日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Neuraminidase 1 secondary deficiency contributes to CNS pathology in neurological mucopolysaccharidoses via brain protein hypersialylation

神经氨酸酶 1 继发性缺乏症通过脑蛋白过度唾液酸化作用导致神经系统粘多糖贮积症的中枢神经系统病变。

Xu, TianMeng; Heon-Roberts, Rachel; Moore, Travis; Dubot, Patricia; Pan, Xuefang; Guo, Tianlin; Cairo, Christopher W; Holley, Rebecca J; Bigger, Brian; Durcan, Thomas M; Levade, Thierry; Ausseil, Jerôme; Amilhon, Bénédicte; Gorelik, Alexei; Nagar, Bhushan; Khan, Shaukat; Tomatsu, Shunji; Sturiale, Luisa; Palmigiano, Angelo; Röckle, Iris; Thiesler, Hauke; Hildebrandt, Herbert; Garozzo, Domenico; Pshezhetsky, Alexey V

Cathepsin B inhibition blocks amyloidogenesis in the mouse models of neurological lysosomal diseases MPS IIIC and sialidosis.

组织蛋白酶 B 抑制剂可阻断神经溶酶体疾病 MPS IIIC 和唾液酸沉积症小鼠模型中的淀粉样蛋白生成

Viana Gustavo M, Pan Xuefang, Fan Shuxian, Xu TianMeng, Wyatt Alexandra, Pshezhetsky Alexey V

TMIC-62. Astrocyte-expressed FASN as a novel candidate drug target for glioblastoma

TMIC-62. 星形胶质细胞表达的FASN作为胶质母细胞瘤的新型候选药物靶点

Van Doorn, C E; Tyree, J B; Jaramillo, A A; Gómez Soria, I; Finneran, Dylan; Jackman, Briana G; Desjarlais, Taylor; Morgan, Dave; Gordon, Marcia N; Kumari, Namrata; Sodders, Maggie; Marathi, Archana; Olsen, Abby; Cho, Kei Kwangwook; Bertherat, Féodora; Carlyle, Becky C; Bengoa‐Vergniory, Nora; Cowley, Sally A; Wade‐Martins, Richard; Carmichael, James Eric; Liu, Martha; Xu, TianMeng; Tuduri, Pola S; Ding, Michelle; Manseau, Frédéric S; Williams, Sylvain; da Silva Mansano, Naira; Wray, Susan; Girijala, Veena; Farias, Antolin Serrano; Suvarnapathaki, Sanika; Traversa, Benito; Aude, Carlos Andres; Torroella, Jordina Rincon; Yi, Li; Massai, Francesco; Moussaud, Simon; Iyer, Preeti; Fitzek, Martina; Preston, Marian; Gaetani, Massimiliano; Schmierer, Bernhard; Gustavsson, Anna-Lena; Smith, Dave; Davis, Andrew; Mega, Alessandro; Östman, Arne

Secondary deficiency of neuraminidase 1 contributes to CNS pathology in neurological mucopolysaccharidoses via hypersialylation of brain glycoproteins

神经氨酸酶 1 的继发性缺乏通过脑糖蛋白的过度唾液酸化,导致神经系统粘多糖贮积症的中枢神经系统病变。

Xu, TianMeng; Heon-Roberts, Rachel; Moore, Travis; Dubot, Patricia; Pan, Xuefang; Guo, Tianlin; Cairo, Christopher W; Holley, Rebecca; Bigger, Brian; Durcan, Thomas M; Levade, Thierry; Ausseil, Jerôme; Amilhon, Bénédicte; Gorelik, Alexei; Nagar, Bhushan; Sturiale, Luisa; Palmigiano, Angelo; Röckle, Iris; Thiesler, Hauke; Hildebrandt, Herbert; Garozzo, Domenico; Pshezhetsky, Alexey V

Exploring the needs and coping strategies of family caregivers taking care of dying patients at home: a field study

探索在家照顾临终患者的家庭照护者的需求和应对策略:一项实地研究

Zhang, Xiaotian; Xu, Tianmeng; Qin, Yuan; Wang, Minghui; Li, Zhaoyu; Song, Jingyu; Tang, Qianqian; Wang, Zidan; Xu, Lijie; Wu, Lingling; Yue, Peng