日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Differential response to ofatumumab in anti-AChR and anti-MuSK positive myasthenia gravis patients: a single-center retrospective study

抗乙酰胆碱受体抗体(AChR)和抗肌肉特异性酪氨酸激酶抗体(MuSK)阳性重症肌无力患者对奥法妥木单抗的反应差异:一项单中心回顾性研究

Zhou, Qian; Ouyang, Yuzhen; Jiang, Fei; Zeng, Qiuming; He, Ting; Wen, Zeyi; Shi, Guanzhong; Dong, Xiaohua; Cai, Haobing; Xiang, Wei; Su, Miao; Li, Kailin; Yang, Huan

IgA autoantibodies demonstrate a novel mechanism of MuSK myasthenia gravis pathology

IgA自身抗体揭示了MuSK重症肌无力病理学的一种新机制

Masi, Gianvito; Chen, Kangzhi; Bayer, Alexandra C; Bayarri-Olmos, Rafael; Pham, Minh C; Wallace, Annabel; Falso, Silvia; Evoli, Amelia; Iorio, Raffaele; Hoehn, Kenneth B; Iwasaki, Akiko; Nowak, Richard J; O'Connor, Kevin C

Muskelin is a substrate adaptor of the highly regulated Drosophila embryonic CTLH E3 ligase

Muskelin是果蝇胚胎CTLH E3连接酶的一种底物适配器,该酶受到高度调控。

Chloe A Briney #,Jesslyn C Henriksen #,Chenwei Lin,Lisa A Jones,Leif Benner,Addison B Rains,Roxana Gutierrez,Philip R Gafken,Olivia S Rissland

COVID-19-associated delayed-onset MuSK-positive myasthenia gravis presenting solely with respiratory failure: a case report

COVID-19 相关迟发性 MuSK 阳性重症肌无力,仅表现为呼吸衰竭:病例报告

Cao, Xiao-Guang; Ni, Jun-Xi; Zhu, Xiong-Feng; Meng, Hua-Dong; Huang, Chong-Jian

Efgartigimod combined with rituximab helps improve the symptoms and reduce the use of corticosteroids in patients with MuSK antibody-positive MG: a single case report

依夫加替莫德联合利妥昔单抗可改善MuSK抗体阳性重症肌无力患者的症状并减少糖皮质激素的使用:一例病例报告

Zheng, Xiujun; Wang, Jing; Cai, Tongtong; Zhou, Houshi

Inhibition of Muscle-Specific Protein Kinase (MuSK) Releases Organophosphate-Aged Acetylcholinesterase (AChE) from C2C12 Cells.

抑制肌肉特异性蛋白激酶(MuSK)可从 C2C12 细胞中释放有机磷酸酯老化的乙酰胆碱酯酶(AChE)。

Moncada-Restrepo Monica, Eysoldt Sarah, Medina Jeronimo, Di Guida Valentina, Chambers Jeremy W

MuSK Regulates Neuromuscular Junction Nav1.4 Localization and Excitability

MuSK调节神经肌肉接头Nav1.4的定位和兴奋性

Fish, Lauren A; Ewing, Madison D; Rich, Kelly A; Xi, Chengjie; Chen, Isabella; Jaime, Diego; Madigan, Laura A; Wang, Xueyong; Shahtout, Justin L; Feder, Rita E; Funai, Katsuhiko; Christian, Jan L; Wharton, Kristi A; Rich, Mark M; Arnold, William D; Fallon, Justin R

Efficacy and safety of rituximab in anti-MuSK myasthenia Gravis: a systematic review and meta-analysis

利妥昔单抗治疗抗MuSK重症肌无力的疗效和安全性:系统评价和荟萃分析

Chayanopparat, Siripong; Banyatcharoen, Perasin; Jitprapaikulsan, Jiraporn; Uawithya, Ekdanai; Apiraksattayakul, Natnasak; Viarasilpa, Vasinee

Differential Scanning Calorimetry as a Monitoring Tool for the Effectiveness of Therapeutic Plasma Exchange in Anti-AChR Myasthenia Gravis, Anti-MuSK Myasthenia Gravis, and Myasthenic Syndrome: A Case Series

差示扫描量热法作为监测抗乙酰胆碱受体(AChR)重症肌无力、抗肌肉特异性酪氨酸激酶(MuSK)重症肌无力和肌无力综合征治疗性血浆置换疗效的工具:病例系列研究

Ilieva, Viktoria; Tenchov, Boris; Virovska, Daniela; Nencheva, Denitsa; Kalayanov, Maksim; Farfarov, Alexandar; Yamakova, Yordanka; Abarova, Silviya

SRSF6 and SRSF1 coordinately enhance the inclusion of human MUSK exon 10 to generate a Wnt-sensitive MuSK isoform

SRSF6 和 SRSF1 协同增强人 MUSK 外显子 10 的插入,从而生成 Wnt 敏感的 MuSK 亚型。

Farhana Nasrin ,Preeti Nagar ,Md Rafikul Islam ,Shabiha Afroj Heeamoni ,Md Mahbub Hasan ,Kinji Ohno ,Mohammad Alinoor Rahman