Mitochondrial dysfunction and Ca(2+) dysregulation in human iPSC-derived neurons carrying presenilin-1 mutation arise under stress via an MCU-1-independent mechanism.
携带早老素-1突变的人类iPSC衍生神经元在应激下通过MCU-1非依赖性机制出现线粒体功能障碍和Ca(2+)失调。
期刊:Scientific Reports
影响因子:3.9
doi:10.1038/s41598-026-35597-0
Wilson Carlos, Galeano Pablo, Remedi MarÃa Mónica, Novack Gisela Vanina, Campanelli Lorenzo, Gastaldi Laura, Miglietta Esteban, Rossi Andres Hugo, Olivar Natividad, Brusco Luis Ignacio, Castaño Eduardo Miguel, Cáceres Alfredo, Morelli Laura