Short-term succinic acid treatment mitigates cerebellar mitochondrial OXPHOS dysfunction, neurodegeneration and ataxia in a Purkinje-specific spinocerebellar ataxia type 1 (SCA1) mouse model
短期琥珀酸治疗可减轻浦肯野特异性脊髓小脑共济失调 1 型 (SCA1) 小鼠模型中的小脑线粒体 OXPHOS 功能障碍、神经退行性病变和共济失调
期刊:PLoS One
影响因子:2.9
doi:10.1371/journal.pone.0188425
Austin Ferro, Emily Carbone, Jenny Zhang, Evan Marzouk, Monica Villegas, Asher Siegel, Donna Nguyen, Thomas Possidente, Jessilyn Hartman, Kailen Polley, Melissa A Ingram, Georgia Berry, Thomas H Reynolds, Bernard Possidente, Kimberley Frederick, Stephen Ives, Sarita Lagalwar