A biopiezocatalyst harnessing mechanical energy to enhance bioplastic production from CO(2) and organic carbon

一种利用机械能增强二氧化碳和有机碳生产生物塑料的生物压电催化剂

Tremblay, Pier-Luc; Xu, Mengying; Joya, Muhammad Babur; Wang, Yujie; He, Chun; Li, Ziqiu; Li, Lian; Xu, Kai; Feng, Yujie; Zhang, Tian

An electronic medical record retrieval system can be used to identify missed diagnosis in patients with primary ciliary dyskinesia

电子病历检索系统可用于识别原发性纤毛运动障碍患者的漏诊病例。

Zhou, Wangji; Chen, Qiaoling; Wang, Yaqi; Guo, Anhui; Wu, Aohua; Liu, Xueqi; Dai, Jinrong; Meng, Shuzhen; Situ, Christopher; Liu, Yaping; Xu, Kai-Feng; Zhu, Weiguo; Tian, Xinlun

Progression and mortality of patients with cystic fibrosis in China

中国囊性纤维化患者的病情进展和死亡率

Zhou, Wangji; Wang, Yaqi; Yang, Yanli; Sun, Yanyan; Cheng, Chongsheng; Dai, Jinrong; Meng, Shuzhen; Chen, Keqi; Zhao, Yang; Liu, Xueqi; Zhang, Dingding; Liu, Song; Zhu, Weiguo; Liu, Yaping; Xu, Kai-Feng; Tian, Xinlun

Whole exome sequencing enhances diagnosis of hereditary bronchiectasis

全外显子组测序可提高遗传性支气管扩张症的诊断率

Zhou, Wangji; Li, Yixuan; Zheng, Haixia; He, Miao; Zhang, Miaoyan; Chen, Qiaoling; Situ, Christopher; Wang, Yaqi; Zhang, Ting; Chen, Keqi; Dai, Jinrong; Meng, Shuzhen; Liu, Xueqi; Wu, Aohua; Liu, Yaping; Xu, Kai-Feng; Tian, Xinlun; Zhang, Xue

Increased malignancy risk in patients with lymphangioleiomyomatosis: findings from a Chinese cohort

淋巴管肌瘤病患者恶性肿瘤风险增加:一项中国队列研究的发现

Zhang, Xiaoxin; Cheng, Chongsheng; Wang, Hanghang; Liu, Junya; Zhao, Jiapeng; Zhang, Xinhe; Li, Xinyao; Xu, Kai-Feng

Associations of VEGF-D levels with clinical manifestations in lymphangioleiomyomatosis: a cross-sectional analysis of 631 cases.

VEGF-D 水平与淋巴管肌瘤病临床表现的相关性:631 例病例的横断面分析

Yang Luning, Wang Hanghang, Cheng Chongsheng, Zhang Miaoyan, Hu Danjing, Wang Yani, Zhang Tengyue, Zhang Xiaoxin, Liu Song, Xu Wenshuai, Liu Junya, Dai Jinrong, Meng Shuzhen, Yang Yanli, Wang Shao-Ting, Tian Xinlun, Xu Kai-Feng