Huntingtin preserves mitochondrial genome integrity in neurons, which is impaired in Huntington's disease.
亨廷顿蛋白能够维持神经元中线粒体基因组的完整性,而亨廷顿病会损害这种完整性
期刊:
影响因子:
doi:10.1101/2025.07.24.666629
Pradhan Subrata, Gaikwad Sagar, Tsai Chi-Lin, Smith Charlene, Zhang Nan, Bush Keegan, Chakraborty Anirban, Yuan Subo, Choudhary Sanjeev, Keene C Dirk, Ellerby Lisa M, Hazra Tapas K, La Spada Albert R, Wairkar Yogesh P, Ashizawa Tatsuo, Tainer John A, Pandita Tej K, Thompson Leslie M, Sarkar Partha S