Abstract
Amelogenesis imperfecta (AI) is a heterogeneous group of conditions characterized by inherited developmental defects of enamel. Patients with AI often have progressive and severe loss of occlusal vertical dimensions (OVD), resulting in challenging dental rehabilitation. In this case report, we present the management of a 24-year-old male patient who previously underwent orthodontics, direct and indirect restorations, and continued to have progressive tooth wear. His vertical dimensions were restored in two phases, firstly with provisional restorations at the improved OVD, followed by a combination of monolithic zirconia and lithium disilicate full-coverage crowns. A removable acrylic appliance was then constructed to protect his teeth. This report emphasizes the importance of preserving and protecting the OVD from an early age to prevent more costly and complicated management in future.