Abstract
With the development and publication of the S2k guidelines of the Association of the Scientific Medical Societies in Germany (AWMF) on the diagnostics, treatment and aftercare of low-grade appendiceal mucinous neoplasm (LAMN), the currently available evidence about this rare disease is summarized. The guidelines serve as a foundation for an appropriate evidence-based oncological treatment of this patient cohort. This article provides a short summary of the most important points for the clinical practice.