日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Prevention of ubiquitination at K6 and K9 in mutant huntingtin exacerbates disease pathology in a knock-in mouse model

在基因敲入小鼠模型中,突变亨廷顿蛋白K6和K9位点泛素化的抑制会加剧疾病病理。

Qi, Pengfei; Yu-Taeger, Libo; Han, Hezhou; Zhou, Junbo; Singer-Mikosch, Elisabeth; Casadei, Nicolas; Riess, Olaf; Ziv, Noam E; Ciechanover, Aaron; Phuc Nguyen, Hoa Huu

Intravenous MSC-Treatment Improves Impaired Brain Functions in the R6/2 Mouse Model of Huntington's Disease via Recovered Hepatic Pathological Changes

静脉注射 MSC 治疗可通过恢复肝脏病理变化来改善 R6/2 亨廷顿氏病小鼠模型中受损的脑功能

Libo Yu-Taeger, Ali El-Ayoubi, Pengfei Qi, Lusine Danielyan, Hoa Huu Phuc Nguyen

Loss-of-function of GNAL dystonia gene impairs striatal dopamine receptors-mediated adenylyl cyclase/ cyclic AMP signaling pathway

GNAL 肌张力障碍基因功能丧失会损害纹状体多巴胺受体介导的腺苷酸环化酶/环磷酸腺苷信号通路

Ilham El Atiallah, Giulia Ponterio, Maria Meringolo, Giuseppina Martella, Giuseppe Sciamanna, Annalisa Tassone, Martina Montanari, Maria Mancini, Antonio N Castagno, Libo Yu-Taeger, Hoa Huu Phuc Nguyen, Paola Bonsi, Antonio Pisani

Intronic enhancers of the human SNCA gene predominantly regulate its expression in brain in vivo

人类SNCA基因的内含子增强子主要调控其在体内大脑中的表达。

Cheng, Fubo; Zheng, Wenxu; Liu, Chang; Barbuti, Peter Antony; Yu-Taeger, Libo; Casadei, Nicolas; Huebener-Schmid, Jeannette; Admard, Jakob; Boldt, Karsten; Junger, Katrin; Ueffing, Marius; Houlden, Henry; Sharma, Manu; Kruger, Rejko; Grundmann-Hauser, Kathrin; Ott, Thomas; Riess, Olaf

DYT6 mutated THAP1 is a cell type dependent regulator of the SP1 family

DYT6 突变的 THAP1 是 SP1 家族的细胞类型依赖性调节剂

Fubo Cheng, Wenxu Zheng, Peter Antony Barbuti, Paola Bonsi, Chang Liu, Nicolas Casadei, Giulia Ponterio, Maria Meringolo, Jakob Admard, Claire Marie Dording, Libo Yu-Taeger, Huu Phuc Nguyen, Kathrin Grundmann-Hauser, Thomas Ott, Henry Houlden, Antonio Pisani, Rejko Krüger, Olaf Riess

Evidences for Mutant Huntingtin Inducing Musculoskeletal and Brain Growth Impairments via Disturbing Testosterone Biosynthesis in Male Huntington Disease Animals

有证据表明突变型亨廷顿蛋白会通过干扰雄性亨廷顿病动物的睾酮生物合成而诱发肌肉骨骼和大脑生长障碍

Libo Yu-Taeger, Arianna Novati, Jonasz Jeremiasz Weber, Elisabeth Singer-Mikosch, Ann-Sophie Pabst, Fubo Cheng, Carsten Saft, Jennifer Koenig, Gisa Ellrichmann, Taneli Heikkinen, Mahmoud A Pouladi, Olaf Riess, Huu Phuc Nguyen

Differential Cellular Balance of Olfactory and Vomeronasal Epithelia in a Transgenic BACHD Rat Model of Huntington's Disease

亨廷顿氏病转基因 BACHD 大鼠模型中嗅觉和犁鼻上皮细胞的差异细胞平衡

Lina-Marielle Krysewski, Nicole Power Guerra, Annika Glatzel, Carsten Holzmann, Veronica Antipova, Oliver Schmitt, Libo Yu-Taeger, Huu Phuc Nguyen, Andreas Wree, Martin Witt

Site-specific ubiquitination of pathogenic huntingtin attenuates its deleterious effects

致病性亨廷顿蛋白的位点特异性泛素化可减弱其有害作用。

Hakim-Eshed, Vicky; Boulos, Ayub; Cohen-Rosenzweig, Chen; Yu-Taeger, Libo; Ziv, Tamar; Kwon, Yong Tae; Riess, Olaf; Phuc Nguyen, Hoa Huu; Ziv, Noam E; Ciechanover, Aaron

Impaired dopamine- and adenosine-mediated signaling and plasticity in a novel rodent model for DYT25 dystonia

DYT25 肌张力障碍新型啮齿动物模型中多巴胺和腺苷介导的信号传导和可塑性受损

Libo Yu-Taeger, Thomas Ott, Paola Bonsi, Celina Tomczak, Zinah Wassouf, Giuseppina Martella, Giuseppe Sciamanna, Paola Imbriani, Giulia Ponterio, Annalisa Tassone, Julia M Schulze-Hentrich, Rose Goodchild, Olaf Riess, Antonio Pisani, Kathrin Grundmann-Hauser, Huu Phuc Nguyen

Intranasal Administration of Mesenchymal Stem Cells Ameliorates the Abnormal Dopamine Transmission System and Inflammatory Reaction in the R6/2 Mouse Model of Huntington Disease

间充质干细胞鼻腔给药改善亨廷顿病 R6/2 小鼠模型中的异常多巴胺传递系统和炎症反应

Libo Yu-Taeger, Janice Stricker-Shaver, Katrin Arnold, Patrycja Bambynek-Dziuk, Arianna Novati, Elisabeth Singer, Ali Lourhmati, Claire Fabian, Janine Magg, Olaf Riess, Matthias Schwab, Alexandra Stolzing, Lusine Danielyan, Hoa Huu Phuc Nguyen