日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Acceptability and Determinants for Implementation of the EnzySystem, a Novel Near-Patient Testing Platform for Haemophilia A

EnzySystem(一种新型的甲型血友病床旁检测平台)的可接受性及其实施决定因素

Bavinck, Aernoud P; Davis, Kyle; van Engelshoven, Lisa; van Lier, Monique G; Hamacher, Tanja; Blijlevens, Nicole M A; Shapiro, Amy; Schols, Saskia E M; van Heerde, Waander L

Clinical phenotype and pathophysiological mechanisms underlying qualitative low VWF

临床表型和低VWF相关的病理生理机制

Atiq, Ferdows; Blok, Robin; van Kwawegen, Calvin B; Hulshof, Anne-Marije; Doherty, Dearbhla; Lavin, Michelle; van der Bom, Johanna G; O'Connell, Niamh M; de Meris, Joke; Ryan, Kevin; Schols, Saskia E M; van Heerde, Waander L; Doyle, Mairead; Byrne, Mary; Heubel-Moenen, Floor C J I; van Galen, Karin P M; Preston, Roger J S; Cnossen, Marjon H; Fijnvandraat, Karin; Baker, Ross I; Meijer, Karina; James, Paula; Di Paola, Jorge; Eikenboom, Jeroen; Leebeek, Frank W G; O'Donnell, James S

Consensus-Based Expert Recommendations for Diagnosis and Clinical Management of Vanishing White Matter

基于共识的专家建议:白质消失的诊断和临床管理

van Voorst, Romy J; Schoenmakers, Daphne H; Bonkowsky, Joshua L; Vanderver, Adeline; Krägeloh-Mann, Ingeborg; Bernard, Geneviève; Bertini, Enrico; Fatemi, Ali; Sgobbi, Paulo V; Wolf, Nicole I; Groeschel, Samuel; Tonduti, Davide; Sevin, Caroline; Orthmann-Murphy, Jennifer L; Schöls, Ludger; Salsano, Ettore; Brais, Bernard; Jaffe, Nicole; Ter Horst, Kasper W; Hannema, Sabine E; Hayes, Katherine G; Meyburg, Jochen; van Heerde, Marc; Sbrocchi, Anne Marie; van Spaendonk, Rosalina; Thiffault, Isabelle; Hofsteenge, Geesje H; Sudmeier-Broek, Carolina; Timmer, Corrie; Skwirut, Donna; Buck, Allyson; Hollberg, Bret; Chapleau, Ron; Dekker, Hanka; Campbell, Susan G; Abbink, Truus E M; Leferink, Prisca S; van der Knaap, Marjo S

Measuring FVIII Activity and Thrombin Generation Simultaneously With a Novel Point of Care Platform (EnzySystem HemA): Qualitative Usability Evaluation

利用新型即时检测平台(EnzySystem HemA)同时测量FVIII活性和凝血酶生成:定性可用性评估

Bavinck, Aernoud; Schols, Saskia E M; Teunissen, Wilfred; Shapiro, Amy; Blijlevens, Nicole M A; Davis, Kyle; van Heerde, Waander

The spectrum of neutralizing and non-neutralizing anti-FVIII antibodies in a nationwide cohort of 788 persons with hemophilia A

在一项全国性队列研究中,788名A型血友病患者体内中和性和非中和性抗FVIII抗体的谱系分析

Oomen, Ilja; Verhagen, Marieke; Miranda, Mariarosaria; Allacher, Peter; Beckers, Erik A M; Blijlevens, Nicole M A; van der Bom, Johanna G; Coppens, Michiel; Driessens, Mariëtte; Eikenboom, Jeroen C J; Fijnvandraat, Karin; Hassan, Shermarke; van Heerde, Waander L; Hooimeijer, H Louise; Jansen, Joop H; Kaijen, Paul; Leebeek, Frank W G; Meijer, Daniëlle; Paul, Helmut; Rijpma, Sanna R; Rosendaal, Frits R; Smit, Cees; van Vulpen, Lize F D; Voorberg, Jan; Schols, Saskia E M; Gouw, Samantha C

Pharmacokinetic-Pharmacodynamic Modelling in Hemophilia A: Relating Thrombin and Plasmin Generation to Factor VIII Activity After Administration of a VWF/FVIII Concentrate

A型血友病的药代动力学-药效学模型:VWF/FVIII浓缩物给药后凝血酶和纤溶酶生成与VIII因子活性的关系

Valke, Lars L F G; Cloesmeijer, Michael E; Mansouritorghabeh, Hassan; Barteling, Wideke; Blijlevens, Nicole M A; Cnossen, Marjon H; Mathôt, Ron A A; Schols, Saskia E M; van Heerde, Waander L

Feasibility of a quality-improvement program based on routinely collected health outcomes in Dutch primary care physical therapist practice: a mixed-methods study

基于荷兰基层医疗理疗师实践中常规收集的健康结果的质量改进计划的可行性:一项混合方法研究

Smeekens, Lsf; Verburg, A C; Maas, Mjm; van Heerde, R; van Kerkhof, A; van der Wees, P J

In patients with hemophilia, a decreased thrombin generation profile is associated with a severe bleeding phenotype

在血友病患者中,凝血酶生成能力下降与严重的出血表型相关。

Verhagen, Marieke J A; van Heerde, Waander L; van der Bom, Johanna G; Beckers, Erik A M; Blijlevens, Nicole M A; Coppens, Michiel; Gouw, Samantha C; Jansen, Joop H; Leebeek, Frank W G; van Vulpen, Lize F D; Meijer, Daniëlle; Schols, Saskia E M

Importance of Genotyping in von Willebrand Disease to Elucidate Pathogenic Mechanisms and Variability in Phenotype

基因分型在血管性血友病中的重要性:阐明致病机制和表型变异

Atiq, Ferdows; Boender, Johan; van Heerde, Waander L; Tellez Garcia, Juan M; Schoormans, Selene C; Krouwel, Sandy; Cnossen, Marjon H; Laros-van Gorkom, Britta A P; de Meris, Joke; Fijnvandraat, Karin; van der Bom, Johanna G; Meijer, Karina; van Galen, Karin P M; Eikenboom, Jeroen; Leebeek, Frank W G

Desmopressin response depends on the presence and type of genetic variants in patients with type 1 and type 2 von Willebrand disease

去氨加压素反应取决于 1 型和 2 型血管性血友病患者是否存在基因变异及其类型。

Atiq, Ferdows; Heijdra, Jessica; Snijders, Fleur; Boender, Johan; Kempers, Eva; van Heerde, Waander L; Maas, Dominique P M S M; Krouwel, Sandy; Schoormans, Selene C; de Meris, Joke; Schols, Saskia E M; van Galen, Karin P M; van der Bom, Johanna G; Cnossen, Marjon H; Meijer, Karina; Fijnvandraat, Karin; Eikenboom, Jeroen; Leebeek, Frank W G