日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Evolutionary insights and structural characterization guide the development of RAG1/RAG2-deficient swine models for immunological research

进化论见解和结构表征指导着RAG1/RAG2缺陷型猪模型在免疫学研究中的应用。

Zhang, Rui; Wu, Yunpeng; Sun, Tianqi; Luan, Tianqi; Ren, Yanling; Zhang, Yilin; Lin, Lihao; Meng, Teng; Wang, Jin; Qiu, Yefeng

RAG1-independent atypical B cell development in chickens: Redefining the role of RAG1 in avian immunology

鸡体内不依赖于RAG1的非典型B细胞发育:重新定义RAG1在禽类免疫学中的作用

Woo, Seung Je; Lee, Kyung Youn; Kim, Jin Lee; Kim, Tae Hyun; Han, Jae Yong

Proximity-based proteomic profiling uncovers distinct interactome of human RAG1 and RAG2

基于邻近性的蛋白质组学分析揭示了人RAG1和RAG2的独特相互作用组

Hong, Junye; Zheng, Xueming; Wei, Kunyu; Lu, Qingyi; Huang, Guangrui; Zhang, Yuhang

Safety and efficacy of gene therapy for RAG1-deficient SCID

RAG1缺陷型重症联合免疫缺陷症基因治疗的安全性和有效性

Staal, Frank J T; Pike-Overzet, Karin; de Kivit, Sander; Ott de Bruin, Lisa; Mamede, Lucia; Pergent, Martine; Prevot, Johan; Rothe, Michael; Schambach, Axel; Lankester, Arjan

Response to: Safety and efficacy considerations of HSC-based gene therapy for RAG1-deficient SCID

针对“基于造血干细胞的基因疗法治疗RAG1缺陷型重症联合免疫缺陷症的安全性和有效性考量”的回应

Montini, Eugenio; Naldini, Luigi; Booth, Claire; Kohn, Donald B; Aiuti, Alessandro

How RAG1/2 evolved from ancestral transposases to initiate V(D)J recombination without transposition

RAG1/2 如何从祖先转座酶进化而来,从而在不发生转座的情况下启动 V(D)J 重组

Chen, Xuemin; Yao, Liangrui; Li, Wenwen; Ma, Shanshan; Yuan, Xingyun; Yang, Yang; Yuan, Yuan; Liu, Yumei; Liu, Lan; Wang, Huaibin; Gellert, Martin; Yang, Wei

RAG1 lentiviral gene therapy restores T-cell development of RAG1-SCID patient cells in artificial thymic organoids

RAG1慢病毒基因疗法可恢复RAG1-SCID患者细胞在人工胸腺类器官中的T细胞发育

Meng, Xiaolin; Melsen, Janine E; van der Holst, Rosalie; de Mooij, Bas; Vloemans, Sandra; van Eggermond, Marja; Berghuis, Dagmar; Lankester, Arjan C; de Kivit, Sander; Pike-Overzet, Karin; Langerak, Anton W; Staal, Frank J T; Ott de Bruin, Lisa M; Canté-Barrett, Kirsten

Tracing Genetic Divergence and Phylogeographic Patterns of Gekko gecko Linnaeus, 1758 (Squamata: Gekkonidae) Across Southeast Asia Using RAG1 Sequence

使用 RAG1 序列追踪东南亚地区壁虎 Linnaeus, 1758(有鳞目:壁虎科)的遗传分化和系统发育地理学模式

Laotongsan, Panida; Pilap, Warayutt; Jaroenchaiwattanachote, Chavanut; Pasorn, Pattana; Saijuntha, Jatupon; Tawong, Wittaya; Kongbuntad, Watee; Wongpakam, Komgrit; Inkhavilay, Khamla; Sithirith, Mak; Tantrawatpan, Chairat; Saijuntha, Weerachai

The ClinGen Severe Combined Immunodeficiency Disease Variant Curation Expert Panel: Specifications for classification of variants in ADA , DCLRE1C , IL2RG , IL7R , JAK3 , RAG1 , and RAG2

ClinGen 重症联合免疫缺陷病变异注释专家组:ADA、DCLRE1C、IL2RG、IL7R、JAK3、RAG1 和 RAG2 变异分类规范

Jacovas, Vanessa C; Zelnick, Michelle; McNulty, Shannon; Ross, Justyne E; Khurana, Namrata; Pan, Xueyang; Nieto, Alejandro; Martin, Shiloh; McLean, Benjamin; Elnagheeb, Marwa A; Cowan, Morton J; Puck, Jennifer M; Hershfield, Mike; Verbsky, James; Walter, Jolan; Allenspach, Eric; Chan, Alice Y; van Oers, Nicolai S C; Ghosh, Rajarshi; Piazza, Megan; Yuan, Bo; Notarangelo, Luigi D; Johnson, Britt A; Chinn, Ivan K

Factors associated with and kinetics of anti-IFN-α autoantibodies in RAG1/2 deficiency

RAG1/2缺陷中抗IFN-α自身抗体的相关因素及动力学

Wang, Chen; Potts, David Evan; Sun, Bijun; Toth, Marta; Ujhazi, Boglarka; Sharapova, Svetlana; Miller, Rahim; Rosen, Lindsey; Yilmaz, Melis; Larsen, Kellie; Delmonte, Ottavia M; Poskitt, Laura E; Allenspach, Eric J; de la Morena, Maria Teresa; Ward, Brant R; Hernandez, Joseph D; Geier, Christoph B; Bolanos, Hannie Zomer; Al-Herz, Waleed; Kuijpers, Taco W; Petrov, Andrej A; Savic, Sinisa; Chen, Karin; Westermann-Clark, Emma; Dutmer, Cullen M; Kanariou, Maria G; Adeli, Mehdi; Palma, Paolo; Bonfim, Carmem; Lycopoulou, Evangelia; Wolska-Kusnierz, Beata; de Barros Dorna, Mayra; Dbaibo, Ghassan; Bleesing, Jack; Moshous, Despina; Licciardi, Francesco; Neven, Benedicte; Schuetz, Catharina; Geha, Raif S; Miano, Maurizio; Goldman, Stanton C; Raasch, Jason; Gonzalez-Granado, Luis Ignacio; Celmeli, Fatih; Baris, Safa; Abraham, Roshini S; Buchbinder, David K; Butte, Manish J; Wang, Ji-Yang; Wang, Xiaochuan; Strauss, Kevin A; Holland, Steven M; Notarangelo, Luigi D; Walter, Jolan E