日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Cholesterol Deficiency Directs Autophagy-Dependent Secretion of Extracellular Vesicles

胆固醇缺乏症诱导自噬依赖性细胞外囊泡分泌

Yaeger, Jazmine D W; Sengupta, Sonali; Walz, Austin L; Morita, Mayu; Morgan, Terry K; Vermeer, Paola D; Francis, Kevin R

Editorial: Studying rare diseases using induced pluripotent stem cell (iPSC)-based model systems

社论:利用诱导多能干细胞(iPSC)模型系统研究罕见病

Francis, Kevin R; Chen, Guokai; Kiris, Erkan

Dishevelled localization and function are differentially regulated by structurally distinct sterols

Dishevelled 的定位和功能受结构不同的甾醇差异性调控

Sengupta, Sonali; Yaeger, Jazmine D W; Schultz, Maycie M; May, Danielle G; Roux, Kyle J; Francis, Kevin R

Altered Cerebrospinal Fluid Proteins in Smith-Lemli-Opitz Syndrome

史密斯-莱姆利-奥皮茨综合征患者的脑脊液蛋白改变

Li, Wenping; Pergande, Melissa R; Serna-Perez, Fidel; Patel, Vinayak; Crutchfield, Christopher A; Searle, Brian C; Picache, Jaqueline A; Farhat, Nicole M; Wassif, Christopher A; Backlund, Peter S; Bianconi, Simona; Pacak, Karel; Freel, Bethany A; Francis, Kevin R; Porter, Forbes D; Cologna, Stephanie M

Compromised lipid metabolism, mitochondria respiration and neuroprotective effects in iPSC-derived astrocytes from a Smith-Lemli-Opitz syndrome patient.

Smith-Lemli-Opitz 综合征患者的 iPSC 衍生星形胶质细胞的脂质代谢、线粒体呼吸和神经保护作用受损。

Kawatani Keiji, Baker Samantha K, Yaeger Jazmine D W, Anderson Ruthellen H, Ren Yingxue, Li Zonghua, Bao Hanmei, Han Xianlin, Francis Kevin R, Kanekiyo Takahisa

Lipidomics reveals cell specific changes during pluripotent differentiation to neural and mesodermal lineages.

脂质组学揭示了多能细胞分化为神经和中胚层谱系过程中细胞特异性的变化

Odenkirk Melanie T, Jostes Haley C, Francis Kevin R, Baker Erin S

MLC1 alteration in iPSCs give rise to disease-like cellular vacuolation phenotype in the astrocyte lineage

iPSCs中MLC1的改变会导致星形胶质细胞谱系出现类似疾病的细胞空泡化表型

Sharma, Saumya; Bharti, Vishal; Das, Prosad Kumar; Rahman, Abdul; Sharma, Harshita; Rauthan, Riya; Rc, Madhumita; Gupta, Neerja; Shukla, Rashmi; Mohanty, Sujata; Kabra, Madhulika; Francis, Kevin R; Chakraborty, Debojyoti

Lipidomics Reveals Cell Specific Changes During Pluripotent Differentiation to Neural and Mesodermal Lineages.

脂质组学揭示了多能性细胞向神经和中胚层谱系分化过程中的细胞特异性变化

Odenkirk Melanie T, Jostes Haley C, Francis Kevin R, Baker Erin S

Macrophage signaling and function are regulated by distinct sterol biochemistries.

巨噬细胞信号传导和功能受不同的甾醇生化过程调控

Yaeger Jazmine D W, Kerkvliet Jason G, Pradhan Bijaya, Lawver Amelia G, Sengupta Sonali, Thiex Natalie W, Francis Kevin R

Sterols lower energetic barriers of membrane bending and fission necessary for efficient clathrin-mediated endocytosis

甾醇类物质降低了膜弯曲和裂变所需的能量屏障,而这对于有效的网格蛋白介导的内吞作用至关重要。

Anderson, Ruthellen H; Sochacki, Kem A; Vuppula, Harika; Scott, Brandon L; Bailey, Elizabeth M; Schultz, Maycie M; Kerkvliet, Jason G; Taraska, Justin W; Hoppe, Adam D; Francis, Kevin R