日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Androgens Accentuate TGF-β Dependent Erk/Smad Activation During Thoracic Aortic Aneurysm Formation in Marfan Syndrome Male Mice

雄激素增强马凡氏综合征雄性小鼠胸主动脉瘤形成过程中 TGF-β 依赖性 Erk/Smad 的激活

Yasushi Tashima, Hao He, Jason Z Cui, Albert J Pedroza, Ken Nakamura, Nobu Yokoyama, Cristiana Iosef, Grayson Burdon, Tiffany Koyano, Atsushi Yamaguchi, Michael P Fischbein

Divergent effects of canonical and non-canonical TGF-β signalling on mixed contractile-synthetic smooth muscle cell phenotype in human Marfan syndrome aortic root aneurysms

经典和非经典 TGF-β 信号对人类马凡氏综合征主动脉根部动脉瘤中混合收缩-合成平滑肌细胞表型的不同影响

Albert J Pedroza, Tiffany Koyano, Jeffrey Trojan, Adam Rubin, Itai Palmon, Kevin Jaatinen, Grayson Burdon, Paul Chang, Yasushi Tashima, Jason Z Cui, Gerry Berry, Cristiana Iosef, Michael P Fischbein

Characterization of doxycycline-mediated inhibition of Marfan syndrome-associated aortic dilation by multiphoton microscopy

通过多光子显微镜表征强力霉素介导的马凡氏综合征相关主动脉扩张的抑制

Arash Y Tehrani #, Jason Z Cui #, T Bucky Jones, Ester Hotova, Monica Castro, Pascal Bernatchez, Cornelis van Breemen, Mitra Esfandiarei

Quantitative proteomics reveal lineage-specific protein profiles in iPSC-derived Marfan syndrome smooth muscle cells

定量蛋白质组学揭示 iPSC 衍生的马凡氏综合征平滑肌细胞谱系特异性蛋白质谱

Cristiana Iosef, Albert J Pedroza, Jason Z Cui, Alex R Dalal, Mamoru Arakawa, Yasushi Tashima, Tiffany K Koyano, Grayson Burdon, Samantha M P Churovich, Joshua O Orrick, Mitchel Pariani, Michael P Fischbein

Aortic Dimensions, Biophysical Properties, and Plasma Biomarkers in Children and Adults with Marfan or Loeys-Dietz Syndrome

患有马凡氏综合征或 Loeys-Dietz 综合征的儿童和成人的主动脉尺寸、生物物理特性和血浆生物标志物

Jason Z Cui, Kevin C Harris, Koen Raedschelders, Zsuzsanna Hollander, James E Potts, Astrid De Souza, Marla Kiess, Bruce M McManus, Pascal Bernatchez, Leslie A Raffin, Heidi Paine, Cornelis van Breemen, George G S Sandor, Mitra Esfandiarei

In vivo characterization of doxycycline-mediated protection of aortic function and structure in a mouse model of Marfan syndrome-associated aortic aneurysm

在马凡氏综合征相关主动脉瘤小鼠模型中,强力霉素介导的主动脉功能和结构保护的体内表征

Jason Z Cui, Ling Lee, Xiaoye Sheng, Fanny Chu, Christine P Gibson, Taline Aydinian, David C Walker, George G S Sandor, Pascal Bernatchez, Glen F Tibbits, Cornelis van Breemen, Mitra Esfandiarei