日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Graft-derived VWF drives platelet activation and thrombocytopenia during porcine liver xenotransplantation to brain-dead human recipients

在将猪肝异种移植到脑死亡的人类受体时,移植来源的VWF驱动血小板活化和血小板减少症。

Zhao, Liang; Apostolidis, Sokratis A; Suzuki, Aae; Sarkar, Amrita; Guo, Qian; Li, Felix; Sagar, Alex; Fallon, John; Elzawahry, Mohamed A; Abbas, Syed Hussain; Lanieri, Leanne; Getchell, Kristen; Low, Susan C; Olthoff, Kim M; Furth, Emma E; Keating, Brendan J; Friend, Peter; Poncz, Mortimer; Shaked, Abraham; Abrams, Charles S

RAB5C Increases Endothelial Release of VWF by Regulating Vesicle Trafficking.

RAB5C 通过调节囊泡运输增加内皮细胞释放 VWF。

Reventun Paula, Toledano-Sanz Pablo, Delgado-Marin Maria, Viskadourou Maria, Foster D Brian, de Vries Paul S, Sabater-Lleal Maria, Alcharani Nunzio, Gonzalez-Cucharero Claudia, Osburn William O, Morrison Alanna C, Wolberg Alisa S, Smith Nicholas L, Arvanitis Marios, Lowenstein Charles J

Allele-selective disruption of pathogenic VWF variants in type 2 von Willebrand disease using CRISPR/Cas9

利用 CRISPR/Cas9 技术对 2 型血管性血友病中的致病性 VWF 变异体进行等位基因选择性破坏

Bär, Isabel; Groten, Stijn A; Barraclough, Alastair; Bürgisser, Petra E; van Kwawegen, Calvin; Lenting, Peter J; van Moort, Iris; Eikenboom, Jeroen C J; Leebeek, Frank W G; Voorberg, Jan; van den Biggelaar, Maartje; Bierings, Ruben

Population PK of VWF: toward personalized surgery

VWF的群体药代动力学:迈向个体化手术

Boban, Ana

HMB-002: a monovalent antibody that elevates circulating VWF and FVIII levels for treatment of von Willebrand disease

HMB-002:一种单价抗体,可提高循环中VWF和FVIII水平,用于治疗血管性血友病。

Häger, Mattias; Zivkovic, Minka; Gandhi, Prafull S; Rasmussen, Caroline; Bonvoisin, Cécile; Harrison, Rane A; Poulsen, Emil; Huskens, Dana; Roest, Mark; Ferrara, Fortunato; Naretto, Anais; Renaud, Lionel; Olsen, Ole H; Eskesen, Nicolas O; Holten-Andersen, Lars; Malladi, Ruthvik; Rea, Catherine J; Sørensen, Benny; Urbanus, Rolf T; Østergaard, Henrik

Low-input proteomics identifies vWF as a negative regulator of Tet2 mutant hematopoietic stem cell expansion.

低输入蛋白质组学鉴定出 vWF 是 Tet2 突变造血干细胞扩增的负调控因子。

Landscape and Spectrum of VWF Variants in Type 2 Von Willebrand Disease: Insights from a German Patient Cohort

2型血管性血友病中VWF变异体的分布及谱系:来自德国患者队列的启示

Yadegari, Hamideh; Halimeh, Susan; Krahforst, Alexander; Pavlova, Anna; Pezeshkpoor, Behnaz; Müller, Jens; Pötzsch, Bernd; Biswas, Arijit; Marquardt, Natascha; Scholz, Ute; Richter, Heinrich; Trobisch, Heiner; Liebscher, Karin; Olivieri, Martin; Trautmann-Grill, Karolin; Tiebel, Oliver; Knöfler, Ralf; Oldenburg, Johannes

A non-coding ABO regulatory variant associated with VWF levels, thrombosis risk, and COVID-19 severity is topologically linked to ADAMTS13 in endothelial cells

一种与血管性血友病因子(VWF)水平、血栓形成风险和新冠肺炎(COVID-19)严重程度相关的非编码ABO血型调控变异体,在内皮细胞中与ADAMTS13存在拓扑关联。

Esposito, Douglas Victorino; Sobrinho, Hellen Ferreira de Souza; Marques, Marcelo Rocha

Platelet Adhesion and Aggregation Dynamics over Collagen- and VWF-coated Surfaces: Insights from Dissipative Particle Dynamics Simulations and Microfluidic Experiments

血小板在胶原蛋白和VWF涂层表面上的粘附和聚集动力学:来自耗散粒子动力学模拟和微流控实验的启示

Tarafder, Anik; Wang, Shigang; Wu, Yilin; Han, Dong; Griffith, Bartley P; Wu, Zhongjun J

Abnormal von Willebrand factor multimer pattern without VWF variants in autosomal-recessive cutis laxa type IIA

常染色体隐性遗传性皮肤松弛症IIA型中存在异常的血管性血友病因子多聚体模式,但无VWF变异。

Jacobs, Jeremy W; Bibb, Lorin A; Syed, Nadia; Demet, Rosemary; Booth, Garrett S; Gailani, David