日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

PPAR-gamma agonist pioglitazone recovers mitochondrial quality control in fibroblasts from PITRM1-deficient patients

PPAR-γ激动剂吡格列酮可恢复PITRM1缺陷患者成纤维细胞的线粒体质量控制

Alessia Di Donfrancesco ,Christian Berlingieri ,Marta Giacomello ,Chiara Frascarelli ,Ana Paula Magalhaes Rebelo ,Laurence A Bindoff ,Segel Reeval ,Paul Renbaum ,Filippo M Santorelli ,Giulia Massaro ,Carlo Viscomi ,Massimo Zeviani ,Daniele Ghezzi ,Emanuela Bottani ,Dario Brunetti

Required Elements in tRNA for Methylation by the Eukaryotic tRNA (Guanine- N2-) Methyltransferase (Trm11-Trm112 Complex)

真核生物 tRNA (鸟嘌呤-N2-)甲基转移酶 (Trm11-Trm112 复合物) 甲基化所需的 tRNA 元件

Yu Nishida,Shiho Ohmori,Risa Kakizono,Kunpei Kawai,Miyu Namba,Kazuki Okada,Ryota Yamagami,Akira Hirata,Hiroyuki Hori

Loss of function of the mitochondrial peptidase PITRM1 induces proteotoxic stress and Alzheimer's disease-like pathology in human cerebral organoids

线粒体肽酶PITRM1功能丧失会在人类脑类器官中诱导蛋白毒性应激和类似阿尔茨海默病的病理变化

María José Pérez # ,Dina Ivanyuk # ,Vasiliki Panagiotakopoulou ,Gabriele Di Napoli ,Stefanie Kalb ,Dario Brunetti ,Rawaa Al-Shaana ,Stephan A Kaeser ,Sabine Anne-Kristin Fraschka ,Mathias Jucker ,Massimo Zeviani ,Carlo Viscomi ,Michela Deleidi

Role of PITRM1 in Mitochondrial Dysfunction and Neurodegeneration

PITRM1在粒线粒体功能障碍和神经退行性疾病中的作用

Brunetti, Dario; Catania, Alessia; Viscomi, Carlo; Deleidi, Michela; Bindoff, Laurence A; Ghezzi, Daniele; Zeviani, Massimo

The 2'-O-methyladenosine nucleoside modification gene OsTRM13 positively regulates salt stress tolerance in rice

2'-O-甲基腺苷核苷修饰基因OsTRM13正向调控水稻的耐盐性。

Youmei Wang,Dongqin Li,Junbao Gao,Xukai Li,Rui Zhang,Xiaohuan Jin,Zhen Hu,Bo Zheng,Staffan Persson,Peng Chen

TRMT1-Catalyzed tRNA Modifications Are Required for Redox Homeostasis To Ensure Proper Cellular Proliferation and Oxidative Stress Survival

TRMT1 催化的 tRNA 修饰是维持氧化还原稳态所必需的,以确保细胞正常增殖和氧化应激生存

Joshua M Dewe, Benjamin L Fuller, Jenna M Lentini, Stefanie M Kellner, Dragony Fu

Insights into molecular plasticity in protein complexes from Trm9-Trm112 tRNA modifying enzyme crystal structure.

从Trm9-Trm112 tRNA修饰酶晶体结构中了解蛋白质复合物的分子可塑性。