日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Hematopoietic stem cell transplantation for purine nucleoside phosphorylase deficiency: an EBMT-IEWP retrospective study

造血干细胞移植治疗嘌呤核苷磷酸化酶缺乏症:一项EBMT-IEWP回顾性研究

Herrmann, Uli S; Felber, Matthias; Worth, Austen; Haskologlu, Sule; Dogu, Figen; Lewis, Victor A; Strahm, Brigitte; Groll, Andreas; Gennery, Andrew R; Hauck, Fabian; Wynn, Robert; Coussons, Mary; Meyts, Isabelle; Lindemans, Caroline; Bordon, Victoria; Bredius, Robbert G M; Kühl, Jörn-Sven; Völler, Mirjam; Zirngibl, Felix; Zaidman, Irina; Laberko, Alexandra; Zeilhofer, Ulrike; Hauri-Hohl, Mathias; Lankester, Arjan; Ikinciogullari, Aydan; Guilcher, Gregory M T; Hackenberg, Annette; Yeşilipek, Akif; Davies, Graham; Rao, Kanchan; Hershfield, Michael Steven; Parikh, Suhag H; Gilbert, Patrick; Bettoni da Cunha Riehm, Claudia; Albert, Michael H; Schulz, Ansgar S; Hönig, Manfred; Neven, Bénédicte; Güngör, Tayfun

Allogeneic haematopoietic stem-cell transplantation for children with refractory systemic juvenile idiopathic arthritis and associated lung disease: outcomes from an international, retrospective cohort study

异基因造血干细胞移植治疗难治性全身型幼年特发性关节炎合并肺部疾病患儿:一项国际回顾性队列研究的结果

Matt, Michael G; Drozdov, Daniel; Bendstrup, Elisabeth; Glerup, Mia; Hauge, Ellen-Margrethe; Masmas, Tania; Schneider, Elvira Cannizzaro; Zeilhofer, Ulrike B; Abu-Arja, Rolla F; Driest, Kyla D; Oved, Joseph H; Onel, Karen; Ebens, Christen L; Chellapandian, Deepakbabu; Chandrakasan, Shanmuganathan; Prahalad, Sampath; Roth, Johannes; Prockop, Susan E; Silva, Juliana; Schapiro, Andrew H; Towe, Christopher; Chandra, Sharat; Grom, Alexei; Schulert, Grant S; Marsh, Rebecca A

A role for leucine-rich, glioma inactivated 1 in regulating pain sensitivity

富含亮氨酸的胶质瘤失活蛋白1在调节疼痛敏感性中的作用

Farah, Adham; Patel, Ryan; Poplawski, Piotr; Wastie, Benjamin J; Tseng, Mandy; Barry, Allison M; Daifallah, Omar; Dubb, Akash; Paul, Ivan; Cheng, Hoi Lao; Feroz, Faisal; Su, Yuhe; Chan, Marva; Zeilhofer, Hanns Ulrich; Price, Theodore J; Bennett, David L; Bannister, Kirsty; Dawes, John M

Light-Activated Agonist-Potentiator of GABA(A) Receptors for Reversible Neuroinhibition in Wildtype Mice

光激活的GABA(A)受体激动剂-增强剂,可对野生型小鼠产生可逆性神经抑制作用

Maleeva, Galyna; Nin-Hill, Alba; Wirth, Ulrike; Rustler, Karin; Ranucci, Matteo; Opar, Ekin; Rovira, Carme; Bregestovski, Piotr; Zeilhofer, Hanns Ulrich; König, Burkhard; Alfonso-Prieto, Mercedes; Gorostiza, Pau

Reducing Mortality and Morbidity in Children with Severe Combined Immunodeficiency in Switzerland: the Role of Newborn Screening

降低瑞士重症联合免疫缺陷患儿的死亡率和发病率:新生儿筛查的作用

Soomann, Maarja; Prader, Seraina; Pinto Monteiro, Aline; Zeilhofer, Ulrike; Hauri-Hohl, Mathias; Güngör, Tayfun; Pachlopnik Schmid, Jana; Trück, Johannes; Felber, Matthias

γ1 GABA(A) Receptors in Spinal Nociceptive Circuits

脊髓伤害性回路中的γ1 GABA(A)受体

Neumann, Elena; Cramer, Teresa; Acuña, Mario A; Scheurer, Louis; Beccarini, Camilla; Luscher, Bernhard; Wildner, Hendrik; Zeilhofer, Hanns Ulrich

Inhibitory Kcnip2 neurons of the spinal dorsal horn control behavioral sensitivity to environmental cold

脊髓背角的抑制性 Kcnip2 神经元控制对环境寒冷的行为敏感性

Gioele W Albisetti, Robert P Ganley, Francesca Pietrafesa, Karolina Werynska, Marília Magalhaes de Sousa, Rebecca Sipione, Louis Scheurer, Michael R Bösl, Pawel Pelczar, Hendrik Wildner, Hanns Ulrich Zeilhofer

c-Maf-positive spinal cord neurons are critical elements of a dorsal horn circuit for mechanical hypersensitivity in neuropathy

c-Maf 阳性脊髓神经元是神经病变机械超敏反应背角回路的关键元素

Noémie Frezel, Matteo Ranucci, Edmund Foster, Hagen Wende, Pawel Pelczar, Raquel Mendes, Robert P Ganley, Karolina Werynska, Simon d'Aquin, Camilla Beccarini, Carmen Birchmeier, Hanns Ulrich Zeilhofer, Hendrik Wildner

Targeted anatomical and functional identification of antinociceptive and pronociceptive serotonergic neurons that project to the spinal dorsal horn

针对投射到脊髓背角的抗伤害性和促伤害性血清素神经元进行有针对性的解剖和功能识别

Robert Philip Ganley, Marilia Magalhaes de Sousa, Kira Werder, Tugce Öztürk, Raquel Mendes, Matteo Ranucci, Hendrik Wildner, Hanns Ulrich Zeilhofer

Targeting the interaction of GABAB receptors with CaMKII with an interfering peptide restores receptor expression after cerebral ischemia and inhibits progressive neuronal death in mouse brain cells and slices

利用干扰肽靶向 GABAB 受体与 CaMKII 的相互作用,可恢复脑缺血后的受体表达,并抑制小鼠脑细胞和脑切片中的进行性神经元死亡

Karthik Balakrishnan, Mohammad Hleihil, Musadiq A Bhat, Robert P Ganley, Markus Vaas, Jan Klohs, Hanns Ulrich Zeilhofer, Dietmar Benke