Fibrillin microfibril structure identifies long-range effects of inherited pathogenic mutations affecting a key regulatory latent TGFβ-binding site
纤维蛋白微纤维结构可识别影响关键调节性潜在 TGFβ 结合位点的遗传致病突变的长期影响
期刊:Nature Structural & Molecular Biology
影响因子:12.5
doi:10.1038/s41594-023-00950-8
Alan R F Godwin, Rana Dajani, Xinyang Zhang, Jennifer Thomson, David F Holmes, Christin S Adamo, Gerhard Sengle, Michael J Sherratt, Alan M Roseman, Clair Baldock
信号转导
WB
TGF-β
Human
TMEFF1/Tomoregulin-1