日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Mitochondrial bioenergetics and cardiolipin remodeling abnormalities in mitochondrial trifunctional protein deficiency

线粒体三功能蛋白缺乏症中的线粒体生物能量学和心磷脂重塑异常

Eduardo Vieira Neto, Meicheng Wang, Austin J Szuminsky, Lethicia Ferraro, Erik Koppes, Yudong Wang, Clinton Van't Land, Al-Walid Mohsen, Geancarlo Zanatta, Areeg H El-Gharbawy, Tamil S Anthonymuthu, Yulia Y Tyurina, Vladimir A Tyurin, Valerian Kagan, Hülya Bayır, Jerry Vockley

CLPX regulates mitochondrial fatty acid β-oxidation in liver cells

CLPX 调节肝细胞线粒体脂肪酸 β-氧化

Ko Suzuki, Yoshiko Kubota, Kiriko Kaneko, Costantine Chasama Kamata, Kazumichi Furuyama

Mitochondrial morphology, bioenergetics and proteomic responses in fatty acid oxidation disorders

脂肪酸氧化障碍中的线粒体形态、生物能量学和蛋白质组学反应

Serena Raimo, Gabriella Zura-Miller, Hossein Fezelinia, Lynn A Spruce, Iordanis Zakopoulos, Al-Walid Mohsen, Jerry Vockley, Harry Ischiropoulos

Targeting viperin to the mitochondrion inhibits the thiolase activity of the trifunctional enzyme complex

将毒蛇素靶向线粒体可抑制三功能酶复合物的硫解酶活性

Arti B Dumbrepatil, Kelcie A Zegalia, Keerthi Sajja, Robert T Kennedy, E Neil G Marsh