PPAR-gamma agonist pioglitazone recovers mitochondrial quality control in fibroblasts from PITRM1-deficient patients
PPAR-γ激动剂吡格列酮可恢复PITRM1缺陷患者成纤维细胞的线粒体质量控制
期刊:Frontiers in Pharmacology
影响因子:4.4
doi:10.3389/fphar.2023.1220620
Alessia Di Donfrancesco ,Christian Berlingieri ,Marta Giacomello ,Chiara Frascarelli ,Ana Paula Magalhaes Rebelo ,Laurence A Bindoff ,Segel Reeval ,Paul Renbaum ,Filippo M Santorelli ,Giulia Massaro ,Carlo Viscomi ,Massimo Zeviani ,Daniele Ghezzi ,Emanuela Bottani ,Dario Brunetti