Tracing the enteric neural crest cell pathway from origin to colonization: insights into Hirschsprung's disease

追踪肠神经嵴细胞从起源到定植的路径:对先天性巨结肠症的启示

阅读:2

Abstract

The enteric nervous system (ENS) is a highly organized network of neurons and glial cells within the intestinal wall, which orchestrates the precise regulation of gastrointestinal motility, nutrient absorption, and mucosal barrier function through interconnected ganglia and plexuses. Originating from enteric neural crest cells (ENCCs), the ENS develops as ENCCs undergo a coordinated migratory process to colonize the entire gastrointestinal tract. Defective migration of ENCCs leads to neurodevelopmental disorders, such as Hirschsprung's disease (HSCR), in which the distal intestine remains aganglionic. In recent years, breakthroughs in single-cell RNA sequencing and spatial transcriptomics have significantly advanced our ability to resolve gut cellular networks, uncovering spatiotemporal heterogeneity and lineage diversification during ENS development. Nevertheless, the inherent complexity of intestinal tissues-including diverse cell types, microenvironmental interactions, and multiscale regulatory networks-continues to impede mechanistic insights and precision therapeutics for enteric neurodevelopmental disorders. This review provides a comprehensive synthesis of molecular mechanisms underlying ENS migration, encompassing critical signaling pathways, migratory dynamics, and multicellular regulatory networks. We further discuss emerging technologies and unresolved questions in this rapidly evolving field.

特别声明

1、本页面内容包含部分的内容是基于公开信息的合理引用;引用内容仅为补充信息,不代表本站立场。

2、若认为本页面引用内容涉及侵权,请及时与本站联系,我们将第一时间处理。

3、其他媒体/个人如需使用本页面原创内容,需注明“来源:[生知库]”并获得授权;使用引用内容的,需自行联系原作者获得许可。

4、投稿及合作请联系:info@biocloudy.com。