A novel Gerstmann-Sträussler-Scheinker disease mutation defines a precursor for amyloidogenic 8 kDa PrP fragments and reveals N-terminal structural changes shared by other GSS alleles
一种新的 Gerstmann-Sträussler-Scheinker 病突变定义了淀粉样变性 8 kDa PrP 片段的前体,并揭示了其他 GSS 等位基因共有的 N 端结构变化
期刊:PLoS Pathogens
影响因子:5.5
doi:10.1371/journal.ppat.1006826
Robert C C Mercer, Nathalie Daude, Lyudmyla Dorosh, Ze-Lin Fu, Charles E Mays, Hristina Gapeshina, Serene L Wohlgemuth, Claudia Y Acevedo-Morantes, Jing Yang, Neil R Cashman, Michael B Coulthart, Dawn M Pearson, Jeffrey T Joseph, Holger Wille, Jiri G Safar, Gerard H Jansen, Maria Stepanova, Brian D