日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Identification of small molecules that enhance aminoglycoside-mediated suppression of CFTR and NF1 nonsense mutations.

鉴定能增强氨基糖苷类药物对 CFTR 和 NF1 无义突变抑制作用的小分子。

Sammons Joshua, Chen Jianguo, Thrasher Kari, Fu Lianwu, Du Ming, Wen Hui, Bostwick J Robert, Vinson Paige, Moukha-Chafiq Omar, Augelli-Szafran Corinne, Keeling Kim M, Wallis Deeann, Kesterson Robert A, Rowe Steven M, Bedwell David M

Correction: Immortalization and characterization of Schwann cell lines derived from NF1-associated cutaneous neurofibromas

更正:源自NF1相关皮肤神经纤维瘤的雪旺细胞系的永生化和表征

Li, Hua; Pemov, Alexander; Allaway, Robert; Muir, David F; Chang, Lung-Ji; Banerjee, Jineta; Scott, Alexandra J; Nagy, Jaime M W; Liu, Jian; Carrió, Meritxell; Mazuelas, Helena; Yachnis, Anthony; Lee, Sang Y; Zhang, Xiaochun; Lyu, Yang; Stewart, Douglas R; Hirbe, Angela; Blakeley, Jaishri O; Serra, Eduard; Wallis, Deeann; Wallace, Margaret R

Immortalization and characterization of Schwann cell lines derived from NF1-associated cutaneous neurofibromas

NF1相关皮肤神经纤维瘤来源的雪旺细胞系的永生化和表征

Li, Hua; Pemov, Alexander; Allaway, Robert; Muir, David F; Chang, Lung-Ji; Banerjee, Jineta; Scott, Alexandra J; Nagy, Jaime M W; Liu, Jian; Carrió, Meritxell; Mazuelas, Helena; Yachnis, Anthony; Lee, Sang Y; Zhang, Xiaochun; Lyu, Yang; Stewart, Douglas R; Hirbe, Angela; Blakeley, Jaishri O; Serra, Eduard; Wallis, Deeann; Wallace, Margaret R

Precision preclinical modeling to advance cancer treatment

精准的临床前模型助力癌症治疗

Gutmann, David H; Boehm, Jesse S; Karlsson, Elinor K; Padron, Eric; Seshadri, Mukund; Wallis, Deeann; Snyder, Joshua C

Repair of Mutated NF1 mRNA with Trans-Splicing Group I Intron Ribozymes

利用反式剪接组 I 内含子核酶修复突变的 NF1 mRNA

Leier, André; Han, Xu; Aghzadi, Jehanne; Westin, Erik; Liu, Jian; Marquez Lago, Tatiana T; Kesterson, Robert A; Korf, Bruce R; Wallis, Deeann; Müller, Ulrich F

Global proteomics and affinity mass spectrometry analysis of human Schwann cells indicates that variation in and loss of neurofibromin (NF1) alters protein expression and cellular and mitochondrial metabolism

人类雪旺细胞的整体蛋白质组学和亲和力质谱分析表明,神经纤维蛋白 (NF1) 的变化和丢失会改变蛋白质表达以及细胞和线粒体的代谢

Christian X Fay, Elizabeth R M Zunica, Elias Awad, William Bradley, Cameron Church, Jian Liu, Hui Liu, David K Crossman, James A Mobley, John P Kirwan, Christopher L Axelrod, Erik Westin, Robert A Kesterson, Deeann Wallis

Designing and Implementing a Heart Team: Institutional Experiences Over the Past 10 Years

设计和实施心脏团队:过去十年的机构经验

Akram, Mahrukh F; Burgess, Andrea L; Stickland, Deeann; Willekes, Charles L; McNamara, Richard F; McNamara, David A

Direct Optical Quantification of Chain Collapse, Reduced Dielectric, and Water Release Driving Protein Phase Separation

直接光学定量分析驱动蛋白质相分离的链坍塌、介电常数降低和水释放

Perets, Ethan A; Spies, Jacob A; Cheong, Justin H; Shi, Lixue; Asamoto, DeeAnn K; Holehouse, Alex S; Kim, Judy E; Min, Wei; Neu, Jens; Yan, Elsa C Y

Ecological countermeasures to prevent pathogen spillover and subsequent pandemics

防止病原体溢出和后续大流行的生态对策

Plowright, Raina K; Ahmed, Aliyu N; Coulson, Tim; Crowther, Thomas W; Ejotre, Imran; Faust, Christina L; Frick, Winifred F; Hudson, Peter J; Kingston, Tigga; Nameer, P O; O'Mara, M Teague; Peel, Alison J; Possingham, Hugh; Razgour, Orly; Reeder, DeeAnn M; Ruiz-Aravena, Manuel; Simmons, Nancy B; Srinivas, Prashanth N; Tabor, Gary M; Tanshi, Iroro; Thompson, Ian G; Vanak, Abi T; Vora, Neil M; Willison, Charley E; Keeley, Annika T H

snRNA-seq of human cutaneous neurofibromas before and after selumetinib treatment implicates role of altered Schwann cell states, inter-cellular signaling, and extracellular matrix in treatment response

人类皮肤神经纤维瘤在接受司美替尼治疗前后的 snRNA-seq 提示改变的施万细胞状态、细胞间信号传导和细胞外基质在治疗反应中的作用

Cameron Church #, Christian X Fay #, Emil Kriukov, Hui Liu, Ashley Cannon, Lauren Ashley Baldwin, David K Crossman, Bruce Korf, Margaret R Wallace, Andrea M Gross, Brigitte C Widemann, Robert A Kesterson, Petr Baranov, Deeann Wallis