Abstract
Pemphigus foliaceus is a superficial autoimmune blistering disorder of the skin. Localized forms of pemphigus foliaceus are rare. Only a few cases have been described. We report a case of an 81-year-old man with pemphigus foliaceus who initially presented with localized dermatomal facial lesions. Due to this atypical presentation, making the diagnosis was challenging. To our knowledge, this is the first case of localized pemphigus foliaceus with a dermatomal distribution to be recorded.