日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Proteomics profiling of serum and liver in GSD Ia and Ib patients: insights into complication mechanisms and circulation biomarkers

GSD Ia 和 Ib 患者血清和肝脏蛋白质组学分析:对并发症机制和循环生物标志物的深入了解

Xiao, Ruiqi; Gross-Valle, Candelas; Gerding, Albert; Thorne, Adam M; Oosterveer, Maaike H; Derks, Terry G J; de Meijer, Vincent E; Heiner-Fokkema, M Rebecca; Bakker, Barbara M; Wolters, Justina C

Microvillus inclusion disease-associated MYO5B deficiency impairs endosome-to-mitochondrion iron transfer.

微绒毛包涵体病相关的 MYO5B 缺乏症会损害内体到线粒体的铁转移。

Sun Chang, Leng Changsen, Sun Mingyue, Lin Yuan, Xu Mingqian, Martinez-Barriocanal Águeda, Gerding Albert, Kuipers Jeroen, de Leeuw Jim, Bakker Barbara M, Arango Diego, van IJzendoorn Sven C D

Untargeted Proteomics Profiling of Liver and Plasma in Fed and Fasted Liver-Specific Glycogen Storage Disease Type Ia (GSD Ia) Mice: Toward Potential Protein Biomarkers

对喂食和禁食状态下肝脏特异性糖原贮积症 Ia 型 (GSD Ia) 小鼠的肝脏和血浆进行非靶向蛋白质组学分析:探索潜在的蛋白质生物标志物

Xiao, Ruiqi; de Vries, Hilda I; Gross-Valle, Candelas; Bleeker, Aycha; Derks, Terry G J; Bakker, Barbara M; Oosterveer, Maaike H; Wolters, Justina C

Loss of Early Growth Response Protein 1 in the Liver Leads to Hepatic Lipid Accumulation Driven by an Imbalance Between Fatty Acid β-Oxidation and Oxidative Phosphorylation.

肝脏中早期生长反应蛋白 1 的缺失导致肝脏脂质积累,这是由于脂肪酸 β-氧化和氧化磷酸化之间的不平衡所致。

Verzijl Cristy R C, Struik Dicky, Gerding Albert, Eilers Roos E, Thomas Rachel E, Koster Mirjam, Langelaar-Makkinje Miriam, Smit Marieke, Huijkman Nicolette, Havinga Rick, Kloosterhuis Niels, Bloks Vincent W, Wolters Justina C, de Boer Jan Freark, van de Sluis Bart, Bakker Barbara M, Jonker Johan W

Long-Term Dietary Restriction Has a Strong and Positive Effect on Both Hepatic and Peripheral Insulin Sensitivity, in an Age- and Diet-Dependent Manner

长期饮食限制对肝脏和外周胰岛素敏感性均有显著的积极影响,且这种影响与年龄和饮食习惯相关。

Fisher, Joel C; Reijne, Aaffien C; Hribar, Kaja; Vieira-Lara, Marcel A; Talarovicova, Alzbeta; Reijngoud, Dirk-Jan; van Niekerk, David D; Snoep, Jacky L; van Dijk, Gertjan; Bakker, Barbara M

The relation between dietary polysaccharide intake and urinary excretion of tetraglucoside

膳食多糖摄入量与尿四糖苷排泄量的关系

Gross-Valle, Candelas; Jacobs, Tessa C; Dijck-Brouwer, Janneke D A; Lubberts, Janniek; Bakker, Barbara M; Bakker, Stephan J L; van der Veen, Yvonne; Schreuder, Andrea B; Derks, Terry G J; van der Krogt, Jennifer; Groen, Joost; Heiner-Fokkema, M Rebecca

iPSC-Derived Liver Organoids as a Tool to Study Medium Chain Acyl-CoA Dehydrogenase Deficiency.

利用 iPSC 衍生的肝脏类器官研究中链酰基辅酶 A 脱氢酶缺乏症

Kiyuna Ligia A, Horcas-Nieto José M, Odendaal Christoff, Langelaar-Makkinje Miriam, Gerding Albert, Broekhuis Mathilde J C, Bonanini Flavio, Singh Madhulika, Kurek Dorota, Harms Amy C, Hankemeier Thomas, Foijer Floris, Derks Terry G J, Bakker Barbara M

Endogenous Glucose Production in Patients With Glycogen Storage Disease Type Ia Estimated by Oral D-[6,6-2H2]-glucose

口服D-[6,6-2H2]-葡萄糖法估算Ia型糖原贮积症患者的内源性葡萄糖生成

Rossi, Alessandro; Oosterveer, Maaike H; van Dijk, Theo H; Bleeker, Aycha; Koehorst, Martijn; Weinstein, David A; Bakker, Barbara M; Derks, Terry G J

Longitudinal Metabolomics Data Analysis Informed by Mechanistic Models

基于机制模型的纵向代谢组学数据分析

Li, Lu; Hoefsloot, Huub; Bakker, Barbara M; Horner, David; Rasmussen, Morten A; Smilde, Age K; Acar, Evrim

Analyzing postprandial metabolomics data using multiway models: a simulation study

利用多维模型分析餐后代谢组学数据:一项模拟研究

Li, Lu; Yan, Shi; Bakker, Barbara M; Hoefsloot, Huub; Chawes, Bo; Horner, David; Rasmussen, Morten A; Smilde, Age K; Acar, Evrim